Nutrition therapy of organic acidaemias with amino acid-based formulas: Emphasis on methylmalonic and propionic acidaemia

Journal of Inherited Metabolic Disease

Volumn 29, Issue 2-3, 2006, Pages 281-287

  Yannicelli, Steven ^a  

^a SHS North America   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

AMINO ACID; BIOTIN; CARNITINE; METRONIDAZOLE; MINERAL; NITROGEN; VITAMIN;

AMINO ACID DEFICIENCY; ANOREXIA; ARTICLE; CALORIC INTAKE; CARNITINE DEFICIENCY; CLINICAL FEATURE; DEVELOPMENTAL DISORDER; DIET THERAPY; ENERGY BALANCE; ENERGY EXPENDITURE; FAILURE TO THRIVE; GROWTH RETARDATION; HUMAN; HYPERAMMONEMIA; HYPERSENSITIVITY REACTION; INFECTION RISK; METABOLIC ACIDOSIS; METHYLMALONIC ACIDEMIA; MORBIDITY; MORTALITY; NUTRITIONAL ASSESSMENT; NUTRITIONAL REQUIREMENT; NUTRITIONAL VALUE; OSTEOPENIA; OSTEOPOROSIS; PATIENT MONITORING; PREDICTION; PROPIONIC ACIDEMIA; PROTEIN INTAKE; PROTEIN RESTRICTION; RISK ASSESSMENT; STANDARDIZATION; TREATMENT OUTCOME;

AMINO ACID METABOLISM, INBORN ERRORS; AMINO ACIDS; CHEMISTRY, PHARMACEUTICAL; DIETARY SUPPLEMENTS; ENERGY METABOLISM; HUMANS; METHYLMALONIC ACID; NUTRITIONAL SUPPORT; PROPIONIC ACIDS; PROTEINS; TREATMENT OUTCOME;

EID: 33745091218     PISSN: 01418955     EISSN: 15732665     Source Type: Journal    
DOI: 10.1007/s10545-006-0267-2     Document Type: Article

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