-
1
-
-
33746127253
-
Über eine eigenartige herdförmige Erkrankung des Zentralnervensystems
-
Creutzfeldt H. Über eine eigenartige herdförmige Erkrankung des Zentralnervensystems. Z ges Neurol Psychiat 1920; 57: 1-18.
-
(1920)
Z ges Neurol Psychiat
, vol.57
, pp. 1-18
-
-
Creutzfeldt, H.1
-
2
-
-
51849177198
-
Über eigenartige Erkrankungen des Zentralnervensystems mit bemerkenswerten anatomischen Befunde (Spastische Pseudosklerose-Encephalomyelopathie mit disseminierten Degenerationsherden)
-
Jakob A. Über eigenartige Erkrankungen des Zentralnervensystems mit bemerkenswerten anatomischen Befunde (Spastische Pseudosklerose-Encephalomyelopathie mit disseminierten Degenerationsherden). Z ges Neurol Psychiat 1921; 64: 147-228.
-
(1921)
Z ges Neurol Psychiat
, vol.64
, pp. 147-228
-
-
Jakob, A.1
-
3
-
-
45749093810
-
Creutzfeldt-Jakob disease in Austria: an autopsy-controlled study
-
Gelpi E, Heinzl H, Höftberger R, et al. Creutzfeldt-Jakob disease in Austria: an autopsy-controlled study. Neuroepidemiology 2008; 30: 215-221.
-
(2008)
Neuroepidemiology
, vol.30
, pp. 215-221
-
-
Gelpi, E.1
Heinzl, H.2
Höftberger, R.3
-
4
-
-
51549111981
-
Atypical BSE (BASE) transmitted from asymptomatic aging cattle to a primate
-
Comoy EE, Casalone C, Lescoutra-Etchegaray N, et al. Atypical BSE (BASE) transmitted from asymptomatic aging cattle to a primate. PLoS One 2008; 3: e3017.
-
(2008)
PLoS One
, vol.3
-
-
Comoy, E.E.1
Casalone, C.2
Lescoutra-Etchegaray, N.3
-
5
-
-
56949108846
-
Transmission of atypical bovine prions to mice transgenic for human prion protein
-
Béringue V, Herzog L, Reine F, et al. Transmission of atypical bovine prions to mice transgenic for human prion protein. Emerg Infect Dis 2008; 14: 1898-1901.
-
(2008)
Emerg Infect Dis
, vol.14
, pp. 1898-1901
-
-
Béringue, V.1
Herzog, L.2
Reine, F.3
-
6
-
-
41149112365
-
Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain
-
Kong Q, Zheng M, Casalone C, et al. Evaluation of the human transmission risk of an atypical bovine spongiform encephalopathy prion strain. J Virol 2008; 82: 3697-3701.
-
(2008)
J Virol
, vol.82
, pp. 3697-3701
-
-
Kong, Q.1
Zheng, M.2
Casalone, C.3
-
7
-
-
0029904189
-
Risk factors for Creutzfeldt-Jakob disease: a reanalysis of case-control studies
-
Wientjens D, Davanipour Z, Hofman A, et al. Risk factors for Creutzfeldt-Jakob disease: a reanalysis of case-control studies. Neurology 1996; 46: 1287-1291.
-
(1996)
Neurology
, vol.46
, pp. 1287-1291
-
-
Wientjens, D.1
Davanipour, Z.2
Hofman, A.3
-
8
-
-
41849101689
-
Risk factors for sporadic Creutzfeldt-Jakob disease
-
Ward HJ, Everington D, Cousens SN, et al. Risk factors for sporadic Creutzfeldt-Jakob disease. Ann Neurol 2008; 63: 347-354.
-
(2008)
Ann Neurol
, vol.63
, pp. 347-354
-
-
Ward, H.J.1
Everington, D.2
Cousens, S.N.3
-
9
-
-
0025820942
-
Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease
-
Palmer MS, Dryden AJ, Hughes JT, Collinge J. Homozygous prion protein genotype predisposes to sporadic Creutzfeldt-Jakob disease. Nature 1991; 352: 340-342.
-
(1991)
Nature
, vol.352
, pp. 340-342
-
-
Palmer, M.S.1
Dryden, A.J.2
Hughes, J.T.3
Collinge, J.4
-
10
-
-
0025859996
-
Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease
-
Collinge J, Palmer MS, Dryden AJ. Genetic predisposition to iatrogenic Creutzfeldt-Jakob disease. Lancet 1991; 337: 1441-1442.
