Loss of C. elegans BBS-7 and BBS-8 protein function results in cilia defects and compromised intraflagellar transport

Genes and Development

Volumn 18, Issue 13, 2004, Pages 1630-1642

  Blacque, Oliver E ^a   Reardon, Michael J ^b   Li, Chunmei ^a   McCarthy, Jonathan ^a   Mahjoub, Moe R ^a   Ansley, Stephen J ^c   Badano, Jose L ^c   Mah, Allan K ^a   Beales, Philip L ^e   Davidson, William S ^a   Johnsen, Robert C ^a   Audeh, Mark ^b   Plasterk, Ronald H A ^f   Baillie, David L ^a   Katsanis, Nicholas ^c,d   Quarmby, Lynne M ^a   Wicks, Stephen R ^b   Leroux, Michel R ^a  

^a SIMON FRASER UNIVERSITY   (Canada)

^b BOSTON COLLEGE   (United States)

^c JOHNS HOPKINS UNIVERSITY   (United States)

^d JOHNS HOPKINS UNIVERSITY   (United States)

^e UNIVERSITY COLLEGE LONDON   (United Kingdom)

^f HUBRECHT INSTITUTE   (Netherlands)

Author keywords

Bardet Biedl syndrome; Basal body; BBS proteins; Caenorhabditis elegans; Cilia and flagella; Intraflagellar transport

Indexed keywords

CAENORHABDITIS ELEGANS PROTEIN; POLARIS PROTEIN; PROTEIN; PROTEIN BBS 7; PROTEIN BBS 8; PROTEIN CHE 11; PROTEIN CHE 2; PROTEIN OSM 5; UNCLASSIFIED DRUG;

ARTICLE; AXONEME; BARDET BIEDL SYNDROME; BBS 7 GENE; BBS 8 GENE; BIOGENESIS; CAENORHABDITIS ELEGANS; CARDIOMYOPATHY; DEVELOPMENTAL DISORDER; DIABETES MELLITUS; EUKARYOTIC FLAGELLUM; GENE; GENE MUTATION; LEARNING DISORDER; NONHUMAN; OBESITY; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

ANIMALS; ANIMALS, GENETICALLY MODIFIED; CAENORHABDITIS ELEGANS; CAENORHABDITIS ELEGANS PROTEINS; CHEMOTAXIS; CILIA; FLAGELLA; HELMINTH PROTEINS; MUTATION; NERVE TISSUE PROTEINS; PROTEIN TRANSPORT; PROTEINS;

CAENORHABDITIS; CAENORHABDITIS ELEGANS; EUKARYOTA; INVERTEBRATA;

EID: 3042738924     PISSN: 08909369     EISSN: None     Source Type: Journal    
DOI: 10.1101/gad.1194004     Document Type: Article

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