Glomerular pathology in Alport syndrome: A molecular perspective

Pediatric Nephrology

Volumn 27, Issue 6, 2012, Pages 885-890

  Cosgrove, Dominic ^a  

^a BOYS TOWN NATIONAL RESEARCH HOSPITAL   (United States)

Author keywords

Alport syndrome; Glomerular basement membrane; Pathobiology; Podocyte

Indexed keywords

ALPHA1 INTEGRIN; CHEMOKINE RECEPTOR CCR2; COLLAGEN TYPE 4; CYCLOSPORIN; DIPEPTIDYL CARBOXYPEPTIDASE INHIBITOR; GELATINASE A; GELATINASE B; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE INHIBITOR; LAMININ; LAMININ 111; LAMININ 211; LAMININ BETA1; MACROPHAGE ELASTASE; MATRIX METALLOPROTEINASE INHIBITOR; MONOCYTE CHEMOTACTIC PROTEIN 1; RAMIPRIL; STROMELYSIN; STROMELYSIN 2; TRANSFORMING GROWTH FACTOR BETA1; UNCLASSIFIED DRUG;

ALPORT SYNDROME; CELL INTERACTION; DISEASE COURSE; DRUG EFFICACY; ENZYME INDUCTION; GENE MUTATION; GENE REPLACEMENT THERAPY; GENE SEQUENCE; GLOMERULOPATHY; GLOMERULUS FILTRATION; HUMAN; MESANGIUM CELL; MOLECULAR PATHOLOGY; NONHUMAN; PATHOGENESIS; PODOCYTE; POINT MUTATION; PRIORITY JOURNAL; PROTEIN ASSEMBLY; PROTEIN CLEAVAGE; PROTEIN DEGRADATION; PROTEIN EXPRESSION; PROTEIN INDUCTION; PROTEIN TRANSPORT; PROTEINURIA; REVIEW; STEM CELL TRANSPLANTATION;

ANIMALS; COLLAGEN TYPE IV; DISEASE PROGRESSION; GENETIC PREDISPOSITION TO DISEASE; HUMANS; KIDNEY FAILURE, CHRONIC; KIDNEY GLOMERULUS; MODELS, ANIMAL; MUTATION; NEPHRITIS, HEREDITARY; PHENOTYPE; PROGNOSIS; PROTEINURIA;

EID: 84863983649     PISSN: 0931041X     EISSN: 1432198X     Source Type: Journal    
DOI: 10.1007/s00467-011-1868-z     Document Type: Review

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