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Volumn 376, Issue 9757, 2010, Pages 2018-2031

Sickle-cell disease

Author keywords

[No Author keywords available]

Indexed keywords

5 AZA 2' DEOXYCYTIDINE; ACETYLCYSTEINE; BOSENTAN; BUTYRIC ACID; DEXAMETHASONE; DIPYRIDAMOLE; FINASTERIDE; GLUTAMINE; HEPARIN; HYDROXYMETHYLGLUTARYL COENZYME A REDUCTASE INHIBITOR; HYDROXYUREA; LENALIDOMIDE; PHOSPHODIESTERASE V INHIBITOR; POMALIDOMIDE; SALAZOSULFAPYRIDINE; SILDENAFIL; VARESPLADIB;

EID: 78650179046     PISSN: 01406736     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0140-6736(10)61029-X     Document Type: Conference Paper
Times cited : (1543)

References (150)
  • 1
    • 12844276479 scopus 로고    scopus 로고
    • A case for developing North-South partnerships for research in sickle cell disease
    • D Weatherall, K Hofman, G Rodgers, J Ruffin, S Hrynkow A case for developing North-South partnerships for research in sickle cell disease Blood 105 2005 921 923
    • (2005) Blood , vol.105 , pp. 921-923
    • Weatherall, D.1    Hofman, K.2    Rodgers, G.3    Ruffin, J.4    Hrynkow, S.5
  • 2
    • 84928862267 scopus 로고
    • Peculiar elongated and sickle-shaped red blood corpuscles in a case of severe anemia
    • JB Herrick Peculiar elongated and sickle-shaped red blood corpuscles in a case of severe anemia Arch Intern Med 6 1910 517 521
    • (1910) Arch Intern Med , vol.6 , pp. 517-521
    • Herrick, J.B.1
  • 3
    • 0006177989 scopus 로고
    • Further observations on sickle cell anemia
    • VP Sydenstricker Further observations on sickle cell anemia J Am Med Ass 83 1924 12 15
    • (1924) J Am Med Ass , vol.83 , pp. 12-15
    • Sydenstricker, V.P.1
  • 4
    • 0006193759 scopus 로고
    • Case of sickle cell anaemia with necropsy
    • GS Graham Case of sickle cell anaemia with necropsy Arch Intern Med 34 1924 778 800
    • (1924) Arch Intern Med , vol.34 , pp. 778-800
    • Graham, G.S.1
  • 6
    • 0000343671 scopus 로고
    • The significance of the paucity of sickle cells in newborn negro infants
    • J Watson, AW Staham, FP Billelo The significance of the paucity of sickle cells in newborn negro infants Am J Med Sci 215 1948 419 423
    • (1948) Am J Med Sci , vol.215 , pp. 419-423
    • Watson, J.1    Staham, A.W.2    Billelo, F.P.3
  • 7
    • 0000840367 scopus 로고
    • X-ray and solubility studies of the haemoglobin of sickle-cell anaemia patients
    • MF Perutz, AM Liquori, F Eirich X-ray and solubility studies of the haemoglobin of sickle-cell anaemia patients Nature 167 1951 929 931
    • (1951) Nature , vol.167 , pp. 929-931
    • Perutz, M.F.1    Liquori, A.M.2    Eirich, F.3
  • 8
    • 0021239479 scopus 로고
    • Prevention of pneumococcal infection in children with homozygous sickle cell disease
    • AB John, A Ramlal, H Jackson, GH Maude, AW Sharma, GR Serjeant Prevention of pneumococcal infection in children with homozygous sickle cell disease BMJ 26 1984 1567 1570
    • (1984) BMJ , vol.26 , pp. 1567-1570
    • John, A.B.1    Ramlal, A.2    Jackson, H.3    Maude, G.H.4    Sharma, A.W.5    Serjeant, G.R.6
  • 9
    • 0022628893 scopus 로고
    • Prophylaxis with oral penicillin in children with sickle cell anemia
    • MH Gaston, JL Verter, G Woods Prophylaxis with oral penicillin in children with sickle cell anemia N Engl J Med 314 1986 1593 1599
    • (1986) N Engl J Med , vol.314 , pp. 1593-1599
    • Gaston, M.H.1    Verter, J.L.2    Woods, G.3
  • 11
    • 0029025475 scopus 로고
    • Effect of hydroxyurea on frequency of painful crises in sickle cell anemia
    • S Charache, ML Terrin, RD Moore Effect of hydroxyurea on frequency of painful crises in sickle cell anemia N Engl J Med 332 1995 1317 1322
    • (1995) N Engl J Med , vol.332 , pp. 1317-1322
    • Charache, S.1    Terrin, M.L.2    Moore, R.D.3
  • 12
    • 0032474692 scopus 로고    scopus 로고
    • Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography
    • RJ Adams, VC McKie, L Hsu Prevention of a first stroke by transfusions in children with sickle cell anemia and abnormal results on transcranial Doppler ultrasonography N Engl J Med 339 1998 5 11
    • (1998) N Engl J Med , vol.339 , pp. 5-11
    • Adams, R.J.1    McKie, V.C.2    Hsu, L.3
  • 15
    • 0016834459 scopus 로고
    • The presence of hemoglobin S and C Harlem in an individual in the United States
    • W Moo-Penn, K Bechtel, D Jue The presence of hemoglobin S and C Harlem in an individual in the United States Blood 46 1975 363 367
    • (1975) Blood , vol.46 , pp. 363-367
    • Moo-Penn, W.1    Bechtel, K.2    Jue, D.3
  • 16
    • 0010114289 scopus 로고
    • Hemoglobin S Antilles: A variant with lower solubility than hemoglobin S and producing sickle cell disease in heterozygotes
    • N Monplaisir, G Merault, C Poyart Hemoglobin S Antilles: a variant with lower solubility than hemoglobin S and producing sickle cell disease in heterozygotes Proc Natl Acad Sci USA 83 1986 9363 9367
    • (1986) Proc Natl Acad Sci USA , vol.83 , pp. 9363-9367
    • Monplaisir, N.1    Merault, G.2    Poyart, C.3
  • 17
    • 0026018259 scopus 로고
    • Sickle cell disease in a patient with sickle cell trait and compound heterozygosity for hemoglobin S and hemoglobin Quebec-Chori
    • HE Witkowska, BH Lubin, Y Beuzard Sickle cell disease in a patient with sickle cell trait and compound heterozygosity for hemoglobin S and hemoglobin Quebec-Chori N Engl J Med 325 1991 1150 1154
    • (1991) N Engl J Med , vol.325 , pp. 1150-1154
    • Witkowska, H.E.1    Lubin, B.H.2    Beuzard, Y.3
  • 18
    • 0032400879 scopus 로고    scopus 로고
    • HbS-Oman heterozygote: A new dominant sickle syndrome
    • RL Nagel, S Daar, JR Romero HbS-Oman heterozygote: a new dominant sickle syndrome Blood 92 1998 4375 4382
    • (1998) Blood , vol.92 , pp. 4375-4382
    • Nagel, R.L.1    Daar, S.2    Romero, J.R.3
  • 21
    • 0030853711 scopus 로고    scopus 로고
    • Pathogenesis and treatment of sickle cell disease
    • HF Bunn Pathogenesis and treatment of sickle cell disease N Engl J Med 337 1997 762 769
    • (1997) N Engl J Med , vol.337 , pp. 762-769
    • Bunn, H.F.1
  • 22
    • 0021931288 scopus 로고
    • Hemoglobin S polymerization: Primary determinant of the hemolytic and clinical severity of the sickling syndromes
    • GM Brittenham, AN Schechter, CT Noguchi Hemoglobin S polymerization: primary determinant of the hemolytic and clinical severity of the sickling syndromes Blood 65 1985 183 189
    • (1985) Blood , vol.65 , pp. 183-189
    • Brittenham, G.M.1    Schechter, A.N.2    Noguchi, C.T.3
  • 23
    • 0023859033 scopus 로고
    • Levels of fetal hemoglobin necessary for treatment of sickle cell disease
    • CT Noguchi, GP Rodgers, G Serjeant, AN Schechter Levels of fetal hemoglobin necessary for treatment of sickle cell disease N Engl J Med 318 1988 96 99
    • (1988) N Engl J Med , vol.318 , pp. 96-99
