Reorganization of Cajal bodies and nucleolar targeting of coilin in motor neurons of type i spinal muscular atrophy

Histochemistry and Cell Biology

Volumn 137, Issue 5, 2012, Pages 657-667

  Tapia, Olga ^a   Bengoechea, Rocío ^a   Palanca, Ana ^a   Arteaga, Rosa ^b   Val Bernal, J Fernando ^b   Tizzano, Eduardo F ^c   Berciano, María T ^a   Lafarga, Miguel ^a  

^a UNIVERSITY OF CANTABRIA   (Spain)

^b HOSPITAL UNIVERSITARIO MARQUÉS DE VALDECILLA   (Spain)

^c HOSPITAL DE LA SANTA CREU I SANT PAU   (Spain)

Author keywords

Cajal bodies; Gems; Motor neurons; PML bodies; Pre mRNA splicing disease; Spinal muscular atrophy

Indexed keywords

COILIN; PROTEIN; PROTEIN PA28GAMMA; SMALL NUCLEAR RIBONUCLEOPROTEIN; SURVIVAL MOTOR NEURON PROTEIN 1; UNCLASSIFIED DRUG; NUCLEAR PROTEIN; P80-COILIN; SMN1 PROTEIN, HUMAN;

ARTICLE; CELL NUCLEUS INCLUSION BODY; CELL STRESS; COILED BODY; CONTROLLED STUDY; EXON; GENE DELETION; HOMOZYGOSITY; HUMAN; HUMAN TISSUE; IMMUNOCYTOCHEMISTRY; INFANT; MALE; MOTONEURON; NUCLEOLUS; PRIORITY JOURNAL; PROTEIN TARGETING; QUANTITATIVE ANALYSIS; SPINAL MUSCULAR ATROPHY; SPLICEOSOME; WESTERN BLOTTING; CHEMISTRY; GENETICS; HEREDITARY SPINAL MUSCULAR ATROPHY; METABOLISM; PATHOLOGY;

CELL NUCLEOLUS; COILED BODIES; HUMANS; MOTOR NEURONS; NUCLEAR PROTEINS; SPINAL MUSCULAR ATROPHIES OF CHILDHOOD; SURVIVAL OF MOTOR NEURON 1 PROTEIN;

EID: 84862865734     PISSN: 09486143     EISSN: 1432119X     Source Type: Journal    
DOI: 10.1007/s00418-012-0921-8     Document Type: Article

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