DEAP-HUS: Deficiency of CFHR plasma proteins and autoantibody-positive form of hemolytic uremic syndrome

Pediatric Nephrology

Volumn 25, Issue 10, 2010, Pages 2009-2019

  Zipfel, Peter F ^a,b   MacHe, Christoph ^c   Müller, Dominik ^d   Licht, Christoph ^e   Wigger, Marianne ^f   Skerka, Christine ^a  

^a HANS KNÖLL INSTITUTE   (Germany)

^b FRIEDRICH SCHILLER UNIVERSITY JENA   (Germany)

^c MEDICAL UNIVERSITY OF GRAZ   (Austria)

^d CHARITÉ UNIVERSITÄTSMEDIZIN BERLIN   (Germany)

^e HOSPITAL FOR SICK CHILDREN   (Canada)

^f UNIVERSITY OF ROSTOCK   (Germany)

Author keywords

CFHR1 CFHR3 deficiency; DEAP HUS; Factor H autoantibodies; Immunosuppression; Plasma therapy; Transplantation

Indexed keywords

AUTOANTIBODY; AZATHIOPRINE; COMPLEMENT FACTOR H ANTIBODY; COMPLEMENT FACTOR H RELATED PROTEIN 1; COMPLEMENT FACTOR H RELATED PROTEIN 3; CYCLOPHOSPHAMIDE; ECULIZUMAB; IMMUNOGLOBULIN; MYCOPHENOLIC ACID 2 MORPHOLINOETHYL ESTER; PLASMA PROTEIN; RITUXIMAB; UNCLASSIFIED DRUG;

ACUTE KIDNEY FAILURE; ANTIBODY DETECTION; ANTIBODY PRODUCTION; CHROMOSOME 1; CHROMOSOME DELETION; DEFICIENCY OF COMPLEMENT FACTOR H RELATED PLASMA PROTEIN AND AUTOANTIBODY POSITIVE FORM OF HEMOLYTIC UREMIC SYNDROME; ENZYME LINKED IMMUNOSORBENT ASSAY; HEMOLYTIC UREMIC SYNDROME; MICROANGIOPATHY; PLASMA TRANSFUSION; PLASMAPHERESIS; PRIORITY JOURNAL; PROTEIN STRUCTURE; REVIEW; THROMBOCYTOPENIA;

AUTOANTIBODIES; AUTOANTIGENS; BLOOD PROTEINS; CHILD; COMPLEMENT C3B INACTIVATOR PROTEINS; COMPLEMENT FACTOR H; HEMOLYTIC-UREMIC SYNDROME; HUMANS;

EID: 77956231486     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-010-1446-9     Document Type: Review

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