Missing mitochondrial Mpv17 gene function induces tissue-specific cell-death pathway in the degenerating inner ear

Cell and Tissue Research

Volumn 347, Issue 2, 2012, Pages 343-356

  Meyer Zum Gottesberge, Angela Maria ^a   Massing, Thomas ^a   Hansen, Stefan ^a  

^a HEINRICH HEINE UNIVERSITY   (Germany)

Author keywords

Cytoplasmatic vacuolization; Mitochondria; Mouse; Outer hair cell; Radical oxygen species; Stria vascularis

Indexed keywords

MEMBRANE PROTEIN; MITOCHONDRIAL DNA; PROTEIN MPV17; REACTIVE OXYGEN METABOLITE; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; AUDITORY DYSFUNCTION; AUDITORY THRESHOLD; BRAIN STEM RESPONSE; CELL DEGENERATION; CELL PHAGOCYTOSIS; CELL TYPE; CELL VACUOLE; COCHLEA; CONTROLLED STUDY; CYTOLYSIS; EAR DISEASE; FEMALE; GENE FUNCTION; GENE INACTIVATION; HAIR CELL; INNER EAR DEGENERATION; INNER EAR DISEASE; INTERMEDIATE CELL; MALE; MARGINAL CELL; MELANOCYTE; MITOCHONDRIAL GENE; MOUSE; MPV17 GENE; NEUROEPITHELIUM; NONHUMAN; PRIORITY JOURNAL; PROTEIN FUNCTION; STRIA VASCULARIS; TISSUE SPECIFICITY;

ANIMALS; CELL DEATH; COCHLEA; EAR, INNER; FEMALE; GENES, MITOCHONDRIAL; HEARING LOSS, SENSORINEURAL; MALE; MEMBRANE PROTEINS; MICE; MICE, INBRED STRAINS; MITOCHONDRIA; ORGAN OF CORTI; SIGNAL TRANSDUCTION; STRIA VASCULARIS;

MUS;

EID: 84859430852     PISSN: 0302766X     EISSN: 14320878     Source Type: Journal    
DOI: 10.1007/s00441-012-1326-7     Document Type: Article

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