Neurodevelopmental delay in the Cln3Δex7/8 mouse model for Batten disease

Genes, Brain and Behavior

Volumn 8, Issue 3, 2009, Pages 337-345

  Osorio N S ^a   Sampaio Marques, B ^a   Chan, C H ^b   Oliveira, P ^a,c   Pearce, D A ^b   Sousa, N ^a   Rodrigues, F ^a  

^a UNIVERSITY OF MINHO   (Portugal)

^b UNIVERSITY OF ROCHESTER SCHOOL OF MEDICINE AND DENTISTRY   (United States)

^c UNIVERSITY OF MINHO   (Portugal)

Author keywords

Batten; CLN3; Disease models; Genetics; Mouse behaviour; Neurodevelopment; Neuronal ceroid lipofuscinosis

Indexed keywords

CEROID LIPOFUSCINOSIS NEURONAL 3; MEMBRANE PROTEIN; UNCLASSIFIED DRUG; CHAPERONE; CLN3 PROTEIN, MOUSE;

ANIMAL EXPERIMENT; ARTICLE; BEHAVIOR CHANGE; BODY POSTURE; CONTROLLED STUDY; DEVELOPMENTAL DISORDER; EXPLORATORY BEHAVIOR; GAIT; GENE MUTATION; GRIP STRENGTH; HETEROZYGOTE; HOMOZYGOTE; LOCOMOTION; MOTOR COORDINATION; MOTOR DYSFUNCTION; MOUSE; NERVE CELL DIFFERENTIATION; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; RIGHTING REFLEX; AGING; ANIMAL; BRAIN; C57BL MOUSE; CHILD; DISEASE MODEL; FEMALE; GENETIC PREDISPOSITION; GENETICS; GENOTYPE; GROWTH, DEVELOPMENT AND AGING; HUMAN; MALE; METABOLISM; PATHOPHYSIOLOGY; PSYCHOMOTOR DISORDER; TRANSGENIC MOUSE;

ANIMALIA; MUS;

AGING; ANIMALS; BRAIN; CHILD; DEVELOPMENTAL DISABILITIES; DISEASE MODELS, ANIMAL; FEMALE; GENETIC PREDISPOSITION TO DISEASE; GENOTYPE; HETEROZYGOTE; HUMANS; MALE; MEMBRANE GLYCOPROTEINS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MOLECULAR CHAPERONES; MOTOR SKILLS DISORDERS; NEURONAL CEROID-LIPOFUSCINOSES;

EID: 65249141161     PISSN: 16011848     EISSN: 1601183X     Source Type: Journal    
DOI: 10.1111/j.1601-183X.2009.00478.x     Document Type: Article

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