-
(1991)
Lancet
, vol.337
, pp. 1441-1442
-
-
Collinge, J.1
Palmer, M.S.2
Dryden, A.J.3
-
11
-
-
70350188098
-
Genomic and post-genomic analyses of human prion diseases
-
Pocchiari M, Poleggi A, Principe S, Graziano S, Cardone F. Genomic and post-genomic analyses of human prion diseases. Genome Med 2009; 1: 63.
-
(2009)
Genome Med
, vol.1
, pp. 63
-
-
Pocchiari, M.1
Poleggi, A.2
Principe, S.3
Graziano, S.4
Cardone, F.5
-
12
-
-
0028235176
-
Human spongiform encephalopathy: the National Institute of Health series of 300 cases of experimentally transmitted disease
-
Brown P, Gibbs C, Rodgers-Johnson P, et al. Human spongiform encephalopathy: the National Institute of Health series of 300 cases of experimentally transmitted disease. Ann Neurol 1994; 35: 513-529.
-
(1994)
Ann Neurol
, vol.35
, pp. 513-529
-
-
Brown, P.1
Gibbs, C.2
Rodgers-Johnson, P.3
-
13
-
-
0032816292
-
Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects
-
Parchi P, Giese A, Capellari S, et al. Classification of sporadic Creutzfeldt-Jakob disease based on molecular and phenotypic analysis of 300 subjects. Ann Neurol 1999; 46: 224-233.
-
(1999)
Ann Neurol
, vol.46
, pp. 224-233
-
-
Parchi, P.1
Giese, A.2
Capellari, S.3
-
14
-
-
4944246589
-
Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies
-
Pocchiari M, Puopolo M, Croes E, et al. Predictors of survival in sporadic Creutzfeldt-Jakob disease and other human transmissible spongiform encephalopathies. Brain 2004; 127: 2348-2359.
-
(2004)
Brain
, vol.127
, pp. 2348-2359
-
-
Pocchiari, M.1
Puopolo, M.2
Croes, E.3
-
15
-
-
0032747378
-
How to improve the clinical diagnosis of Creutzfeldt-Jakob disease
-
Poser S, Mollenhauer B, Kraubeta A, et al. How to improve the clinical diagnosis of Creutzfeldt-Jakob disease. Brain 1999; 122: 2345-2351.
-
(1999)
Brain
, vol.122
, pp. 2345-2351
-
-
Poser, S.1
Mollenhauer, B.2
Kraubeta, A.3
-
16
-
-
70349947005
-
Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease
-
Zerr I, Kallenberg K, Summers DM, et al. Updated clinical diagnostic criteria for sporadic Creutzfeldt-Jakob disease. Brain 2009; 132: 2659-2668.
-
(2009)
Brain
, vol.132
, pp. 2659-2668
-
-
Zerr, I.1
Kallenberg, K.2
Summers, D.M.3
-
17
-
-
67649479370
-
MRI lesion profiles in sporadic Creutzfeldt-Jakob disease
-
Meissner B, Kallenberg K, Sanchez-Juan P, et al. MRI lesion profiles in sporadic Creutzfeldt-Jakob disease. Neurology 2009; 72: 1994-2001.
-
(2009)
Neurology
, vol.72
, pp. 1994-2001
-
-
Meissner, B.1
Kallenberg, K.2
Sanchez-Juan, P.3
-
18
-
-
0034718472
-
Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt-Jakob disease
-
Zerr I, Pocchiari M, Collins S, et al. Analysis of EEG and CSF 14-3-3 proteins as aids to the diagnosis of Creutzfeldt-Jakob disease. Neurology 2000; 55: 811-815.
-
(2000)
Neurology
, vol.55
, pp. 811-815
-
-
Zerr, I.1
Pocchiari, M.2
Collins, S.3
-
19
-
-
0037154135
-
Tau protein and 14-3-3 protein in the differential diagnosis of Creutzfeldt-Jakob disease
-
Otto M, Wiltfang J, Cepek L, et al. Tau protein and 14-3-3 protein in the differential diagnosis of Creutzfeldt-Jakob disease. Neurology 2002; 58: 192-197.
