CTGF/CCN-2 over-expression can directly induce features of skeletal muscle dystrophy

Journal of Pathology

Volumn 225, Issue 4, 2011, Pages 490-501

  Morales, María Gabriela ^a   Cabello Verrugio, Claudio ^a,c   Santander, Cristian ^a   Cabrera, Daniel ^a   Goldschmeding, Roel ^b   Brandan, Enrique ^a  

^a PONTIFICIA UNIVERSIDAD CATÓLICA DE CHILE   (Chile)

^b UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^c UNIVERSIDAD DEL DESARROLLO   (Chile)

Author keywords

connective tissue growth factor; fibrosis; skeletal muscle damage; skeletal muscular dystrophies

Indexed keywords

ADENOVIRUS VECTOR; ALPHA SMOOTH MUSCLE ACTIN; COLLAGEN; CONNECTIVE TISSUE GROWTH FACTOR; DECORIN; FIBRONECTIN; MYOSIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CLINICAL FEATURE; DUCHENNE MUSCULAR DYSTROPHY; MALE; MOUSE; MUSCLE FUNCTION; MUSCLE INJURY; MUSCLE ISOMETRIC CONTRACTION; MUSCLE REGENERATION; MUSCULAR DYSTROPHY; MYOFIBROSIS; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; SCAR; TIBIALIS ANTERIOR MUSCLE;

ADENOVIRIDAE; ANIMALS; CELL LINE; CONNECTIVE TISSUE GROWTH FACTOR; DISEASE MODELS, ANIMAL; ELECTROMYOGRAPHY; FIBROSIS; GENE EXPRESSION REGULATION; GENETIC VECTORS; MALE; MICE; MICE, INBRED C57BL; MUSCLE CONTRACTION; MUSCLE, SKELETAL; MUSCULAR DYSTROPHIES; REGENERATION;

EID: 81355149683     PISSN: 00223417     EISSN: 10969896     Source Type: Journal    
DOI: 10.1002/path.2952     Document Type: Article

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