-
1
-
-
0037013262
-
The first nucleotide binding domain of cystic fibrosis transmembrane conductance regulator is a site of stable nucleotide interaction, whereas the second is a site of rapid turnover
-
Aleksandrov LA, Aleksandrov AA, Chang X-B & Riordan JR (2002). The first nucleotide binding domain of cystic fibrosis transmembrane conductance regulator is a site of stable nucleotide interaction, whereas the second is a site of rapid turnover. J Biol Chem 277, 15419-15425.
-
(2002)
J Biol Chem
, vol.277
, pp. 15419-15425
-
-
Aleksandrov, L.A.1
Aleksandrov, A.A.2
Chang, X.-B.3
Riordan, J.R.4
-
2
-
-
0035918147
-
Differential interactions of nucleotides at the two nucleotide binding domains of the cystic fibrosis transmembrane conductance regulator
-
Aleksandrov LA, Mengos A, Chang X-B, Aleksandrov AA & Riordan JR (2001). Differential interactions of nucleotides at the two nucleotide binding domains of the cystic fibrosis transmembrane conductance regulator. J Biol Chem 276, 12918-12923.
-
(2001)
J Biol Chem
, vol.276
, pp. 12918-12923
-
-
Aleksandrov, L.A.1
Mengos, A.2
Chang, X.-B.3
Aleksandrov, A.A.4
Riordan, J.R.5
-
3
-
-
0032503962
-
Regulation of CFTR ion channel gating by MgATP
-
Aleksandrov AA & Riordan JR (1998). Regulation of CFTR ion channel gating by MgATP. FEBS Lett 431, 97-101.
-
(1998)
FEBS Lett
, vol.431
, pp. 97-101
-
-
Aleksandrov, A.A.1
Riordan, J.R.2
-
4
-
-
0027311276
-
Protein kinase A (PKA) still activates CFTR chloride channel after mutagenesis of all 10 PKA consensus phosphorylation sites
-
Chang X-B, Tabcharani JA, Hou Y-X, Jensen TJ, Kartner N, Alon N, Hanrahan JW & Riordan JR (1993). Protein kinase A (PKA) still activates CFTR chloride channel after mutagenesis of all 10 PKA consensus phosphorylation sites. J Biol Chem 268, 11304-11311.
-
(1993)
J Biol Chem
, vol.268
, pp. 11304-11311
-
-
Chang, X.-B.1
Tabcharani, J.A.2
Hou, Y.-X.3
Jensen, T.J.4
Kartner, N.5
Alon, N.6
Hanrahan, J.W.7
Riordan, J.R.8
-
5
-
-
4544232744
-
The ΔF508 mutation disrupts packing of the transmembrane segments of the cystic fibrosis transmembrane conductance regulator
-
Chen EY, Bartlett MC, Loo TW & Clarke DM (2004). The ΔF508 mutation disrupts packing of the transmembrane segments of the cystic fibrosis transmembrane conductance regulator. J Biol Chem 279, 39620-39627.
-
(2004)
J Biol Chem
, vol.279
, pp. 39620-39627
-
-
Chen, E.Y.1
Bartlett, M.C.2
Loo, T.W.3
Clarke, D.M.4
-
6
-
-
0025242929
-
Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis
-
Cheng SH, Gregory RJ, Marshall J, Paul S, Souza DW, White GA, O'Riordan C & Smith AE (1990). Defective intracellular transport and processing of CFTR is the molecular basis of most cystic fibrosis. Cell 63, 827-834.
-
(1990)
Cell
, vol.63
, pp. 827-834
-
-
Cheng, S.H.1
Gregory, R.J.2
Marshall, J.3
Paul, S.4
Souza, D.W.5
White, G.A.6
O'Riordan, C.7
Smith, A.E.8
-
7
-
-
0025348901
-
Stochastic properties of ion channel openings and bursts in a membrane patch that contains two channels: Evidence concerning the number of channels present when a record containing only single openings is observed
-
Colquhoun D & Hawkes AG (1990). Stochastic properties of ion channel openings and bursts in a membrane patch that contains two channels: Evidence concerning the number of channels present when a record containing only single openings is observed. Proc R Soc Lond B Biol Sci 240, 453-477.
-
(1990)
Proc R Soc Lond B Biol Sci
, vol.240
, pp. 453-477
-
-
Colquhoun, D.1
Hawkes, A.G.2
-
8
-
-
0026325533
-
'Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation
-
Dalemans W, Barbry P, Champigny G, Jallat S, Dott K, Dreyer D, Crystal RG, Parvani A, Lecocq J-P & Lazdunski M (1991). 'Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutation. Nature 354, 526-528.
-
(1991)
Nature
, vol.354
, pp. 526-528
-
-
Dalemans, W.1
Barbry, P.2
Champigny, G.3
Jallat, S.4
Dott, K.5
Dreyer, D.6
Crystal, R.G.7
Parvani, A.8
Lecocq, J.-P.9
Lazdunski, M.10
-
9
-
-
0026781952
-
Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive
-
Denning GM, Anderson MP, Amara JF, Marshall J, Smith AE & Welsh MJ (1992). Processing of mutant cystic fibrosis transmembrane conductance regulator is temperature-sensitive. Nature 358, 761-764.