-
(2002)
Neurology
, vol.58
, pp. 192-197
-
-
Otto, M.1
Wiltfang, J.2
Cepek, L.3
-
20
-
-
33747689817
-
CSF tests in the differential diagnosis of Creutzfeldt-Jakob disease
-
Sanchez-Juan P, Green A, Ladogana A, et al. CSF tests in the differential diagnosis of Creutzfeldt-Jakob disease. Neurology 2006; 67: 637-643.
-
(2006)
Neurology
, vol.67
, pp. 637-643
-
-
Sanchez-Juan, P.1
Green, A.2
Ladogana, A.3
-
21
-
-
0028876473
-
Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease (CJD) and other human spongiform encephalopathies (prion diseases)
-
Budka H, Aguzzi A, Brown P, et al. Neuropathological diagnostic criteria for Creutzfeldt-Jakob disease (CJD) and other human spongiform encephalopathies (prion diseases). Brain Pathol 1995; 5: 459-466.
-
(1995)
Brain Pathol
, vol.5
, pp. 459-466
-
-
Budka, H.1
Aguzzi, A.2
Brown, P.3
-
22
-
-
84886004769
-
WHO Manual for Strengthening Diagnosis and Surveillance of Creutzfeldt-Jakob Disease
-
Zeidler M, Gibbs CJ, Meslin F. WHO Manual for Strengthening Diagnosis and Surveillance of Creutzfeldt-Jakob Disease. Geneva: WHO, 1998.
-
(1998)
Geneva: WHO
-
-
Zeidler, M.1
Gibbs, C.J.2
Meslin, F.3
-
23
-
-
0028893815
-
The nosology of Creutzfeldt-Jakob disease and conditions related to the accumulation of PrPCJD in the nervous system
-
Richardson EP Jr, Masters CL. The nosology of Creutzfeldt-Jakob disease and conditions related to the accumulation of PrPCJD in the nervous system. Brain Pathol 1995; 5: 33-41.
-
(1995)
Brain Pathol
, vol.5
, pp. 33-41
-
-
Richardson Jr, E.P.1
Masters, C.L.2
-
25
-
-
0019175731
-
Creutzfeldt-Jakob disease with extensive degeneration of white matter
-
Park TS, Kleinman GM, Richardson EP. Creutzfeldt-Jakob disease with extensive degeneration of white matter. Acta Neuropathol (Berl) 1980; 52: 239-242.
-
(1980)
Acta Neuropathol (Berl)
, vol.52
, pp. 239-242
-
-
Park, T.S.1
Kleinman, G.M.2
Richardson, E.P.3
-
26
-
-
0019514305
-
Panencephalopathic type of Creutzfeldt-Jakob disease: primary involvement of the cerebral white matter
-
Mizutani T, Okumura A, Oda M, Shiraki H. Panencephalopathic type of Creutzfeldt-Jakob disease: primary involvement of the cerebral white matter. J Neurol Neurosurg Psychiatry 1981; 44: 103-115.
-
(1981)
J Neurol Neurosurg Psychiatry
, vol.44
, pp. 103-115
-
-
Mizutani, T.1
Okumura, A.2
Oda, M.3
Shiraki, H.4
-
27
-
-
65349174484
-
Panencephalopathic Creutzfeldt-Jakob disease in the Netherlands and the UK: clinical and pathological characteristics of nine patients
-
Jansen C, Head MW, Rozemuller AJ, Ironside JW. Panencephalopathic Creutzfeldt-Jakob disease in the Netherlands and the UK: clinical and pathological characteristics of nine patients. Neuropathol Appl Neurobiol 2009; 35: 272-282.
-
(2009)
Neuropathol Appl Neurobiol
, vol.35
, pp. 272-282
-
-
Jansen, C.1
Head, M.W.2
Rozemuller, A.J.3
Ironside, J.W.4
-
29
-
-
0030929562
-
Distribution of parvalbumin-immunoreactive neurons in brain correlates with hippocampal and temporal cortical pathology in Creutzfeldt-Jakob disease
-
Guentchev M, Hainfellner JA, Trabattoni GR, Budka H. Distribution of parvalbumin-immunoreactive neurons in brain correlates with hippocampal and temporal cortical pathology in Creutzfeldt-Jakob disease. J Neuropathol Exp Neurol 1997; 56: 1119-1124.
