The intraflagellar transport protein Ift80 is essential for photoreceptor survival in a zebrafish model of jeune asphyxiating thoracic dystrophy

Investigative Ophthalmology and Visual Science

Volumn 51, Issue 7, 2010, Pages 3792-3799

  Hudak, Leah M ^a   Lunt, Shannon ^a   Chang, Chi Hsuan ^a   Winkler, Ethan ^a   Flammer, Halley ^a   Lindsey, Michael ^a   Perkins, Brian D ^a  

^a TEXAS A AND M UNIVERSITY   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CARRIER PROTEIN; CELL PROTEIN; INTRAFLAGELLAR TRANSPORT PROTEIN 80; MORPHOLINE DERIVATIVE; OPSIN; OPSIN ANTIBODY; PROTEIN ANTIBODY; PROTEIN BBS4; PROTEIN BBS8; UNCLASSIFIED DRUG; IFT80 PROTEIN, ZEBRAFISH; ZEBRAFISH PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL RECESSIVE DISORDER; BARDET BIEDL SYNDROME GENE; CELL DEATH; CELL SURVIVAL; CONTROLLED STUDY; EMBRYO; GENE; GENE INTERACTION; GENE TARGETING; HISTOPATHOLOGY; IMMUNOHISTOCHEMISTRY; IN SITU HYBRIDIZATION; JEUNE ASPHYXIATING THORACIC DYSTROPHY; NONHUMAN; PATHOPHYSIOLOGY; PHOTORECEPTOR; PHOTORECEPTOR OUTER SEGMENT; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN FUNCTION; PROTEIN INTERACTION; PROTEIN STABILITY; PROTEIN TRANSPORT; RETINA CONE; RETINA DEGENERATION; RETINA ROD; TRANSMISSION ELECTRON MICROSCOPY; VISUAL DISORDER; WESTERN BLOTTING; ZEBRA FISH; ANIMAL; ASPHYXIA; DISEASE MODEL; DRUG EFFECT; FLUORESCENT ANTIBODY TECHNIQUE; GENE SILENCING; GENETICS; HEREDITARY MULTIPLE EXOSTOSIS; KIDNEY POLYCYSTIC DISEASE; NICK END LABELING; PATHOLOGY; PHOTORECEPTOR CELL; PHYSIOLOGY; POLYACRYLAMIDE GEL ELECTROPHORESIS; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; THORAX DISEASE;

ANIMALS; ASPHYXIA; BLOTTING, WESTERN; CARRIER PROTEINS; CELL SURVIVAL; DISEASE MODELS, ANIMAL; ELECTROPHORESIS, POLYACRYLAMIDE GEL; EXOSTOSES, MULTIPLE HEREDITARY; FLUORESCENT ANTIBODY TECHNIQUE, INDIRECT; GENE SILENCING; IN SITU HYBRIDIZATION; IN SITU NICK-END LABELING; KIDNEY DISEASES, CYSTIC; PHOTORECEPTOR CELLS, VERTEBRATE; RETINAL DEGENERATION; REVERSE TRANSCRIPTASE POLYMERASE CHAIN REACTION; THORACIC DISEASES; ZEBRAFISH; ZEBRAFISH PROTEINS;

EID: 77955905294     PISSN: 01460404     EISSN: 15525783     Source Type: Journal    
DOI: 10.1167/iovs.09-4312     Document Type: Article

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