    • Noguchi, C.T.1    Rodgers, G.P.2    Serjeant, G.3    Schechter, A.N.4
  • 24
    • 0036177721 scopus 로고    scopus 로고
    • Sickle cell vaso-occlusion: Multistep and multicellular paradigm
    • PS Frenette Sickle cell vaso-occlusion: multistep and multicellular paradigm Curr Opin Hematol 9 2002 101 106
    • (2002) Curr Opin Hematol , vol.9 , pp. 101-106
    • Frenette, P.S.1
  • 26
    • 0037588990 scopus 로고    scopus 로고
    • Transgenic sickle mice have vascular inflammation
    • JD Belcher, CJ Bryant, J Nguyen Transgenic sickle mice have vascular inflammation Blood 101 2003 3953 3959
    • (2003) Blood , vol.101 , pp. 3953-3959
    • Belcher, J.D.1    Bryant, C.J.2    Nguyen, J.3
  • 28
    • 20444468127 scopus 로고    scopus 로고
    • Endothelial cell NADPH oxidase mediates the cerebral microvascular dysfunction in sickle cell transgenic mice
    • KC Wood, RP Hebbel, DN Granger Endothelial cell NADPH oxidase mediates the cerebral microvascular dysfunction in sickle cell transgenic mice Faseb J 19 2005 989 991
    • (2005) Faseb J , vol.19 , pp. 989-991
    • Wood, K.C.1    Hebbel, R.P.2    Granger, D.N.3
  • 29
    • 21144440415 scopus 로고    scopus 로고
    • Critical role of endothelial cell activation in hypoxia-induced vasoocclusion in transgenic sickle mice
    • JD Belcher, H Mahaseth, TE Welch Critical role of endothelial cell activation in hypoxia-induced vasoocclusion in transgenic sickle mice Am J Physiol Heart Circ Physiol 288 2005 H2715 H2725
    • (2005) Am J Physiol Heart Circ Physiol , vol.288
    • Belcher, J.D.1    Mahaseth, H.2    Welch, T.E.3
  • 30
    • 0028291736 scopus 로고
    • Mortality in sickle cell disease. Life expectancy and risk factors for early death
    • OS Platt, DJ Brambilla, WF Rosse Mortality in sickle cell disease. Life expectancy and risk factors for early death N Engl J Med 330 1994 1639 1644
    • (1994) N Engl J Med , vol.330 , pp. 1639-1644
    • Platt, O.S.1    Brambilla, D.J.2    Rosse, W.F.3
  • 31
    • 0031001007 scopus 로고    scopus 로고
    • Natural history of blood pressure in sickle cell disease: Risks for stroke and death associated with relative hypertension in sickle cell anemia
    • CH Pegelow, L Colangelo, M Steinberg Natural history of blood pressure in sickle cell disease: risks for stroke and death associated with relative hypertension in sickle cell anemia Am J Med 102 1997 171 177
    • (1997) Am J Med , vol.102 , pp. 171-177
    • Pegelow, C.H.1    Colangelo, L.2    Steinberg, M.3
  • 32
    • 0031965089 scopus 로고    scopus 로고
    • Cerebrovascular accidents in sickle cell disease: Rates and risk factors
    • K Ohene-Frempong, SJ Weiner, LA Sleeper Cerebrovascular accidents in sickle cell disease: rates and risk factors Blood 91 1998 288 294
    • (1998) Blood , vol.91 , pp. 288-294
    • Ohene-Frempong, K.1    Weiner, S.J.2    Sleeper, L.A.3
  • 33
    • 10744233940 scopus 로고    scopus 로고
    • Pulmonary hypertension as a risk factor for death in patients with sickle cell disease
    • MT Gladwin, V Sachdev, ML Jison Pulmonary hypertension as a risk factor for death in patients with sickle cell disease N Engl J Med 350 2004 886 895
    • (2004) N Engl J Med , vol.350 , pp. 886-895
    • Gladwin, M.T.1    Sachdev, V.2    Jison, M.L.3
  • 34
    • 33745699067 scopus 로고    scopus 로고
    • Cerebrovascular disease associated with sickle cell pulmonary hypertension
    • GJ Kato, M Hsieh, R Machado Cerebrovascular disease associated with sickle cell pulmonary hypertension Am J Hematol 81 2006 503 510
    • (2006) Am J Hematol , vol.81 , pp. 503-510
    • Kato, G.J.1    Hsieh, M.2    MacHado, R.3
  • 35
    • 33846279380 scopus 로고    scopus 로고
    • Deconstructing sickle cell disease: Reappraisal of the role of hemolysis in the development of clinical subphenotypes
    • GJ Kato, MT Gladwin, MH Steinberg Deconstructing sickle cell disease: reappraisal of the role of hemolysis in the development of clinical subphenotypes Blood Rev 21 2007 37 47
    • (2007) Blood Rev , vol.21 , pp. 37-47
    • Kato, G.J.1    Gladwin, M.T.2    Steinberg, M.H.3
  • 36
    • 38349071895 scopus 로고    scopus 로고
    • Pulmonary hypertension associated with sickle cell disease: Clinical and laboratory endpoints and disease outcomes
    • LM De Castro, JC Jonassaint, FL Graham, A Ashley-Koch, MJ Telen Pulmonary hypertension associated with sickle cell disease: clinical and laboratory endpoints and disease outcomes Am J Hematol 83 2008 19 25
    • (2008) Am J Hematol , vol.83 , pp. 19-25
    • De Castro, L.M.1    Jonassaint, J.C.2    Graham, F.L.3    Ashley-Koch, A.4    Telen, M.J.5
  • 37
    • 33744810662 scopus 로고    scopus 로고
    • Pulmonary hypertension in patients with sickle cell disease: A longitudinal study
    • KI Ataga, CG Moore, S Jones Pulmonary hypertension in patients with sickle cell disease: a longitudinal study Br J Haematol 134 2006 109 115
    • (2006) Br J Haematol , vol.134 , pp. 109-115
    • Ataga, K.I.1    Moore, C.G.2    Jones, S.3
  • 38
    • 68749095213 scopus 로고    scopus 로고
    • Prospective echocardiography assessment of pulmonary hypertension and its potential etiologies in children with sickle cell disease
    • N Dham, G Ensing, C Minniti Prospective echocardiography assessment of pulmonary hypertension and its potential etiologies in children with sickle cell disease Am J Cardiol 104 2009 713 720
    • (2009) Am J Cardiol , vol.104 , pp. 713-720
    • Dham, N.1    Ensing, G.2    Minniti, C.3
  • 39
    • 62949183515 scopus 로고    scopus 로고
    • Elevated tricuspid regurgitant jet velocity in children and adolescents with sickle cell disease: Association with hemolysis and hemoglobin oxygen desaturation
    • CP Minniti, C Sable, A Campbell Elevated tricuspid regurgitant jet velocity in children and adolescents with sickle cell disease: association with hemolysis and hemoglobin oxygen desaturation Haematologica 94 2009 340 347
    • (2009) Haematologica , vol.94 , pp. 340-347
    • Minniti, C.P.1    Sable, C.2    Campbell, A.3
  • 40
    • 15944398355 scopus 로고    scopus 로고
    • The clinical sequelae of intravascular hemolysis and extracellular plasma hemoglobin: A novel mechanism of human disease
    • RP Rother, L Bell, P Hillmen, MT Gladwin The clinical sequelae of intravascular hemolysis and extracellular plasma hemoglobin: a novel mechanism of human disease JAMA 293 2005 1653 1662
    • (2005) JAMA , vol.293 , pp. 1653-1662
    • Rother, R.P.1    Bell, L.2    Hillmen, P.3    Gladwin, M.T.4
  • 41
    • 0025749683 scopus 로고
    • Hydroxyl radical formation by sickle erythrocyte membranes: Role of pathologic iron deposits and cytoplasmic reducing agents
    • T Repka, RP Hebbel Hydroxyl radical formation by sickle erythrocyte membranes: role of pathologic iron deposits and cytoplasmic reducing agents Blood 78 1991 2753 2758
    • (1991) Blood , vol.78 , pp. 2753-2758
