Bioenergetic defect associated with mKATP channel opening in a mouse model carrying a mitofusin 2 mutation

FASEB Journal

Volumn 25, Issue 5, 2011, Pages 1618-1627

  Guillet, Virginie ^a,b,c   Gueguen, Naïg ^a,c   Cartoni, Romain ^d,e,f   Chevrollier, Arnaud ^a,c   Desquiret, Valérie ^c   Angebault, Claire ^a,b   Amati Bonneau, Patrizia ^a,c   Procaccio, Vincent ^a,b,c   Bonneau, Dominique ^a,b,c   Martinou, Jean Claude ^d   Reynier, Pascal ^a,b,c  

^a CNRS   (France)

^b UNIVERSITÉ D'ANGERS   (France)

^c ANGERS UNIVERSITY HOSPITAL   (France)

^d UNIVERSITY OF GENEVA   (Switzerland)

^e BOSTON CHILDREN S HOSPITAL   (United States)

^f HARVARD MEDICAL SCHOOL   (United States)

Author keywords

Charcot Marie Tooth type 2A; F0F1 ATP synthase; Mitochondria; Potassium channel; Succinate dehydrogenase

Indexed keywords

5 HYDROXYDECANOIC ACID; ADENOSINE TRIPHOSPHATE SENSITIVE POTASSIUM CHANNEL; DIAZOXIDE; MITOFUSIN 2;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; ENZYME ANALYSIS; GENE MUTATION; HEREDITARY MOTOR SENSORY NEUROPATHY; MOUSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN SYNTHESIS INHIBITION;

ANIMALS; BLOTTING, WESTERN; BRAIN; CHARCOT-MARIE-TOOTH DISEASE; DIAZOXIDE; GTP PHOSPHOHYDROLASES; HUMANS; IMMUNOPRECIPITATION; KATP CHANNELS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MITOCHONDRIA; MITOCHONDRIAL PROTEINS;

MUS; MUS MUSCULUS;

EID: 79955658108     PISSN: 08926638     EISSN: 15306860     Source Type: Journal    
DOI: 10.1096/fj.10-173609     Document Type: Article

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