-
(1997)
J Neuropathol Exp Neurol
, vol.56
, pp. 1119-1124
-
-
Guentchev, M.1
Hainfellner, J.A.2
Trabattoni, G.R.3
Budka, H.4
-
30
-
-
0020563627
-
Syndromes of amyotrophic lateral sclerosis and dementia: relation to transmissible Creutzfeldt-Jakob disease
-
Salazar AM, Masters CL, Gajdusek DC, Gibbs CJ Jr. Syndromes of amyotrophic lateral sclerosis and dementia: relation to transmissible Creutzfeldt-Jakob disease. Ann Neurol 1983; 14: 17-26.
-
(1983)
Ann Neurol
, vol.14
, pp. 17-26
-
-
Salazar, A.M.1
Masters, C.L.2
Gajdusek, D.C.3
Gibbs C.J, Jr.4
-
31
-
-
0031847332
-
Coexistence of Alzheimer-type neuropathology in Creutzfeldt-Jakob disease
-
Hainfellner JA, Wanschitz J, Jellinger K, Liberski PP, Gullotta F, Budka H. Coexistence of Alzheimer-type neuropathology in Creutzfeldt-Jakob disease. Acta Neuropathol (Berl) 1998; 96: 116-122.
-
(1998)
Acta Neuropathol (Berl)
, vol.96
, pp. 116-122
-
-
Hainfellner, J.A.1
Wanschitz, J.2
Jellinger, K.3
Liberski, P.P.4
Gullotta, F.5
Budka, H.6
-
32
-
-
0033048202
-
Neuroaxonal pathology in Creutzfeldt-Jakob disease
-
Liberski PP, Budka H. Neuroaxonal pathology in Creutzfeldt-Jakob disease. Acta Neuropathol (Berl) 1999; 97: 329-334.
-
(1999)
Acta Neuropathol (Berl)
, vol.97
, pp. 329-334
-
-
Liberski, P.P.1
Budka, H.2
-
33
-
-
0026644090
-
Regional mapping of prion proteins in brain
-
Taraboulos A, Jendroska K, Serban D, Yang SL, DeArmond SJ, Prusiner SB. Regional mapping of prion proteins in brain. Proc Natl Acad Sci USA 1992; 89: 7620-7624.
-
(1992)
Proc Natl Acad Sci USA
, vol.89
, pp. 7620-7624
-
-
Taraboulos, A.1
Jendroska, K.2
Serban, D.3
Yang, S.L.4
DeArmond, S.J.5
Prusiner, S.B.6
-
34
-
-
0033874288
-
The paraffin-embedded tissue blot detects PrP(Sc) early in the incubation time in prion diseases
-
Schulz-Schaeffer WJ, Tschoke S, Kranefuss N, et al. The paraffin-embedded tissue blot detects PrP(Sc) early in the incubation time in prion diseases. Am J Pathol 2000; 156: 51-56.
-
(2000)
Am J Pathol
, vol.156
, pp. 51-56
-
-
Schulz-Schaeffer, W.J.1
Tschoke, S.2
Kranefuss, N.3
-
35
-
-
0033972393
-
Creutzfeldt-Jakob disease: Carnoy's fixative improves the immunohistochemistry of the proteinase K-resistant prion protein
-
Giaccone G, Canciani B, Puoti G, et al. Creutzfeldt-Jakob disease: Carnoy's fixative improves the immunohistochemistry of the proteinase K-resistant prion protein. Brain Pathol 2000; 10: 31-37.
-
(2000)
Brain Pathol
, vol.10
, pp. 31-37
-
-
Giaccone, G.1
Canciani, B.2
Puoti, G.3
-
36
-
-
0033573778
-
Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples
-
Hill AF, Butterworth RJ, Joiner S, et al. Investigation of variant Creutzfeldt-Jakob disease and other human prion diseases with tonsil biopsy samples. Lancet 1999; 353: 183-189.
-
(1999)
Lancet
, vol.353
, pp. 183-189
-
-
Hill, A.F.1
Butterworth, R.J.2
Joiner, S.3
-
37
-
-
0032828301
-
Disease associated prion protein may deposit in the peripheral nervous system in human transmissible spongiform encephalopathies
-
Hainfellner JA, Budka H. Disease associated prion protein may deposit in the peripheral nervous system in human transmissible spongiform encephalopathies. Acta Neuropathol (Berl) 1999; 98: 458-460.
