The role of Fras1/Frem proteins in the structure and function of basement membrane

International Journal of Biochemistry and Cell Biology

Volumn 43, Issue 4, 2011, Pages 487-495

  Pavlakis, Evangelos ^a,b   Chiotaki, Rena ^a   Chalepakis, Georges ^a  

^a UNIVERSITY OF CRETE   (Greece)

^b MAX PLANCK INSTITUTE FOR BIOPHYSICAL CHEMISTRY   (Germany)

Author keywords

Basement membrane; bleb; Fras1; Fraser syndrome; Frem; Renal defects; Syndactyly

Indexed keywords

COLLAGEN TYPE 7; FRASER SYNDROME PROTEIN 1; FRASER SYNDROME PROTEIN 1 RELATED EXTRACELLULAR MATRIX PROTEIN 1; FRASER SYNDROME PROTEIN 1 RELATED EXTRACELLULAR MATRIX PROTEIN 2; FRASER SYNDROME PROTEIN 1 RELATED EXTRACELLULAR MATRIX PROTEIN 3; MEMBRANE PROTEIN; SCLEROPROTEIN; UNCLASSIFIED DRUG;

ARTICLE; BASEMENT MEMBRANE; BLISTER; CRYPTOPHTHALMOS; DERMOEPIDERMAL JUNCTION; EPITHELIUM; FRASER SYNDROME; GENE MUTATION; HUMAN; KIDNEY AGENESIS; MEMBRANE STRUCTURE; MESENCHYME; NONHUMAN; PHENOTYPE; PROTEIN MOTIF;

MURINAE;

EID: 79952106168     PISSN: 13572725     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.biocel.2010.12.016     Document Type: Review

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