Residual Cajal bodies in coilin knockout mice fail to recruit Sm snRNPs and SMN, the spinal muscular atrophy gene product

Journal of Cell Biology

Volumn 154, Issue 2, 2001, Pages 293-307

  Tucker, Karen E ^a,b   Berciano, Maria Teresa ^c   Jacobs, Erica Y ^a,b   LePage, David F ^a   Shpargel, Karl B ^a,b   Rossire, Jennifer J ^a,b   Chan, Edward K L ^d   Lafarga, Miguel ^c   Conlon, Ronald A ^a   Gregory Matera, A ^a,b  

^a CASE WESTERN RESERVE UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY HOSPITALS OF CLEVELAND   (United States)

^c UNIVERSITY OF CANTABRIA   (Spain)

^d SCRIPPS RESEARCH INSTITUTE   (United States)

Author keywords

Coilin; Nuclear organization; SMA; SMN; SnRNPs

Indexed keywords

COILIN; FIBRILLARIN; GENE PRODUCT; PROTEIN; SMALL NUCLEAR RIBONUCLEOPROTEIN; SURVIVAL MOTOR NEURON PROTEIN; UNCLASSIFIED DRUG;

ARTICLE; COILED BODY; COMPLEX FORMATION; KNOCKOUT MOUSE; MOUSE; MUTATION; NONHUMAN; NORTHERN BLOTTING; PRIORITY JOURNAL; PROTEIN EXPRESSION; SPINAL MUSCULAR ATROPHY; WESTERN BLOTTING;

ANIMALS; AUTOANTIGENS; BLOTTING, NORTHERN; CELL LINE; CELL NUCLEOLUS; CHROMOSOMAL PROTEINS, NON-HISTONE; COILED BODIES; CYCLIC AMP RESPONSE ELEMENT-BINDING PROTEIN; FETAL VIABILITY; GENE EXPRESSION; GENE TARGETING; GREEN FLUORESCENT PROTEINS; HOMOZYGOTE; LUMINESCENT PROTEINS; MICE; MICE, KNOCKOUT; NERVE TISSUE PROTEINS; NUCLEAR PROTEINS; ORGAN SPECIFICITY; PHOSPHOPROTEINS; RECOMBINANT FUSION PROTEINS; RIBONUCLEOPROTEINS, SMALL NUCLEAR; RNA SPLICING; RNA, MESSENGER; RNA-BINDING PROTEINS; SURVIVAL RATE;

ANIMALIA; RODENTIA;

EID: 0035939674     PISSN: 00219525     EISSN: None     Source Type: Journal    
DOI: 10.1083/jcb.200104083     Document Type: Article

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