    • Repka, T.1    Hebbel, R.P.2
  • 42
    • 0036908599 scopus 로고    scopus 로고
    • Cell-free hemoglobin limits nitric oxide bioavailability in sickle-cell disease
    • CD Reiter, X Wang, JE Tanus-Santos Cell-free hemoglobin limits nitric oxide bioavailability in sickle-cell disease Nat Med 8 2002 1383 1389
    • (2002) Nat Med , vol.8 , pp. 1383-1389
    • Reiter, C.D.1    Wang, X.2    Tanus-Santos, J.E.3
  • 43
    • 0023912670 scopus 로고
    • Vascular endothelial cells synthesize nitric oxide from L-arginine
    • RM Palmer, DS Ashton, S Moncada Vascular endothelial cells synthesize nitric oxide from L-arginine Nature 333 1988 664 666
    • (1988) Nature , vol.333 , pp. 664-666
    • Palmer, R.M.1    Ashton, D.S.2    Moncada, S.3
  • 44
    • 0029159779 scopus 로고
    • Nitric oxide decreases cytokine-induced endothelial activation. Nitric oxide selectively reduces endothelial expression of adhesion molecules and proinflammatory cytokines
    • R De Caterina, P Libby, HB Peng Nitric oxide decreases cytokine-induced endothelial activation. Nitric oxide selectively reduces endothelial expression of adhesion molecules and proinflammatory cytokines J Clin Invest 96 1995 60 68
    • (1995) J Clin Invest , vol.96 , pp. 60-68
    • De Caterina, R.1    Libby, P.2    Peng, H.B.3
  • 45
    • 33748295731 scopus 로고    scopus 로고
    • Deconstructing endothelial dysfunction: Soluble guanylyl cyclase oxidation and the NO resistance syndrome
    • MT Gladwin Deconstructing endothelial dysfunction: soluble guanylyl cyclase oxidation and the NO resistance syndrome J Clin Invest 116 2006 2330 2332
    • (2006) J Clin Invest , vol.116 , pp. 2330-2332
    • Gladwin, M.T.1
  • 46
    • 21444441271 scopus 로고    scopus 로고
    • Dysregulated arginine metabolism, hemolysis-associated pulmonary hypertension, and mortality in sickle cell disease
    • CR Morris, GJ Kato, M Poljakovic Dysregulated arginine metabolism, hemolysis-associated pulmonary hypertension, and mortality in sickle cell disease JAMA 294 2005 81 90
    • (2005) JAMA , vol.294 , pp. 81-90
    • Morris, C.R.1    Kato, G.J.2    Poljakovic, M.3
  • 47
    • 38549131853 scopus 로고    scopus 로고
    • Coagulation activation and inflammation in sickle cell disease-associated pulmonary hypertension
    • KI Ataga, CG Moore, CA Hillery Coagulation activation and inflammation in sickle cell disease-associated pulmonary hypertension Haematologica 93 2008 20 26
    • (2008) Haematologica , vol.93 , pp. 20-26
    • Ataga, K.I.1    Moore, C.G.2    Hillery, C.A.3
  • 48
    • 44649183571 scopus 로고    scopus 로고
    • Microvesicles in haemoglobinopathies offer insights into mechanisms of hypercoagulability, haemolysis and the effects of therapy
    • M Westerman, A Pizzey, J Hirschman Microvesicles in haemoglobinopathies offer insights into mechanisms of hypercoagulability, haemolysis and the effects of therapy Br J Haematol 142 2008 126 135
    • (2008) Br J Haematol , vol.142 , pp. 126-135
    • Westerman, M.1    Pizzey, A.2    Hirschman, J.3
  • 50
    • 77049164783 scopus 로고
    • Protection afforded by sickle cell trait against subtertian malarial infection
    • AC Allison Protection afforded by sickle cell trait against subtertian malarial infection BMJ 1 1954 290 295
    • (1954) BMJ , vol.1 , pp. 290-295
    • Allison, A.C.1
  • 52
    • 44949128064 scopus 로고    scopus 로고
    • Global epidemiology of haemoglobin disorders and derived service indicators
    • B Modell, M Darlison Global epidemiology of haemoglobin disorders and derived service indicators Bull World Health Organ 86 2008 480 487
    • (2008) Bull World Health Organ , vol.86 , pp. 480-487
    • Modell, B.1    Darlison, M.2
  • 54
    • 2542451884 scopus 로고    scopus 로고
    • The global distribution and population at risk of malaria: Past, present, and future
    • SI Hay, CA Guerra, AJ Tatem, AM Noor, RW Snow The global distribution and population at risk of malaria: past, present, and future Lancet Infect Dis 4 2004 327 336
    • (2004) Lancet Infect Dis , vol.4 , pp. 327-336
    • Hay, S.I.1    Guerra, C.A.2    Tatem, A.J.3    Noor, A.M.4    Snow, R.W.5
  • 55
    • 20844435977 scopus 로고    scopus 로고
    • Sickle cell trait and the risk of Plasmodium falciparum malaria and other childhood diseases
    • TN Williams, TW Mwangi, S Wambua Sickle cell trait and the risk of Plasmodium falciparum malaria and other childhood diseases J Infect Dis 192 2005 178 186
    • (2005) J Infect Dis , vol.192 , pp. 178-186
    • Williams, T.N.1    Mwangi, T.W.2    Wambua, S.3
  • 56
    • 34249679269 scopus 로고    scopus 로고
    • Hemoglobin variants and disease manifestations in severe falciparum malaria
    • J May, JA Evans, C Timmann Hemoglobin variants and disease manifestations in severe falciparum malaria JAMA 297 2007 2220 2226
    • (2007) JAMA , vol.297 , pp. 2220-2226
    • May, J.1    Evans, J.A.2    Timmann, C.3
  • 57
    • 70349207216 scopus 로고    scopus 로고
    • The impact of malaria parasitism: From corpuscles to communities
    • TE Wellems, K Hayton, RM Fairhurst The impact of malaria parasitism: from corpuscles to communities J Clin Invest 119 2009 2496 2505
    • (2009) J Clin Invest , vol.119 , pp. 2496-2505
    • Wellems, T.E.1    Hayton, K.2    Fairhurst, R.M.3
  • 58
    • 14644387484 scopus 로고    scopus 로고
    • Mortality from sickle cell disease in Africa
    • GR Serjeant Mortality from sickle cell disease in Africa BMJ 330 2005 432 433
    • (2005) BMJ , vol.330 , pp. 432-433
    • Serjeant, G.R.1
  • 59
    • 33947509031 scopus 로고    scopus 로고
    • Sickle cell disease in Africa: Burden and research priorities
    • J Makani, TN Williams, K Marsh Sickle cell disease in Africa: burden and research priorities Ann Trop Med Parasitol 101 2007 3 14
    • (2007) Ann Trop Med Parasitol , vol.101 , pp. 3-14
    • Makani, J.1    Williams, T.N.2    Marsh, K.3
  • 60
    • 0043245973 scopus 로고    scopus 로고
    • Effect of a comprehensive clinical care program on disease course in severely ill children with sickle cell anemia in a sub-Saharan African setting
    • MC Rahimy, A Gangbo, G Ahouignan Effect of a comprehensive clinical care program on disease course in severely ill children with sickle cell anemia in a sub-Saharan African setting Blood 102 2003 834 838
    • (2003) Blood , vol.102 , pp. 834-838
    • Rahimy, M.C.1    Gangbo, A.2    Ahouignan, G.3
  • 61
    • 70349869344 scopus 로고    scopus 로고
    • Bacteraemia in Kenyan children with sickle-cell anaemia: A retrospective cohort and case-control study
    • TN Williams, S Uyoga, A Macharia Bacteraemia in Kenyan children with sickle-cell anaemia: a retrospective cohort and case-control study Lancet 374 2009 1364 1370
    • (2009) Lancet , vol.374 , pp. 1364-1370
    • Williams, T.N.1    Uyoga, S.2    MacHaria, A.3
  • 62
    • 0242298737 scopus 로고    scopus 로고
