Myelin genes are downregulated in canine fucosidosis

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1812, Issue 11, 2011, Pages 1418-1426

  Fletcher, Jessica L ^a,b,c   Kondagari, Gauthami S ^a   Wright, Amanda L ^a   Thomson, Peter C ^a   Williamson, Peter ^a   Taylor, Rosanne M ^a  

^a UNIVERSITY OF SYDNEY   (Australia)

^b UNIVERSITY OF NEW SOUTH WALES   (Australia)

^c GARVAN INSTITUTE OF MEDICAL RESEARCH   (Australia)

Author keywords

Canine disease model; Fucosidosis; Hypomyelination; Lysosomal storage disease; Microarray

Indexed keywords

2',3' CYCLIC NUCLEOTIDE 3' PHOSPHODIESTERASE; ALPHA 2 MACROGLOBULIN; ALPHA LEVO FUCOSIDASE; ALPHA MANNOSIDASE; APOLIPOPROTEIN E; BETA GLUCURONIDASE; CASPASE 10; CASPASE 8; CD14 ANTIGEN; CD68 ANTIGEN; CHEMOKINE RECEPTOR CCR1; CHEMOKINE RECEPTOR CCR5; INTERLEUKIN 1ALPHA; INTERLEUKIN 6; MYELIN; MYELIN AND LYMPHOCYTE PROTEIN; MYELIN ASSOCIATED GLYCOPROTEIN; MYELIN OLIGODENDROCYTE GLYCOPROTEIN; OLIGODENDROCYTE MYELIN PARANODAL AND INNER LOOP PROTEIN; PROTEIN; PROTEIN BAX; PROTEIN BCL 2; PROTEIN BID; PROTEIN KINASE SYK; TOLL LIKE RECEPTOR 4; TRANSFORMING GROWTH FACTOR BETA1; TUMOR NECROSIS FACTOR RECEPTOR 1; TUMOR NECROSIS FACTOR RECEPTOR 2; UNCLASSIFIED DRUG;

ANIMAL MODEL; ANIMAL TISSUE; APOPTOSIS; ARTICLE; ASTROCYTE; CALCIUM METABOLISM; CELL DEATH; CELL VACUOLE; CONTROLLED STUDY; CYTOPLASM; DOWN REGULATION; ENZYME REPLACEMENT; EXPERIMENTAL DOG; FRONTAL CORTEX; FUCOSIDOSIS; GENE EXPRESSION; GENE EXPRESSION PROFILING; GENETIC ANALYSIS; MICROGLIA; MYELINATION; NERVE CELL; NERVE CONDUCTION; NONHUMAN; OLIGODENDROGLIA; PRIORITY JOURNAL; SIGNAL TRANSDUCTION; TISSUE MICROARRAY; UPREGULATION;

ANIMALS; BIOLOGICAL MARKERS; BRAIN; CELL DEATH; DOGS; DOWN-REGULATION; FUCOSIDOSIS; GENE EXPRESSION PROFILING; IMMUNOENZYME TECHNIQUES; INFLAMMATION; MYELIN PROTEINS; OLIGODENDROGLIA; OLIGONUCLEOTIDE ARRAY SEQUENCE ANALYSIS; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; RNA, MESSENGER;

EID: 80053440324     PISSN: 09254439     EISSN: 1879260X     Source Type: Journal    
DOI: 10.1016/j.bbadis.2011.06.001     Document Type: Article

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