Leukocyte adhesion deficiency type 1 (LAD-1)/variant. A novel immunodeficiency syndrome characterized by dysfunctional β2 integrins

Journal of Clinical Investigation

Volumn 100, Issue 7, 1997, Pages 1725-1733

  Kuijpers, Taco W ^a,c   Van Lier, René A W ^a   Hamann, Dörte ^a   De Boer, Martin ^a   Thung, L Yin ^b   Weening, Ron S ^a   Verhoeven, Arthur J ^a   Roos, Dirk ^a  

^a UNIVERSITY OF AMSTERDAM   (Netherlands)

^b SLOTERVAART HOSPITAL   (Netherlands)

^c ACADEMIC MEDICAL CENTER   (Netherlands)

Author keywords

Aggregation; Bleeding tendency; Chemotaxis; Integrins; Leukocyte adhesion deficiency

Indexed keywords

CD11 ANTIGEN; CD18 ANTIGEN; INTEGRIN;

ANTIGEN EXPRESSION; ARTICLE; BACTERIAL INFECTION; BLEEDING TENDENCY; CHEMOTAXIS; CLINICAL FEATURE; CONTROLLED STUDY; GRANULOCYTOSIS; HUMAN; HUMAN CELL; IMMUNE DEFICIENCY; INFLAMMATION; LEUKOCYTE ADHESION DEFICIENCY; PRIORITY JOURNAL; T LYMPHOCYTE; WOUND HEALING;

EID: 0030885763     PISSN: 00219738     EISSN: None     Source Type: Journal    
DOI: 10.1172/JCI119697     Document Type: Article

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