    • Invasive pneumococcal infections in children with sickle cell disease in the era of penicillin prophylaxis, antibiotic resistance, and 23-valent pneumococcal polysaccharide vaccination
    • TV Adamkiewicz, S Sarnaik, GR Buchanan Invasive pneumococcal infections in children with sickle cell disease in the era of penicillin prophylaxis, antibiotic resistance, and 23-valent pneumococcal polysaccharide vaccination J Pediatr 143 2003 438 444
    • (2003) J Pediatr , vol.143 , pp. 438-444
    • Adamkiewicz, T.V.1    Sarnaik, S.2    Buchanan, G.R.3
  • 64
    • 75649093820 scopus 로고    scopus 로고
    • Malaria in patients with sickle cell anemia: Burden, risk factors, and outcome at the outpatient clinic and during hospitalization
    • J Makani, AN Komba, SE Cox Malaria in patients with sickle cell anemia: burden, risk factors, and outcome at the outpatient clinic and during hospitalization Blood 115 2010 215 220
    • (2010) Blood , vol.115 , pp. 215-220
    • Makani, J.1    Komba, A.N.2    Cox, S.E.3
  • 65
    • 77956576772 scopus 로고    scopus 로고
    • High mortality from P. falciparum in children living with sickle cell anemia on the coast of Kenya
    • CM McAuley, C Webb, J Makani High mortality from P. falciparum in children living with sickle cell anemia on the coast of Kenya Blood 116 2010 1663 1668
    • (2010) Blood , vol.116 , pp. 1663-1668
    • McAuley, C.M.1    Webb, C.2    Makani, J.3
  • 66
    • 33744942102 scopus 로고    scopus 로고
    • Health transitions in sub-Saharan Africa: Overview of mortality trends in children under 5 years old (1950-2000)
    • M Garenne, E Gakusi Health transitions in sub-Saharan Africa: overview of mortality trends in children under 5 years old (1950-2000) Bull World Health Organ 84 2006 470 478
    • (2006) Bull World Health Organ , vol.84 , pp. 470-478
    • Garenne, M.1    Gakusi, E.2
  • 67
    • 58349114639 scopus 로고    scopus 로고
    • Neonatal/newborn haemoglobinopathy screening in Europe and Africa
    • BJ Bain Neonatal/newborn haemoglobinopathy screening in Europe and Africa J Clin Pathol 62 2009 53 56
    • (2009) J Clin Pathol , vol.62 , pp. 53-56
    • Bain, B.J.1
  • 69
    • 0024467330 scopus 로고
    • Leg ulcers in patients with sickle cell disease
    • M Koshy, R Entsuah, A Koranda Leg ulcers in patients with sickle cell disease Blood 74 1989 1403 1408
    • (1989) Blood , vol.74 , pp. 1403-1408
    • Koshy, M.1    Entsuah, R.2    Koranda, A.3
  • 71
    • 34547450531 scopus 로고    scopus 로고
    • Intergenic variants of HBS1L-MYB are responsible for a major quantitative trait locus on chromosome 6q23 influencing fetal hemoglobin levels in adults
    • SL Thein, S Menzel, X Peng Intergenic variants of HBS1L-MYB are responsible for a major quantitative trait locus on chromosome 6q23 influencing fetal hemoglobin levels in adults Proc Natl Acad Sci USA 104 2007 11346 11351
    • (2007) Proc Natl Acad Sci USA , vol.104 , pp. 11346-11351
    • Thein, S.L.1    Menzel, S.2    Peng, X.3
  • 72
    • 34748864128 scopus 로고    scopus 로고
    • A QTL influencing F cell production maps to a gene encoding a zinc-finger protein on chromosome 2p15
    • S Menzel, C Garner, I Gut A QTL influencing F cell production maps to a gene encoding a zinc-finger protein on chromosome 2p15 Nat Genet 39 2007 1197 1199
    • (2007) Nat Genet , vol.39 , pp. 1197-1199
    • Menzel, S.1    Garner, C.2    Gut, I.3
  • 73
    • 50149117726 scopus 로고    scopus 로고
    • DNA polymorphisms at the BCL11A, HBS1L-MYB and beta-globin loci associate with fetal hemoglobin levels and pain crises in sickle cell disease
    • G Lettre, VG Sankaran, MA Bezerra DNA polymorphisms at the BCL11A, HBS1L-MYB and beta-globin loci associate with fetal hemoglobin levels and pain crises in sickle cell disease Proc Natl Acad Sci USA 105 2008 11869 11874
    • (2008) Proc Natl Acad Sci USA , vol.105 , pp. 11869-11874
    • Lettre, G.1    Sankaran, V.G.2    Bezerra, M.A.3
  • 74
    • 0020057099 scopus 로고
    • The interaction of alpha thalassaemia and homozygous sickle-cell disease
    • DR Higgs, BE Aldridge, J Lamb The interaction of alpha thalassaemia and homozygous sickle-cell disease N Engl J Med 306 1982 1441 1446
    • (1982) N Engl J Med , vol.306 , pp. 1441-1446
    • Higgs, D.R.1    Aldridge, B.E.2    Lamb, J.3
  • 75
    • 0022977959 scopus 로고
    • Sickle cell disease in Orissa State, India
    • BC Kar, RK Satapathy, AE Kulozik Sickle cell disease in Orissa State, India Lancet 2 1986 1198 1201
    • (1986) Lancet , vol.2 , pp. 1198-1201
    • Kar, B.C.1    Satapathy, R.K.2    Kulozik, A.E.3
  • 76
    • 0026001987 scopus 로고
    • Two different forms of homozygous sickle cell disease occur in Saudi Arabia
    • MA Padmos, GT Roberts, K Sackey Two different forms of homozygous sickle cell disease occur in Saudi Arabia Br J Haematol 79 1991 93 98
    • (1991) Br J Haematol , vol.79 , pp. 93-98
    • Padmos, M.A.1    Roberts, G.T.2    Sackey, K.3
  • 77
    • 78650176355 scopus 로고    scopus 로고
    • G6PD deficiency, absence of alpha-thalassemia, and hemolytic rate at baseline are significant independent risk factors for abnormally high cerebral velocities in patients with sickle cell anemia
    • F Bernaudin, S Verlhac, S Chevret G6PD deficiency, absence of alpha-thalassemia, and hemolytic rate at baseline are significant independent risk factors for abnormally high cerebral velocities in patients with sickle cell anemia Blood 114 2009 742 743
    • (2009) Blood , vol.114 , pp. 742-743
    • Bernaudin, F.1    Verlhac, S.2    Chevret, S.3
  • 78
    • 34250846041 scopus 로고    scopus 로고
    • The linear effects of alpha-thalassaemia, the UGT1A1 and HMOX1 polymorphisms on cholelithiasis in sickle cell disease
    • N Vasavda, S Menzel, S Kondaveeti The linear effects of alpha-thalassaemia, the UGT1A1 and HMOX1 polymorphisms on cholelithiasis in sickle cell disease Br J Haematol 138 2007 263 270
    • (2007) Br J Haematol , vol.138 , pp. 263-270
    • Vasavda, N.1    Menzel, S.2    Kondaveeti, S.3
  • 80
    • 0029017748 scopus 로고
    • Clinical events in the first decade in a cohort of infants with sickle cell disease
    • FM Gill, LA Sleeper, SJ Weiner Clinical events in the first decade in a cohort of infants with sickle cell disease Blood 86 1995 776 783
    • (1995) Blood , vol.86 , pp. 776-783
    • Gill, F.M.1    Sleeper, L.A.2    Weiner, S.J.3
  • 81
    • 34548269532 scopus 로고    scopus 로고
    • Confirmation of an association between TNF(-308) promoter polymorphism and stroke risk in children with sickle cell anemia
    • C Hoppe, W Klitz, K D'Harlingue Confirmation of an association between TNF(-308) promoter polymorphism and stroke risk in children with sickle cell anemia Stroke 38 2007 2241 2246
    • (2007) Stroke , vol.38 , pp. 2241-2246
    • Hoppe, C.1    Klitz, W.2    D'Harlingue, K.3
  • 82
    • 1542283710 scopus 로고    scopus 로고
