Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3Δex7/8-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis

Neurochemistry International

Volumn 58, Issue 6, 2011, Pages 648-655

  Finn, Rozzy ^a,b,c   Kovács, Attila D ^a,b,c   Pearce, David A ^a,b,c  

^a UNIVERSITY OF ROCHESTER SCHOOL OF MEDICINE AND DENTISTRY   (United States)

^b UNIVERSITY OF SOUTH DAKOTA   (United States)

^c SANFORD RESEARCH   (United States)

Author keywords

AMPA receptor; Batten disease; Cerebellar granule cells; Cln3; Juvenile neuronal ceroid lipofuscinoses; NMDA receptor

Indexed keywords

ALPHA AMINO 3 HYDROXY 5 METHYL 4 ISOXAZOLEPROPIONIC ACID; AMPA RECEPTOR; AMPA RECEPTOR AGONIST; GLUTAMATE RECEPTOR; N METHYL DEXTRO ASPARTIC ACID; N METHYL DEXTRO ASPARTIC ACID RECEPTOR;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CEREBELLUM; CLN3 GENE; CONTROLLED STUDY; GENE; GENE MUTATION; GENE TARGETING; GRANULE CELL; IN VITRO STUDY; KNOCKOUT MOUSE; MALE; MOTOR COORDINATION; MOUSE; NERVE CELL CULTURE; NERVE CELL DIFFERENTIATION; NERVE CELL NECROSIS; NEURONAL CEROID LIPOFUSCINOSIS; NEUROTOXICITY; NONHUMAN; PRIORITY JOURNAL; PROTEIN FUNCTION; PSYCHOMOTOR DISORDER; WILD TYPE;

ANIMALS; CELLS, CULTURED; CEREBELLUM; CYTOPLASMIC GRANULES; GENE KNOCK-IN TECHNIQUES; MEMBRANE GLYCOPROTEINS; MICE; MICE, INBRED C57BL; MOLECULAR CHAPERONES; NEURONAL CEROID-LIPOFUSCINOSES; RECEPTORS, GLUTAMATE; ROTAROD PERFORMANCE TEST;

MUS;

EID: 79953689889     PISSN: 01970186     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.neuint.2011.02.003     Document Type: Article

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