-
(1999)
Acta Neuropathol (Berl)
, vol.98
, pp. 458-460
-
-
Hainfellner, J.A.1
Budka, H.2
-
40
-
-
0036132894
-
Immunohistochemistry for the prion protein: comparison of different monoclonal antibodies in human prion disease subtypes
-
Kovács GG, Head M, Hegyi I, et al. Immunohistochemistry for the prion protein: comparison of different monoclonal antibodies in human prion disease subtypes. Brain Pathol 2002; 12: 1-11.
-
(2002)
Brain Pathol
, vol.12
, pp. 1-11
-
-
Kovács, G.G.1
Head, M.2
Hegyi, I.3
-
41
-
-
8944259890
-
Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease
-
Parchi P, Castellani R, Capellari S, et al. Molecular basis of phenotypic variability in sporadic Creutzfeldt-Jakob disease. Ann Neurol 1996; 39 (6): 767-778.
-
(1996)
Ann Neurol
, vol.39
, Issue.6
, pp. 767-778
-
-
Parchi, P.1
Castellani, R.2
Capellari, S.3
-
42
-
-
0026751775
-
Abnormal isoform of prion protein accumulates in the synaptic structures of the central nervous system in patients with Creutzfeldt-Jakob disease
-
Kitamoto T, Shin RW, Doh-ura K, et al. Abnormal isoform of prion protein accumulates in the synaptic structures of the central nervous system in patients with Creutzfeldt-Jakob disease. Am J Pathol 1992; 140: 1285-1294.
-
(1992)
Am J Pathol
, vol.140
, pp. 1285-1294
-
-
Kitamoto, T.1
Shin, R.W.2
Doh-ura, K.3
-
43
-
-
11144231706
-
Subcellular localization of disease associated prion protein in the human brain
-
Kovács GG, Preusser M, Strohschneider M, Budka H. Subcellular localization of disease associated prion protein in the human brain. Am J Pathol 2005; 166: 287-294.
-
(2005)
Am J Pathol
, vol.166
, pp. 287-294
-
-
Kovács, G.G.1
Preusser, M.2
Strohschneider, M.3
Budka, H.4
-
44
-
-
0342951746
-
A new variant of Creutzfeldt-Jakob disease in the UK
-
Will R, Ironside J, Zeidler M, et al. A new variant of Creutzfeldt-Jakob disease in the UK. Lancet 1996; 347: 921-925.
-
(1996)
Lancet
, vol.347
, pp. 921-925
-
-
Will, R.1
Ironside, J.2
Zeidler, M.3
-
45
-
-
0242361687
-
Extraneural pathologic prion protein in sporadic Creutzfeldt-Jakob disease
-
Glatzel M, Abela E, Maissen M, Aguzzi A. Extraneural pathologic prion protein in sporadic Creutzfeldt-Jakob disease. N Engl J Med 2003; 349: 1812-1820.
-
(2003)
N Engl J Med
, vol.349
, pp. 1812-1820
-
-
Glatzel, M.1
Abela, E.2
Maissen, M.3
Aguzzi, A.4
-
46
-
-
33644651130
-
Detection and localization of PrPSc in the skeletal muscle of patients with variant, iatrogenic, and sporadic Creutzfeldt-Jakob disease
-
Peden AH, Ritchie DL, Head MW, Ironside JW. Detection and localization of PrPSc in the skeletal muscle of patients with variant, iatrogenic, and sporadic Creutzfeldt-Jakob disease. Am J Pathol 2006; 168: 927-935.
-
(2006)
Am J Pathol
, vol.168
, pp. 927-935
-
-
Peden, A.H.1
Ritchie, D.L.2
Head, M.W.3
Ironside, J.W.4
-
47
-
-
33847632588
-
Abnormal prion protein in the pituitary in sporadic and variant Creutzfeldt-Jakob disease
-
Peden AH, Ritchie DL, Uddin HP, et al. Abnormal prion protein in the pituitary in sporadic and variant Creutzfeldt-Jakob disease. J Gen Virol 2007; 88: 1068-1072.
-
(2007)
J Gen Virol
, vol.88
, pp. 1068-1072
-
-
Peden, A.H.1
Ritchie, D.L.2
Uddin, H.P.3
-
48
-
-
0026720748
-
Comparative ultrastructural neuropathology of naturally occurring bovine spongiform encephalopathy and experimentally induced scrapie and Creutzfeldt-Jakob disease
-
Liberski PP, Yanagihara R, Wells GA, Gibbs CJ Jr, Gajdusek DC. Comparative ultrastructural neuropathology of naturally occurring bovine spongiform encephalopathy and experimentally induced scrapie and Creutzfeldt-Jakob disease. J Comp Pathol 1992; 106: 361-381.