    • Gene interactions and stroke risk in children with sickle cell anemia
    • C Hoppe, W Klitz, S Cheng Gene interactions and stroke risk in children with sickle cell anemia Blood 103 2004 2391 2396
    • (2004) Blood , vol.103 , pp. 2391-2396
    • Hoppe, C.1    Klitz, W.2    Cheng, S.3
  • 83
    • 16844366938 scopus 로고    scopus 로고
    • Genetic dissection and prognostic modeling of overt stroke in sickle cell anemia
    • P Sebastiani, MF Ramoni, V Nolan, CT Baldwin, MH Steinberg Genetic dissection and prognostic modeling of overt stroke in sickle cell anemia Nat Genet 37 2005 340 341
    • (2005) Nat Genet , vol.37 , pp. 340-341
    • Sebastiani, P.1    Ramoni, M.F.2    Nolan, V.3    Baldwin, C.T.4    Steinberg, M.H.5
  • 85
    • 0017254548 scopus 로고
    • Climate and painful crisis of sickle-cell disease in Jamaica
    • AM Redwood, EM Williams, P Desai, GR Serjeant Climate and painful crisis of sickle-cell disease in Jamaica BMJ 1 1976 66 68
    • (1976) BMJ , vol.1 , pp. 66-68
    • Redwood, A.M.1    Williams, E.M.2    Desai, P.3    Serjeant, G.R.4
  • 86
    • 33644788545 scopus 로고    scopus 로고
    • Windy weather and low humidity are associated with an increased number of hospital admissions for acute pain and sickle cell disease in an urban environment with a maritime temperate climate
    • S Jones, ER Duncan, N Thomas Windy weather and low humidity are associated with an increased number of hospital admissions for acute pain and sickle cell disease in an urban environment with a maritime temperate climate Br J Haematol 131 2005 530 533
    • (2005) Br J Haematol , vol.131 , pp. 530-533
    • Jones, S.1    Duncan, E.R.2    Thomas, N.3
  • 87
    • 33847402262 scopus 로고    scopus 로고
    • The associations between air quality and the number of hospital admissions for acute pain and sickle-cell disease in an urban environment
    • D Yallop, ER Duncan, E Norris The associations between air quality and the number of hospital admissions for acute pain and sickle-cell disease in an urban environment Br J Haematol 136 2007 844 848
    • (2007) Br J Haematol , vol.136 , pp. 844-848
    • Yallop, D.1    Duncan, E.R.2    Norris, E.3
  • 88
    • 67651056519 scopus 로고    scopus 로고
    • The effects of air quality on haematological and clinical parameters in children with sickle cell anaemia
    • H Mittal, L Roberts, GW Fuller The effects of air quality on haematological and clinical parameters in children with sickle cell anaemia Ann Hematol 88 2009 529 533
    • (2009) Ann Hematol , vol.88 , pp. 529-533
    • Mittal, H.1    Roberts, L.2    Fuller, G.W.3
  • 89
    • 77949357012 scopus 로고    scopus 로고
    • Significant haemoglobinopathies: Guidelines for screening and diagnosis
    • K Ryan, B Bain, D Worthington Significant haemoglobinopathies: guidelines for screening and diagnosis Br J Haematol 149 2010 35 49
    • (2010) Br J Haematol , vol.149 , pp. 35-49
    • Ryan, K.1    Bain, B.2    Worthington, D.3
  • 90
    • 0023906590 scopus 로고
    • Newborn screening for sickle cell disease: Effect on mortality
    • V Vichinsky, D Hurst, A Earles, K Kleman, B Lubin Newborn screening for sickle cell disease: effect on mortality Pediatrics 81 1988 749 755
    • (1988) Pediatrics , vol.81 , pp. 749-755
    • Vichinsky, V.1    Hurst, D.2    Earles, A.3    Kleman, K.4    Lubin, B.5
  • 92
    • 49949152147 scopus 로고    scopus 로고
    • Erythroid adhesion molecules in sickle cell disease: Effect of hydroxyurea
    • J-P Cartron, J Elion Erythroid adhesion molecules in sickle cell disease: effect of hydroxyurea Transfus Clin Biol 15 2008 39 50
    • (2008) Transfus Clin Biol , vol.15 , pp. 39-50
    • Cartron, J.-P.1    Elion, J.2
  • 93
    • 70350545951 scopus 로고    scopus 로고
    • Hydroxyurea generates nitric oxide in human erythroid cells: Mechanisms for gamma-globin gene activation
    • TF Lou, M Singh, A Mackie, W Li, BS Pace Hydroxyurea generates nitric oxide in human erythroid cells: mechanisms for gamma-globin gene activation Exp Biol Med 234 2009 1374 1382
    • (2009) Exp Biol Med , vol.234 , pp. 1374-1382
    • Lou, T.F.1    Singh, M.2    MacKie, A.3    Li, W.4    Pace, B.S.5
  • 94
    • 58249093004 scopus 로고    scopus 로고
    • Hydroxyurea for sickle cell disease: A systematic review for efficacy and toxicity in children
    • JJ Strouse, S Lanzkron, MC Beach Hydroxyurea for sickle cell disease: a systematic review for efficacy and toxicity in children Pediatrics 122 2008 1332 1342
    • (2008) Pediatrics , vol.122 , pp. 1332-1342
    • Strouse, J.J.1    Lanzkron, S.2    Beach, M.C.3
  • 95
    • 45549105597 scopus 로고    scopus 로고
    • Systematic review: Hydroxyurea for the treatment of adults with sickle cell disease
    • S Lankron, JJ Stouse, R Wilson Systematic review: hydroxyurea for the treatment of adults with sickle cell disease Ann Intern Med 48 2008 939 955
    • (2008) Ann Intern Med , vol.48 , pp. 939-955
    • Lankron, S.1    Stouse, J.J.2    Wilson, R.3
  • 96
    • 46849120215 scopus 로고    scopus 로고
    • Influence of sickle cell disease and treatment with hydroxyurea on sperm parameters and fertility of human males
    • I Berthaut, G Guignedoux, F Kirsch-Noir Influence of sickle cell disease and treatment with hydroxyurea on sperm parameters and fertility of human males Hematologica 93 2008 988 993
    • (2008) Hematologica , vol.93 , pp. 988-993
    • Berthaut, I.1    Guignedoux, G.2    Kirsch-Noir, F.3
  • 97
    • 70350637293 scopus 로고    scopus 로고
    • Exposure to hydroxyurea and pregnancy outcomes in sickle cell anemia
    • SK Ballas, WF McCarthy, N Guo Exposure to hydroxyurea and pregnancy outcomes in sickle cell anemia J Natl Med Assoc 101 2009 1046 1051
    • (2009) J Natl Med Assoc , vol.101 , pp. 1046-1051
    • Ballas, S.K.1    McCarthy, W.F.2    Guo, N.3
  • 98
    • 0037414164 scopus 로고    scopus 로고
    • Effect of hydroxyurea on mortality and morbidity in adult sickle cell anemia: Risks and benefits up to 9 years of treatment
    • MH Steinberg, F Barton, O Castro Effect of hydroxyurea on mortality and morbidity in adult sickle cell anemia: risks and benefits up to 9 years of treatment JAMA 289 2003 1645 1651
    • (2003) JAMA , vol.289 , pp. 1645-1651
    • Steinberg, M.H.1    Barton, F.2    Castro, O.3
  • 99
    • 77950622293 scopus 로고    scopus 로고
    • The effect of prolonged administration of hydroxyurea on morbidity and mortality in adult patients with sickle cell syndromes: Results of a 17-year, single-center trial (LaSHS)
    • E Voskaridou, D Christoulas, A Bilalis The effect of prolonged administration of hydroxyurea on morbidity and mortality in adult patients with sickle cell syndromes: results of a 17-year, single-center trial (LaSHS) Blood 115 2010 2354 2363
    • (2010) Blood , vol.115 , pp. 2354-2363
    • Voskaridou, E.1    Christoulas, D.2    Bilalis, A.3
