Selective pattern of motor system damage in gamma-synuclein transgenic mice mirrors the respective pathology in amyotrophic lateral sclerosis

Neurobiology of Disease

Volumn 48, Issue 1, 2012, Pages 124-131

  Peters, Owen M ^a   Millership, Steven ^a   Shelkovnikova, Tatyana A ^a,b   Soto, Ileana ^c,d   Keeling, Lora ^a   Hann, Anthony ^a   Marsh Armstrong, Nicholas ^c,d   Buchman, Vladimir L ^a   Ninkina, Natalia ^a,b  

^a CARDIFF UNIVERSITY   (United Kingdom)

^b INSTITUTE OF PHYSIOLOGICALLY ACTIVE COMPOUNDS   (Russian Federation)

^c JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

^d KENNEDY KRIEGER INSTITUTE   (United States)

Author keywords

Aggregation; ALS; Motor neuron; Neurodegeneration; Neurofilament

Indexed keywords

GAMMA SYNUCLEIN;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LOSS; CONTROLLED STUDY; DEGENERATIVE DISEASE; DISEASE ASSOCIATION; DISEASE MODEL; MOTONEURON; MOTOR NEURON DISEASE; MOUSE; NERVE CELL LESION; NERVE FIBER; NONHUMAN; PRIORITY JOURNAL; PROTEIN EXPRESSION; SENSORY SYSTEM; SYNUCLEINOPATHY; TRANSGENIC MOUSE;

AMYOTROPHIC LATERAL SCLEROSIS; ANIMALS; AXONS; DISEASE MODELS, ANIMAL; GAMMA-SYNUCLEIN; MICE; MICE, TRANSGENIC; MOTOR NEURONS; SPINAL CORD; TOUCH PERCEPTION;

EID: 84864071049     PISSN: 09699961     EISSN: 1095953X     Source Type: Journal    
DOI: 10.1016/j.nbd.2012.06.016     Document Type: Article

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