Succinate dehydrogenase deficiency in human

Cellular and Molecular Life Sciences

Volumn 62, Issue 19-20, 2005, Pages 2317-2324

  Briere J J ^a   Favier, J ^b   El Ghouzzi, V ^a   Djouadi, F ^c   Benit P ^a   Gimenez, A P ^c   Rustin, P ^a  

^a HÔPITAL ROBERT DEBRÉ   (France)

^b HÔPITAL EUROPÉEN GEORGES POMPIDOU   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Encephalomyopathy; Krebs cycle; Mitochondria; Succinate dehydrogenase; Tumour

Indexed keywords

MITOCHONDRIAL ENZYME; SUCCINATE DEHYDROGENASE; SUCCINIC ACID;

CARCINOGENESIS; CATABOLISM; CHILDHOOD DISEASE; CITRIC ACID CYCLE; CLINICAL FEATURE; COMPLEX II DEFICIENCY; ELECTRON TRANSPORT; ENCEPHALOMYOPATHY; ENZYME ACTIVITY; ENZYME SUBUNIT; GENE FUNCTION; GENE MUTATION; GENETIC CODE; HUMAN; MITOCHONDRION; PROTEIN FUNCTION; RESPIRATORY CHAIN; REVIEW;

HUMANS; METABOLISM, INBORN ERRORS; MUTATION; SUCCINATE DEHYDROGENASE; SUCCINIC ACID;

EID: 27144440549     PISSN: 1420682X     EISSN: 15691632     Source Type: Journal    
DOI: 10.1007/s00018-005-5237-6     Document Type: Review

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