  • 100
    • 34547961356 scopus 로고    scopus 로고
    • Hydroxyurea therapy lowers transcranial doppler flow velocities in children with sickle cell anemia
    • SA Zimmerman, WH Schultz, S Burgett, NA Mortier, RE Ware Hydroxyurea therapy lowers transcranial doppler flow velocities in children with sickle cell anemia Blood 110 2007 1043 1047
    • (2007) Blood , vol.110 , pp. 1043-1047
    • Zimmerman, S.A.1    Schultz, W.H.2    Burgett, S.3    Mortier, N.A.4    Ware, R.E.5
  • 101
    • 42349111811 scopus 로고    scopus 로고
    • Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment with hydroxyurea
    • SA Singh, AC Koumbourlis, B Aygun Resolution of chronic hypoxemia in pediatric sickle cell patients after treatment with hydroxyurea Pediatr Blood Cancer 50 2008 1258 1260
    • (2008) Pediatr Blood Cancer , vol.50 , pp. 1258-1260
    • Singh, S.A.1    Koumbourlis, A.C.2    Aygun, B.3
  • 102
    • 27644533273 scopus 로고    scopus 로고
    • Enalapril and hydroxyurea therapy for children with sickle nephropathy
    • CD Fitzhugh, DR Wigfall, RE Ware Enalapril and hydroxyurea therapy for children with sickle nephropathy Pediatr Blood Cancer 45 2005 982 985
    • (2005) Pediatr Blood Cancer , vol.45 , pp. 982-985
    • Fitzhugh, C.D.1    Wigfall, D.R.2    Ware, R.E.3
  • 103
    • 45549101008 scopus 로고    scopus 로고
    • National Institutes of Health Consensus Development Conference statement: Hydroxyurea treatment for sickle cell disease
    • OW Brawley, LJ Cornelius, LR Edwards National Institutes of Health Consensus Development Conference statement: hydroxyurea treatment for sickle cell disease Ann Intern Med. 148 2008 932 938
    • (2008) Ann Intern Med. , vol.148 , pp. 932-938
    • Brawley, O.W.1    Cornelius, L.J.2    Edwards, L.R.3
  • 104
    • 0035138963 scopus 로고    scopus 로고
    • Techniques for blood administration in sickle cell patients
    • JR Eckman Techniques for blood administration in sickle cell patients Semin Hematol 38 2001 23 29
    • (2001) Semin Hematol , vol.38 , pp. 23-29
    • Eckman, J.R.1
  • 105
    • 0025372673 scopus 로고
    • Alloimmunization in sickle cell anaemia and transfusion of racially unmatched blood
    • EP Vichinsky, A Earles, RA Johnson Alloimmunization in sickle cell anaemia and transfusion of racially unmatched blood N Engl J Med 322 1990 1617 1621
    • (1990) N Engl J Med , vol.322 , pp. 1617-1621
    • Vichinsky, E.P.1    Earles, A.2    Johnson, R.A.3
  • 106
    • 1442307460 scopus 로고    scopus 로고
    • Myocardial iron loading in transfusion-dependent thalassemia and sickle cell disease
    • JC Wood, JM Tyszka, S Carson, MD Nelson, TD Coates Myocardial iron loading in transfusion-dependent thalassemia and sickle cell disease Blood 103 2004 1934 1936
    • (2004) Blood , vol.103 , pp. 1934-1936
    • Wood, J.C.1    Tyszka, J.M.2    Carson, S.3    Nelson, M.D.4    Coates, T.D.5
  • 107
    • 33846012866 scopus 로고    scopus 로고
    • A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease
    • E Vichinsky, O Onyekwere, JB Porter A randomised comparison of deferasirox versus deferoxamine for the treatment of transfusional iron overload in sickle cell disease Br J Haematol 136 2007 501 508
    • (2007) Br J Haematol , vol.136 , pp. 501-508
    • Vichinsky, E.1    Onyekwere, O.2    Porter, J.B.3
  • 108
    • 38849161460 scopus 로고    scopus 로고
    • Hematopoietic cell transplantation for thalassaemia and sickle cell disease: Past, present and future
    • M Bhatia, MC Walters Hematopoietic cell transplantation for thalassaemia and sickle cell disease: past, present and future Bone Marrow Transplant 41 2008 109 117
    • (2008) Bone Marrow Transplant , vol.41 , pp. 109-117
    • Bhatia, M.1    Walters, M.C.2
  • 109
    • 71849118976 scopus 로고    scopus 로고
    • Allogeneic hematopoietic stem-cell transplantation for sickle cell disease
    • MM Hsieh, EM Kang, CD Fitzhugh Allogeneic hematopoietic stem-cell transplantation for sickle cell disease N Engl J Med 361 2009 2309 2317
    • (2009) N Engl J Med , vol.361 , pp. 2309-2317
    • Hsieh, M.M.1    Kang, E.M.2    Fitzhugh, C.D.3
  • 110
    • 0035861452 scopus 로고    scopus 로고
    • Correction of sickle cell disease in transgenic mouse models by gene therapy
    • R Pawliuk, KA Westerman, ME Fabry Correction of sickle cell disease in transgenic mouse models by gene therapy Science 294 2001 2368 2371
    • (2001) Science , vol.294 , pp. 2368-2371
    • Pawliuk, R.1    Westerman, K.A.2    Fabry, M.E.3
  • 111
    • 77949441974 scopus 로고    scopus 로고
    • Hematopoietic stem cell gene transfer for the treatment of hemoglobin disorders
    • DA Persons Hematopoietic stem cell gene transfer for the treatment of hemoglobin disorders Hematology Am Soc Hematol Educ Program 2009 690 697
    • (2009) Hematology Am Soc Hematol Educ Program , pp. 690-697
    • Persons, D.A.1
  • 112
    • 37549030199 scopus 로고    scopus 로고
    • Treatment of sickle cell anemia mouse model with iPS cells generated from autologous skin
    • J Hanna, M Wernig, S Markoulaki Treatment of sickle cell anemia mouse model with iPS cells generated from autologous skin Science 318 2007 1920 1923
    • (2007) Science , vol.318 , pp. 1920-1923
    • Hanna, J.1    Wernig, M.2    Markoulaki, S.3
  • 113
    • 55549139821 scopus 로고    scopus 로고
    • Sibling history of asthma is a risk factor for pain in children with sickle cell anemia
    • JJ Field, EA Macklin, Y Yan, RC Strunk, MR DeBaun Sibling history of asthma is a risk factor for pain in children with sickle cell anemia Am J Hematol 83 2008 855 857
    • (2008) Am J Hematol , vol.83 , pp. 855-857
    • Field, J.J.1    MacKlin, E.A.2    Yan, Y.3    Strunk, R.C.4    Debaun, M.R.5
  • 114
    • 0037307055 scopus 로고    scopus 로고
    • Nocturnal oxygen saturation and painful sickle cell crises in children
    • DR Hargrave, A Wade, JP Evans, DK Hewes, FJ Kirkham Nocturnal oxygen saturation and painful sickle cell crises in children Blood 101 2003 846 848
    • (2003) Blood , vol.101 , pp. 846-848
    • Hargrave, D.R.1    Wade, A.2    Evans, J.P.3    Hewes, D.K.4    Kirkham, F.J.5
  • 115
    • 70449719110 scopus 로고    scopus 로고
    • A randomized, controlled clinical trial of ketoprofen for sickle-cell disease vaso-occlusive crises in adults
    • P Bartolucci, T El Murr, F Roudot-Thoraval A randomized, controlled clinical trial of ketoprofen for sickle-cell disease vaso-occlusive crises in adults Blood 114 2009 3742 3747
    • (2009) Blood , vol.114 , pp. 3742-3747
    • Bartolucci, P.1    El Murr, T.2    Roudot-Thoraval, F.3
  • 116
    • 0031573161 scopus 로고    scopus 로고
    • Randomized trial of oral morphine for painful episodes of sickle-cell disease in children
    • SJ Jacobson, BA Kopecky, P Joshi, N Babul Randomized trial of oral morphine for painful episodes of sickle-cell disease in children Lancet 350 1997 1358 1361
