Excessive activity of cathepsin K is associated with cartilage defects in a zebrafish model of mucolipidosis II

DMM Disease Models and Mechanisms

Volumn 5, Issue 2, 2012, Pages 177-190

  Petrey, Aaron C ^a   Flanagan Steet, Heather ^a   Johnson, Steven ^a   Fan, Xiang ^a   De La Rosa, Mitche ^a   Haskins, Mark E ^b   Nairn, Alison V ^a   Moremen, Kelley W ^a   Steet, Richard ^a  

^a UNIVERSITY OF GEORGIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CATHEPSIN K; COLLAGEN TYPE 2; COLLAGENASE 3; MATRIX METALLOPROTEINASE; PROTEINASE;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CARTILAGE; CARTILAGE CELL; CELL ISOLATION; CELL POPULATION; CELL STRUCTURE; EMBRYO; EMBRYO DEVELOPMENT; ENZYME ACTIVITY; EXTRACELLULAR MATRIX; GENETIC TRANSCRIPTION; MORPHOGENESIS; MUCOLIPIDOSIS TYPE 2; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; ZEBRA FISH;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; BASE SEQUENCE; CARTILAGE; CATHEPSIN K; COLLAGEN TYPE II; CRANIOFACIAL ABNORMALITIES; DISEASE MODELS, ANIMAL; EXTRACELLULAR MATRIX PROTEINS; HUMANS; MANNOSEPHOSPHATES; MUCOLIPIDOSES; RNA, MESSENGER; ZEBRAFISH; ZEBRAFISH PROTEINS;

DANIO RERIO;

EID: 84858036607     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.008219     Document Type: Article

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