-
(1992)
J Comp Pathol
, vol.106
, pp. 361-381
-
-
Liberski, P.P.1
Yanagihara, R.2
Wells, G.A.3
Gibbs C.J, Jr.4
Gajdusek, D.C.5
-
49
-
-
0026760367
-
Tubulovesicular structures in Creutzfeldt-Jakob disease
-
Liberski PP, Budka H, Sluga E, Barcikowska M, Kwiecinski H. Tubulovesicular structures in Creutzfeldt-Jakob disease. Acta Neuropathol (Berl) 1992; 84: 238-243.
-
(1992)
Acta Neuropathol (Berl)
, vol.84
, pp. 238-243
-
-
Liberski, P.P.1
Budka, H.2
Sluga, E.3
Barcikowska, M.4
Kwiecinski, H.5
-
51
-
-
12944253111
-
Genetic influence on the structural variations of the abnormal prion protein
-
Parchi P, Zou W, Wang W, et al. Genetic influence on the structural variations of the abnormal prion protein. Proc Natl Acad Sci USA 2000; 97: 10168-10172.
-
(2000)
Proc Natl Acad Sci USA
, vol.97
, pp. 10168-10172
-
-
Parchi, P.1
Zou, W.2
Wang, W.3
-
52
-
-
66949127502
-
Inter-laboratory assessment of PrP Sc typing in Creutzfeldt-Jakob disease: a Western blot study within the NeuroPrion Consortium
-
Parchi P, Notari S, Weber P, et al. Inter-laboratory assessment of PrP Sc typing in Creutzfeldt-Jakob disease: a Western blot study within the NeuroPrion Consortium. Brain Pathol 2009; 19: 384-391.
-
(2009)
Brain Pathol
, vol.19
, pp. 384-391
-
-
Parchi, P.1
Notari, S.2
Weber, P.3
-
53
-
-
0037677595
-
Molecular classification of sporadic Creutzfeldt-Jakob disease
-
Hill AF, Joiner S, Wadsworth JD, et al. Molecular classification of sporadic Creutzfeldt-Jakob disease. Brain 2003; 126: 1333-1346.
-
(2003)
Brain
, vol.126
, pp. 1333-1346
-
-
Hill, A.F.1
Joiner, S.2
Wadsworth, J.D.3
-
54
-
-
0035813151
-
Novel differences between two human prion strains revealed by two-dimensional gel electrophoresis
-
Pan T, Colucci M, Wong BS, et al. Novel differences between two human prion strains revealed by two-dimensional gel electrophoresis. J Biol Chem 2001; 276: 37284-37288.
-
(2001)
J Biol Chem
, vol.276
, pp. 37284-37288
-
-
Pan, T.1
Colucci, M.2
Wong, B.S.3
-
55
-
-
57649233091
-
Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease
-
Notari S, Strammiello R, Capellari S, et al. Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease. J Biol Chem 2008; 283: 30557-30565.
-
(2008)
J Biol Chem
, vol.283
, pp. 30557-30565
-
-
Notari, S.1
Strammiello, R.2
Capellari, S.3
-
56
-
-
70449524296
-
Incidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotypes and co-occurrence of PrP Sc types: an updated classification
-
Parchi P, Stammiello R, Notari S, et al. Incidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotypes and co-occurrence of PrP Sc types: an updated classification. Acta Neuropathol 2009; 118: 659-671.
-
(2009)
Acta Neuropathol
, vol.118
, pp. 659-671
-
-
Parchi, P.1
Stammiello, R.2
Notari, S.3
-
57
-
-
34447344086
-
Involvement of the endosomal-lysosomal system correlates with regional pathology in Creutzfeldt-Jakob disease
-
Kovács GG, Gelpi E, Ströbel T, et al. Involvement of the endosomal-lysosomal system correlates with regional pathology in Creutzfeldt-Jakob disease. J Neuropathol Exp Neurol 2007; 66: 628-636.
