Abnormal barrier function in the pathogenesis of ichthyosis: Therapeutic implications for lipid metabolic disorders

Clinics in Dermatology

Volumn 30, Issue 3, 2012, Pages 311-322

  Elias, Peter M ^a   Williams, Mary L ^b   Feingold, Kenneth R ^a  

^a SAN FRANCISCO VETERANS AFFAIRS MEDICAL CENTER   (United States)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACETYL COENZYME A CARBOXYLASE INHIBITOR; ACYL CERAMIDE; CERAMIDE; CERAMIDE DERIVATIVE; CHOLESTEROL; FARNESOIC ACID; FATTY ACID; FATTY ACID DERIVATIVE; FATTY ACID SYNTHASE INHIBITOR; GLUCOSYLCERAMIDE; LIGASE INHIBITOR; MEVINOLIN; UNCLASSIFIED DRUG;

ABNORMAL EPIDERMAL BARRIER; CHOLESTEROL METABOLISM; CHONDROPATHY; CLINICAL FEATURE; CONGENITAL HEMIDYSPLASIA WITH ICHTHYOSIFORM ERYTHRODERMA AND LIMB DEFECT; CONGENITAL ICHTHYOSIFORM ERYTHRODERMA; CONRADI HUNERMANN HAPPLE SYNDROME; DESMOSTEROLOSIS; DIET THERAPY; DISEASE SEVERITY; DISORDERS OF LIPID AND LIPOPROTEIN METABOLISM; DRUG APPROVAL; DRUG SAFETY; DRUG TREATMENT FAILURE; ENZYME DEFICIENCY; FEEDBACK SYSTEM; GAUCHER DISEASE; GENE; GENE MUTATION; GENE THERAPY; GENETIC DISORDER; HUMAN; HYPERKERATOSIS; ICHTHYOSIS; INHERITANCE; INSULIN INDUCED GENE 1; INSULIN INDUCED GENE 2; KNOCKOUT MOUSE; LATHOSTEROLOSIS; NEUTRAL LIPID STORAGE DISEASE WITH ICHTHYOSIS; NONHUMAN; NOTE; OUTCOME ASSESSMENT; PATHOGENESIS; PHENOTYPE; PRIORITY JOURNAL; REFSUM DISEASE; SIGNAL TRANSDUCTION; SJOEGREN LARSSON SYNDROME; SKIN DISEASE; SMITH LEMLI OPITZ SYNDROME; STEROL C4 METHYL OXIDASE LIKE DEFICIENCY; X LINKED ICHTHYOSIS;

ADMINISTRATION, TOPICAL; ALGORITHMS; ANIMALS; CHOLESTEROL; DISEASE MODELS, ANIMAL; DOSE-RESPONSE RELATIONSHIP, DRUG; DRUG THERAPY, COMBINATION; EPIDERMIS; FEMALE; HUMANS; HYDROXYMETHYLGLUTARYL-COA REDUCTASE INHIBITORS; ICHTHYOSIFORM ERYTHRODERMA, CONGENITAL; ICHTHYOSIS; LIPID METABOLISM DISORDERS; LOVASTATIN; MALE; MICE; PERMEABILITY; PHENOTYPE; SEVERITY OF ILLNESS INDEX; SJOGREN-LARSSON SYNDROME;

EID: 84859745284     PISSN: 0738081X     EISSN: 18791131     Source Type: Journal    
DOI: 10.1016/j.clindermatol.2011.08.017     Document Type: Note

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