Vacuolization of mucolipidosis type II mouse exocrine gland cells represents accumulation of autolysosomes

Molecular Biology of the Cell

Volumn 22, Issue 8, 2011, Pages 1135-1147

  Boonen, Marielle ^a   Van Meel, Eline ^b   Oorschot, Viola ^b   Klumperman, Judith ^b   Kornfeld, Stuart ^a  

^a WASHINGTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

[No Author keywords available]

Indexed keywords

ACID HYDROLASE; LYSOSOME ENZYME; URIDINE DIPHOSPHATE N ACETYLGLUCOSAMINE;

ANIMAL CELL; ARTICLE; AUTOLYSOSOME; BIOACCUMULATION; BIOCHEMICAL COMPOSITION; CELL SPECIFICITY; CELL TYPE; CELL VACUOLE; CONTROLLED STUDY; EXOCRINE CELL; EXOCRINE GLAND; IMMUNOELECTRON MICROSCOPY; LYSOSOME; MOUSE; MUCOLIPIDOSIS TYPE 2; NONHUMAN; PRIORITY JOURNAL; SECRETORY GRANULE; SKIN FIBROBLAST; TISSUE SPECIFICITY;

ACID ANHYDRIDE HYDROLASES; ANIMALS; EXOCRINE GLANDS; FIBROBLASTS; GENE DELETION; HUMANS; LYSOSOMES; MANNOSEPHOSPHATES; MICE; MICE, KNOCKOUT; MICROSCOPY, IMMUNOELECTRON; MUCOLIPIDOSES; ORGAN SPECIFICITY; SECRETORY VESICLES; TRANSFERASES (OTHER SUBSTITUTED PHOSPHATE GROUPS); VACUOLES;

MUS;

EID: 79954577494     PISSN: 10591524     EISSN: 19394586     Source Type: Journal    
DOI: 10.1091/mbc.E10-07-0584     Document Type: Article

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