-
(2007)
J Neuropathol Exp Neurol
, vol.66
, pp. 628-636
-
-
Kovács, G.G.1
Gelpi, E.2
Ströbel, T.3
-
58
-
-
77953133811
-
Distribution of apoptosis-related proteins in sporadic Creutzfeldt-Jakob disease
-
Kovacs GG, Budka H. Distribution of apoptosis-related proteins in sporadic Creutzfeldt-Jakob disease. Brain Res 2010; 1323: 192-199.
-
(2010)
Brain Res
, vol.1323
, pp. 192-199
-
-
Kovacs, G.G.1
Budka, H.2
-
59
-
-
26444453638
-
Sporadic Creutzfeldt-Jakob disease: the extent of microglia activation is dependent on the biochemical type of PrPSc
-
Puoti G, Giaccone G, Mangieri M, et al. Sporadic Creutzfeldt-Jakob disease: the extent of microglia activation is dependent on the biochemical type of PrPSc. J. Neuropathol Exp Neurol 2005; 64: 902-909.
-
(2005)
J. Neuropathol Exp Neurol
, vol.64
, pp. 902-909
-
-
Puoti, G.1
Giaccone, G.2
Mangieri, M.3
-
60
-
-
0032763817
-
Sporadic Creutzfeldt-Jakob disease: co-occurrence of different types of PrP sc in the same brain
-
Puoti G, Giaccone G, Rossi G, Canciani B, Bugiani O, Tagliavini F. Sporadic Creutzfeldt-Jakob disease: co-occurrence of different types of PrP sc in the same brain. Neurology 1999; 53: 2173-2176.
-
(1999)
Neurology
, vol.53
, pp. 2173-2176
-
-
Puoti, G.1
Giaccone, G.2
Rossi, G.3
Canciani, B.4
Bugiani, O.5
Tagliavini, F.6
-
61
-
-
70349937836
-
Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics
-
Cali I, Castellani R, Alshekhlee A, et al. Co-existence of scrapie prion protein types 1 and 2 in sporadic Creutzfeldt-Jakob disease: its effect on the phenotype and prion-type characteristics. Brain 2009; 132: 2643-2658.
-
(2009)
Brain
, vol.132
, pp. 2643-2658
-
-
Cali, I.1
Castellani, R.2
Alshekhlee, A.3
-
62
-
-
70349952066
-
Sporadic Creutzfeldt-Jakob disease: discrete subtypes or a spectrum of disease?
-
Head MW, Ironside JW. Sporadic Creutzfeldt-Jakob disease: discrete subtypes or a spectrum of disease? Brain 2009; 132: 2627-2629.
-
(2009)
Brain
, vol.132
, pp. 2627-2629
-
-
Head, M.W.1
Ironside, J.W.2
-
63
-
-
27744459883
-
Coexistence of multiple PrPSc types in individuals with Creutzfeldt-Jakob disease
-
Polymenidou M, Stoeck K, Glatzel M, Vey M, Bellon A, Aguzzi A. Coexistence of multiple PrPSc types in individuals with Creutzfeldt-Jakob disease. Lancet Neurol 2009; 4: 805-814.
-
(2009)
Lancet Neurol
, vol.4
, pp. 805-814
-
-
Polymenidou, M.1
Stoeck, K.2
Glatzel, M.3
Vey, M.4
Bellon, A.5
Aguzzi, A.6
-
64
-
-
67650630953
-
Further characterisation of the prion protein molecular types detectable in the NIBSC Creutzfeldt-Jakob disease brain reference materials
-
Yull HM, Ironside JW, Head MW. Further characterisation of the prion protein molecular types detectable in the NIBSC Creutzfeldt-Jakob disease brain reference materials. Biologicals 2009; 37: 210-215.
-
(2009)
Biologicals
, vol.37
, pp. 210-215
-
-
Yull, H.M.1
Ironside, J.W.2
Head, M.W.3
-
65
-
-
35348941241
-
A refined method for typing reveals that co-occurrence of PrP Sc types in Creutzfeldt-Jakob disease is not the rule
-
Notari S, Capellari S, Langeveld J, et al. A refined method for typing reveals that co-occurrence of PrP Sc types in Creutzfeldt-Jakob disease is not the rule. Lab Invest 2007; 87: 1103-1112.
-
(2007)
Lab Invest
, vol.87
, pp. 1103-1112
-
-
Notari, S.1
Capellari, S.2
Langeveld, J.3
-
67
-
-
40449120471
-
Prion diseases: from protein to cell pathology
-
Kovács GG, Budka H. Prion diseases: from protein to cell pathology. Am J Pathol 2008; 172: 555-565.