    • (1997) Lancet , vol.350 , pp. 1358-1361
    • Jacobson, S.J.1    Kopecky, B.A.2    Joshi, P.3    Babul, N.4
  • 118
    • 0028199660 scopus 로고
    • High-dose intravenous methylprednisolone therapy for pain in children and adolescents with sickle cell disease
    • TC Griffin, D McIntire, GR Buchanan High-dose intravenous methylprednisolone therapy for pain in children and adolescents with sickle cell disease N Engl J Med 330 1994 733 737
    • (1994) N Engl J Med , vol.330 , pp. 733-737
    • Griffin, T.C.1    McIntire, D.2    Buchanan, G.R.3
  • 119
    • 0035824175 scopus 로고    scopus 로고
    • Purified poloxamer 188 for treatment of acute vaso-occlusive crisis of sickle cell disease: A randomized controlled trial
    • EP Orringer, JF Casella, KI Ataga Purified poloxamer 188 for treatment of acute vaso-occlusive crisis of sickle cell disease: a randomized controlled trial JAMA 286 2001 2099 2106
    • (2001) JAMA , vol.286 , pp. 2099-2106
    • Orringer, E.P.1    Casella, J.F.2    Ataga, K.I.3
  • 120
    • 0037420269 scopus 로고    scopus 로고
    • Preliminary assessment of inhaled nitric oxide for acute vaso-occlusive crisis in pediatric patients with sickle cell disease
    • DL Weiner, PL Hibberd, P Betit, AB Cooper, CA Botelho, C Brugnara Preliminary assessment of inhaled nitric oxide for acute vaso-occlusive crisis in pediatric patients with sickle cell disease JAMA 289 2003 1136 1142
    • (2003) JAMA , vol.289 , pp. 1136-1142
    • Weiner, D.L.1    Hibberd, P.L.2    Betit, P.3    Cooper, A.B.4    Botelho, C.A.5    Brugnara, C.6
  • 122
    • 34249029657 scopus 로고    scopus 로고
    • Incidence of invasive pneumococcal disease among individuals with sickle cell disease before and after the introduction of the pneumococcal conjugate vaccine
    • NB Halasa, SM Shankar, TR Talbot Incidence of invasive pneumococcal disease among individuals with sickle cell disease before and after the introduction of the pneumococcal conjugate vaccine Clin Infect Dis 44 2007 1428 1433
    • (2007) Clin Infect Dis , vol.44 , pp. 1428-1433
    • Halasa, N.B.1    Shankar, S.M.2    Talbot, T.R.3
  • 123
    • 77956047860 scopus 로고    scopus 로고
    • Extracranial internal carotid arterial disease in children with sickle cell anaemia
    • CR Deane, D Goss, J Bartram Extracranial internal carotid arterial disease in children with sickle cell anaemia Haematologica 95 2010 1287 1292
    • (2010) Haematologica , vol.95 , pp. 1287-1292
    • Deane, C.R.1    Goss, D.2    Bartram, J.3
  • 124
    • 37249001371 scopus 로고    scopus 로고
    • Serum lactate dehydrogenase as a biomarker in children with sickle cell disease
    • S O'Driscoll, SE Height, MC Dick, DC Rees Serum lactate dehydrogenase as a biomarker in children with sickle cell disease Br J Haematol 140 2008 206 209
    • (2008) Br J Haematol , vol.140 , pp. 206-209
    • O'Driscoll, S.1    Height, S.E.2    Dick, M.C.3    Rees, D.C.4
  • 125
    • 33646508162 scopus 로고    scopus 로고
    • Pathophysiology and treatment of stroke in sickle-cell disease: Present and future
    • JA Switzer, DC Hess, FT Nichols, RJ Adams Pathophysiology and treatment of stroke in sickle-cell disease: present and future Lancet Neurol 5 2006 501 512
    • (2006) Lancet Neurol , vol.5 , pp. 501-512
    • Switzer, J.A.1    Hess, D.C.2    Nichols, F.T.3    Adams, R.J.4
  • 127
    • 3142590376 scopus 로고    scopus 로고
    • Declining stroke rates in Californian children with sickle cell disease
    • HJ Fullerton, RJ Adams, S Zhao, SC Johnston Declining stroke rates in Californian children with sickle cell disease Blood 104 2004 36 339
    • (2004) Blood , vol.104 , pp. 36-339
    • Fullerton, H.J.1    Adams, R.J.2    Zhao, S.3    Johnston, S.C.4
  • 129
    • 73949087363 scopus 로고    scopus 로고
    • Sickle cell disease and stroke
    • LA Verduzco, DG Nathan Sickle cell disease and stroke Blood 114 2009 5117 5125
    • (2009) Blood , vol.114 , pp. 5117-5125
    • Verduzco, L.A.1    Nathan, D.G.2
  • 130
    • 70349751401 scopus 로고    scopus 로고
    • Pial synangiosis in patients with moyamoya syndrome and sickle cell anemia: Perioperative management and surgical outcome
    • ER Smith, CD McClain, M Heeney, RM Scott Pial synangiosis in patients with moyamoya syndrome and sickle cell anemia: perioperative management and surgical outcome Neurosurg Focus 26 2009 1 8
    • (2009) Neurosurg Focus , vol.26 , pp. 1-8
    • Smith, E.R.1    McClain, C.D.2    Heeney, M.3    Scott, R.M.4
  • 131
    • 67650484216 scopus 로고    scopus 로고
    • Silent infarcts in young children with sickle cell disease
    • JL Kwiatkowski, RA Zimmerman, AN Pollock Silent infarcts in young children with sickle cell disease Br J Haematol 146 2009 300 305
    • (2009) Br J Haematol , vol.146 , pp. 300-305
    • Kwiatkowski, J.L.1    Zimmerman, R.A.2    Pollock, A.N.3
  • 133
    • 33744956531 scopus 로고    scopus 로고
    • Physiological correlates of intellectual function in children with sickle cell disease: Hypoxaemia, hyperaemia and brain infarction
    • AM Hogan, IM Pit-ten Cate, F Vargha-Khadem, M Prengler, FJ Kirkham Physiological correlates of intellectual function in children with sickle cell disease: hypoxaemia, hyperaemia and brain infarction Dev Sci 9 2006 379 387
    • (2006) Dev Sci , vol.9 , pp. 379-387
    • Hogan, A.M.1    Pit-Ten Cate, I.M.2    Vargha-Khadem, F.3    Prengler, M.4    Kirkham, F.J.5
  • 134
    • 56749163948 scopus 로고    scopus 로고
    • Pulmonary complications of sickle cell disease
    • MT Gladwin, E Vichinsky Pulmonary complications of sickle cell disease N Engl J Med 359 2008 2254 2265
    • (2008) N Engl J Med , vol.359 , pp. 2254-2265
    • Gladwin, M.T.1    Vichinsky, E.2
  • 135
    • 0034702282 scopus 로고    scopus 로고
    • Causes and outcomes of the acute chest syndrome in sickle cell disease
    • EP Vichinsky, LD Neumayr, AN Earles Causes and outcomes of the acute chest syndrome in sickle cell disease N Engl J Med 342 2000 1855 1865
    • (2000) N Engl J Med , vol.342 , pp. 1855-1865
    • Vichinsky, E.P.1    Neumayr, L.D.2    Earles, A.N.3
  • 136
    • 0032211192 scopus 로고    scopus 로고
    • Beneficial effect of intravenous dexamethasone in children with mild to moderately severe acute chest syndrome complicating sickle cell disease
    • JC Bernini, ZR Rogers, ES Sandler, JS Reisch, CT Quinn, GR Buchanan Beneficial effect of intravenous dexamethasone in children with mild to moderately severe acute chest syndrome complicating sickle cell disease Blood 92 1998 3082 3089
    • (1998) Blood , vol.92 , pp. 3082-3089
    • Bernini, J.C.1    Rogers, Z.R.2    Sandler, E.S.3    Reisch, J.S.4    Quinn, C.T.5    Buchanan, G.R.6
  • 137
    • 78650173478 scopus 로고    scopus 로고
    • Pulmonary Complications of Hematological Disease
    • R.J. Murray V.C. Broaddus T. Martin 5th edn. Elsevier Philadelphia, PA *et al.
