Panencephalopathic Creutzfeldt-Jakob disease in the Netherlands and the UK: Clinical and pathological characteristics of nine patients

Neuropathology and Applied Neurobiology

Volumn 35, Issue 3, 2009, Pages 272-282

  Jansen, C ^a   Head, M W ^b   Rozemuller, A J M ^a   Ironside, J W ^b  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^b UNIVERSITY OF EDINBURGH   (United Kingdom)

Author keywords

Creutzfeldt Jakob disease; Panencephalopathic type; Prion diseases; Prion protein; Western blot; White matter

Indexed keywords

PRION PROTEIN;

ADULT; AGED; AKINETIC MUTISM; ARTICLE; BRAIN ATROPHY; BRAIN CORTEX LESION; BRAIN DAMAGE; BRAIN WEIGHT; CLINICAL ARTICLE; CLINICAL FEATURE; CODON; CREUTZFELDT JAKOB DISEASE; DISEASE CLASSIFICATION; DISEASE COURSE; DISEASE DURATION; DISEASE SEVERITY; FEMALE; HISTOLOGY; HUMAN; MALE; NERVE CELL DEGENERATION; NETHERLANDS; NEUROPATHOLOGY; PATHOGENESIS; PRIORITY JOURNAL; UNITED KINGDOM; WHITE MATTER;

AGE OF ONSET; AGED; BLOTTING, WESTERN; BRAIN; CREUTZFELDT-JAKOB SYNDROME; DISEASE PROGRESSION; ELECTROENCEPHALOGRAPHY; FEMALE; GREAT BRITAIN; HUMANS; MALE; MIDDLE AGED; NERVE FIBERS, MYELINATED; NETHERLANDS; ORGAN SIZE; POLYMORPHISM, GENETIC; PRIONS; PROTEIN ISOFORMS; PRPSC PROTEINS; SEQUENCE ANALYSIS, DNA;

EID: 65349174484     PISSN: 03051846     EISSN: 13652990     Source Type: Journal    
DOI: 10.1111/j.1365-2990.2008.01004a.x     Document Type: Article

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