-
(2008)
Am J Pathol
, vol.172
, pp. 555-565
-
-
Kovács, G.G.1
Budka, H.2
-
68
-
-
0027483615
-
Neurotoxicity of a prion protein fragment
-
Forloni GL, Angeretti N, Chiesa R, et al. Neurotoxicity of a prion protein fragment. Nature 1993; 362: 543-546.
-
(1993)
Nature
, vol.362
, pp. 543-546
-
-
Forloni, G.L.1
Angeretti, N.2
Chiesa, R.3
-
69
-
-
0034932717
-
Studies on peptide fragments of prion proteins
-
Tagliavini F, Forloni G, d'Ursi P, Bugiani O, Salmona M. Studies on peptide fragments of prion proteins. Adv Protein Chem 2001; 57: 171-202.
-
(2001)
Adv Protein Chem
, vol.57
, pp. 171-202
-
-
Tagliavini, F.1
Forloni, G.2
d'Ursi, P.3
Bugiani, O.4
Salmona, M.5
-
70
-
-
0035859102
-
Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding
-
Saborio GP, Permanne B, Soto C. Sensitive detection of pathological prion protein by cyclic amplification of protein misfolding. Nature 2001; 411: 810-813.
-
(2001)
Nature
, vol.411
, pp. 810-813
-
-
Saborio, G.P.1
Permanne, B.2
Soto, C.3
-
71
-
-
53549095695
-
Cell-free propagation of prion strains
-
Castilla J, Morales R, Saa P, Barria M, Gambetti P, Soto C. Cell-free propagation of prion strains. EMBO J 2008; 27: 2557-2566.
-
(2008)
EMBO J
, vol.27
, pp. 2557-2566
-
-
Castilla, J.1
Morales, R.2
Saa, P.3
Barria, M.4
Gambetti, P.5
Soto, C.6
-
72
-
-
57149144250
-
Effects of human PrP Sc type and PRNP genotype in an in-vitro conversion assay
-
Jones M, Peden AH, Wight D, et al. Effects of human PrP Sc type and PRNP genotype in an in-vitro conversion assay. NeuroReport 2008; 19: 1783-1786.
-
(2008)
NeuroReport
, vol.19
, pp. 1783-1786
-
-
Jones, M.1
Peden, A.H.2
Wight, D.3
-
73
-
-
1642436726
-
Therapeutic approaches to prion diseases
-
Rossi G, Salmona M, Forloni G, Bugiani O, Tagliavini F. Therapeutic approaches to prion diseases. Clin Lab Med 2003; 23: 187-208.
-
(2003)
Clin Lab Med
, vol.23
, pp. 187-208
-
-
Rossi, G.1
Salmona, M.2
Forloni, G.3
Bugiani, O.4
Tagliavini, F.5
-
74
-
-
62149105940
-
Safety and efficacy of quinacrine in human prion disease (PRION-1 study): a patient-preference trial
-
Collinge J, Gorham M, Hudson F, et al. Safety and efficacy of quinacrine in human prion disease (PRION-1 study): a patient-preference trial. Lancet Neurol 2009; 8: 334-344.
-
(2009)
Lancet Neurol
, vol.8
, pp. 334-344
-
-
Collinge, J.1
Gorham, M.2
Hudson, F.3
-
75
-
-
19944375077
-
Compassionate use of quinacrine in Creutzfeldt-Jakob disease fails to show significant effects
-
Haïk S, Brandel JP, Salomon D, et al. Compassionate use of quinacrine in Creutzfeldt-Jakob disease fails to show significant effects. Neurology 2004; 63: 2413-2415.
-
(2004)
Neurology
, vol.63
, pp. 2413-2415
-
-
Haïk, S.1
Brandel, J.P.2
Salomon, D.3
-
76
-
-
0035859806
-
Acridine and phenothiazine derivatives as pharmacotherapeutics for prion disease
-
Korth C, May BC, Cohen FE, Prusiner SB. Acridine and phenothiazine derivatives as pharmacotherapeutics for prion disease. Proc Natl Acad Sci USA 2001; 98: 9836-9841.
-
(2001)
Proc Natl Acad Sci USA
, vol.98
, pp. 9836-9841
-
-
Korth, C.1
May, B.C.2
Cohen, F.E.3
Prusiner, S.B.4
|