    • RF Machado, MT Gladwin Pulmonary Complications of Hematological Disease RJ Murray VC Broaddus T Martin Murray and Nadel's Textbook of Respiratory Medicine 5th edn. 2010 Elsevier Philadelphia, PA 1999 2021
    • (2010) Murray and Nadel's Textbook of Respiratory Medicine , pp. 1999-2021
    • MacHado, R.F.1    Gladwin, M.T.2
  • 138
    • 77956530884 scopus 로고    scopus 로고
    • Prospective multicentric survey on pulmonary hypertension (PH) in adults with sickle cell disease
    • D Bachir, F Parent, L Hajji Prospective multicentric survey on pulmonary hypertension (PH) in adults with sickle cell disease Blood 114 2009 572
    • (2009) Blood , vol.114 , pp. 572
    • Bachir, D.1    Parent, F.2    Hajji, L.3
  • 139
    • 24944476691 scopus 로고    scopus 로고
    • Sildenafil therapy in patients with sickle cell disease and pulmonary hypertension
    • RF Machado, S Martyr, GJ Kato Sildenafil therapy in patients with sickle cell disease and pulmonary hypertension Br J Haematol 130 2005 445 453
    • (2005) Br J Haematol , vol.130 , pp. 445-453
    • MacHado, R.F.1    Martyr, S.2    Kato, G.J.3
  • 140
    • 33846338501 scopus 로고    scopus 로고
    • Diastolic dysfunction is an independent risk factor for death in patients with sickle cell disease
    • V Sachdev, RF Machado, Y Shizukuda Diastolic dysfunction is an independent risk factor for death in patients with sickle cell disease J Am Coll Cardiol 49 2007 472 479
    • (2007) J Am Coll Cardiol , vol.49 , pp. 472-479
    • Sachdev, V.1    MacHado, R.F.2    Shizukuda, Y.3
  • 141
    • 40949129196 scopus 로고    scopus 로고
    • Pulmonary hypertension and cor pulmonale during severe acute chest syndrome in sickle cell disease
    • A Mekontso Dessap, R Leon, A Habibi Pulmonary hypertension and cor pulmonale during severe acute chest syndrome in sickle cell disease Am J Respir Crit Care Med 177 2008 646 653
    • (2008) Am J Respir Crit Care Med , vol.177 , pp. 646-653
    • Mekontso Dessap, A.1    Leon, R.2    Habibi, A.3
  • 142
    • 59049085233 scopus 로고    scopus 로고
    • Sickle cell disease and the kidney
    • JI Scheinman Sickle cell disease and the kidney Nat Clin Pract Nephrol 5 2009 78 88
    • (2009) Nat Clin Pract Nephrol , vol.5 , pp. 78-88
    • Scheinman, J.I.1
  • 143
    • 72049092388 scopus 로고    scopus 로고
    • Renal function in infants with sickle cell anemia: Baseline data from the BABY HUG trial
    • RE Ware, RC Rees, SA Sarnaik Renal function in infants with sickle cell anemia: baseline data from the BABY HUG trial J Pediatr 156 2010 66 70
    • (2010) J Pediatr , vol.156 , pp. 66-70
    • Ware, R.E.1    Rees, R.C.2    Sarnaik, S.A.3
  • 144
    • 33845461527 scopus 로고    scopus 로고
    • Physical therapy alone compared with core decompression and physical therapy for femoral head osteonecrosis in sickle cell disease. Results of a multicenter study at a mean of three years after treatment
    • LD Neumayr, C Aguilar, AN Earles Physical therapy alone compared with core decompression and physical therapy for femoral head osteonecrosis in sickle cell disease. Results of a multicenter study at a mean of three years after treatment J Bone Joint Surg Am 88 2006 2573 2582
    • (2006) J Bone Joint Surg Am , vol.88 , pp. 2573-2582
    • Neumayr, L.D.1    Aguilar, C.2    Earles, A.N.3
  • 145
    • 85056049204 scopus 로고    scopus 로고
    • Percutaneous implantation of autologous bone marrow osteoprogenitor cells as treatment of bone avascular necrosis related to sickle cell disease
    • P Hernigou, G Daltro, P Filippini, MM Mukasa, O Manicom Percutaneous implantation of autologous bone marrow osteoprogenitor cells as treatment of bone avascular necrosis related to sickle cell disease Open Orthop J 2 2008 62 65
    • (2008) Open Orthop J , vol.2 , pp. 62-65
    • Hernigou, P.1    Daltro, G.2    Filippini, P.3    Mukasa, M.M.4    Manicom, O.5
  • 146
    • 43749114559 scopus 로고    scopus 로고
    • Retinal photocoagulation for proliferative sickle cell retinopathy: A prospective clinical trial with new sea fan classification
    • D Sayag, M Binaghi, EH Souied Retinal photocoagulation for proliferative sickle cell retinopathy: a prospective clinical trial with new sea fan classification Eur J Ophthalmol 18 2008 248 254
    • (2008) Eur J Ophthalmol , vol.18 , pp. 248-254
    • Sayag, D.1    Binaghi, M.2    Souied, E.H.3
  • 147
    • 33750607880 scopus 로고    scopus 로고
    • Intravitreal bevacizumab (Avastin) injection associated with regression of retinal neovascularization caused by sickle cell retinopathy
    • RC Siqueira, RA Costa, IU Scott, LP Cintra, R Jorge Intravitreal bevacizumab (Avastin) injection associated with regression of retinal neovascularization caused by sickle cell retinopathy Acta Ophthalmol Scand 84 2006 834 835
    • (2006) Acta Ophthalmol Scand , vol.84 , pp. 834-835
    • Siqueira, R.C.1    Costa, R.A.2    Scott, I.U.3    Cintra, L.P.4    Jorge, R.5
  • 149
    • 70350574017 scopus 로고    scopus 로고
    • Treatment of recurrent priapism in sickle cell anemia with finasteride: A new approach
    • D Rachid-Filho, AG Cavalcanti, LA Favorito, WS Costa, FJ Sampaio Treatment of recurrent priapism in sickle cell anemia with finasteride: a new approach Urology 74 2009 1054 1057
    • (2009) Urology , vol.74 , pp. 1054-1057
    • Rachid-Filho, D.1    Cavalcanti, A.G.2    Favorito, L.A.3    Costa, W.S.4    Sampaio, F.J.5
  • 150
    • 42049117005 scopus 로고    scopus 로고
    • Advances in clinical research in sickle cell disease
    • W Hagar, E Vichinsky Advances in clinical research in sickle cell disease Br J Haematol 141 2008 346 356
    • (2008) Br J Haematol , vol.141 , pp. 346-356
    • Hagar, W.1    Vichinsky, E.2


* 이 정보는 Elsevier사의 SCOPUS DB에서 KISTI가 분석하여 추출한 것입니다.