Human deficiencies of fucosylation and sialylation affecting selectin ligands

Seminars in Immunopathology

Volumn 34, Issue 3, 2012, Pages 383-399

  Lühn, Kerstin ^a   Wild, Martin K ^b  

^a UNIVERSITY OF OXFORD   (United Kingdom)

^b MAX PLANCK INSTITUTE FOR MOLECULAR BIOMEDICINE   (Germany)

Author keywords

Leukocyte adhesion deficiency II . Congenital disorder of glycosylation . Fucosyltransferases . Thrombocytopenia

Indexed keywords

ASIALOGLYCOPROTEIN RECEPTOR; AUTOANTIBODY; CARRIER PROTEIN; CYTIDINE PHOSPHATE N ACYLNEURAMINATE PHOSPHODIESTERASE; FUCOSE; FUCOSYLTRANSFERASE; GLYCAN DERIVATIVE; GUANOSINE DIPHOSPHATE FUCOSE; GUANOSINE DIPHOSPHATE FUCOSE TRANSPORTER; MESSENGER RNA; NOTCH RECEPTOR; SELECTIN; SIALIC ACID; SIALYL LEWIS X ANTIGEN; UNCLASSIFIED DRUG;

AMINO ACID SUBSTITUTION; ANTIBODY RESPONSE; CELL ADHESION; CLINICAL FEATURE; CONFERENCE PAPER; CONGENITAL DISORDER OF GLYCOSYLATION; CONGENITAL DISORDER OF GLYCOSYLATION TYPE 2C; CONGENITAL DISORDER OF GLYCOSYLATION TYPE 2F; DEVELOPMENTAL DISORDER; DIET SUPPLEMENTATION; DOSE RESPONSE; ENZYME DEFECT; FUCOSYLATION; FUCOSYLATION DISORDER; FUT7 GENE; GENE; GENE MUTATION; GFTP GENE; HUMAN; IMMUNE DEFICIENCY; METABOLIC DISORDER; METABOLIC REGULATION; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; SIALYLATION; SIALYLATION DISORDER; THROMBOCYTOPENIA;

AGED; ANIMALS; CELL ADHESION; CELL ADHESION MOLECULES; CONGENITAL DISORDERS OF GLYCOSYLATION; FUCOSE; FUCOSYLTRANSFERASES; GLYCOSYLATION; HUMANS; INFANT; LEUKOCYTES; LIGANDS; MALE; MICE; SELECTINS;

EID: 84866055678     PISSN: 18632297     EISSN: 18632300     Source Type: Journal    
DOI: 10.1007/s00281-012-0304-1     Document Type: Conference Paper

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