-
(1992)
Nature
, vol.358
, pp. 761-764
-
-
Denning, G.M.1
Anderson, M.P.2
Amara, J.F.3
Marshall, J.4
Smith, A.E.5
Welsh, M.J.6
-
10
-
-
11444266284
-
The ΔF508 cystic fibrosis mutation impairs domain-domain interactions and arrests post-translational folding of CFTR
-
Du K, Sharma M & Lukacs GL (2005). The ΔF508 cystic fibrosis mutation impairs domain-domain interactions and arrests post-translational folding of CFTR. Nat Struct Mol Biol 12, 17-25.
-
(2005)
Nat Struct Mol Biol
, vol.12
, pp. 17-25
-
-
Du, K.1
Sharma, M.2
Lukacs, G.L.3
-
11
-
-
0032957204
-
Biosynthesis and degradation of CFTR
-
Kopito RR (1999). Biosynthesis and degradation of CFTR. Physiol Rev 79 (Suppl. 1), S167-S173.
-
(1999)
Physiol Rev
, vol.79
, Issue.SUPPL. 1
-
-
Kopito, R.R.1
-
12
-
-
19944432524
-
Impact of the ΔF508 mutation in first nucleotide-binding domain of human cystic fibrosis transmembrane conductance regulator on domain folding and structure
-
Lewis HA, Zhao X, Wang C, Sauder JM, Rooney I, Noland BW, Lorimer D, Kearins MC, Conners K, Condon B, Maloney PC, Guggino WB, Hunt JF & Emtage S (2005). Impact of the ΔF508 mutation in first nucleotide-binding domain of human cystic fibrosis transmembrane conductance regulator on domain folding and structure. J Biol Chem 280, 1346-1353.
-
(2005)
J Biol Chem
, vol.280
, pp. 1346-1353
-
-
Lewis, H.A.1
Zhao, X.2
Wang, C.3
Sauder, J.M.4
Rooney, I.5
Noland, B.W.6
Lorimer, D.7
Kearins, M.C.8
Conners, K.9
Condon, B.10
Maloney, P.C.11
Guggino, W.B.12
Hunt, J.F.13
Emtage, S.14
-
13
-
-
0029904733
-
ATPase activity of the cystic fibrosis transmembrane conductance regulator
-
Li C, Ramjeesingh M, Wang W, Garami E, Hewryk M, Lee D, Rommens JM, Galley K & Bear CE (1996). ATPase activity of the cystic fibrosis transmembrane conductance regulator. J Biol Chem 271, 28463 -28468.
-
(1996)
J Biol Chem
, vol.271
, pp. 28463-28468
-
-
Li, C.1
Ramjeesingh, M.2
Wang, W.3
Garami, E.4
Hewryk, M.5
Lee, D.6
Rommens, J.M.7
Galley, K.8
Bear, C.E.9
-
14
-
-
0033361889
-
Cystic fibrosis as a disease of misprocessing of the cystic fibrosis transmembrane conductance regulator glycoprotein
-
Riordan JR (1999). Cystic fibrosis as a disease of misprocessing of the cystic fibrosis transmembrane conductance regulator glycoprotein. Am J Hum Genet 64, 1499-1504.
-
(1999)
Am J Hum Genet
, vol.64
, pp. 1499-1504
-
-
Riordan, J.R.1
-
15
-
-
0033153764
-
Rescue of dysfunctional ΔF508-CFTR chloride channel activity by IBMX
-
Schultz BD, Frizzell RA & Bridges RJ (1999). Rescue of dysfunctional ΔF508-CFTR chloride channel activity by IBMX. J Membr Biol 170, 51-66.
-
(1999)
J Membr Biol
, vol.170
, pp. 51-66
-
-
Schultz, B.D.1
Frizzell, R.A.2
Bridges, R.J.3
-
17
-
-
14544300522
-
CFTR channel opening by ATP driven tight dimerization of its nucleotide-binding domains
-
Vergani P, Lockless SW, Nairn AC & Gadsby DC (2005). CFTR channel opening by ATP driven tight dimerization of its nucleotide-binding domains. Nature 433, 876-880.
-
(2005)
Nature
, vol.433
, pp. 876-880
-
-
Vergani, P.1
Lockless, S.W.2
Nairn, A.C.3
Gadsby, D.C.4
-
18
-
-
0034192547
-
Deletion of phenylalanine 508 causes attenuated phosphorylation-dependent activation of CFTR chloride channels
-
Wang F, Zeltwanger S, Hu S & Hwang T-C (2000). Deletion of phenylalanine 508 causes attenuated phosphorylation-dependent activation of CFTR chloride channels. J Physiol 524 3, 637-648.
-
(2000)
J Physiol
, vol.524
, Issue.3
, pp. 637-648
-
-
Wang, F.1
Zeltwanger, S.2
Hu, S.3
Hwang, T.-C.4
-
19
-
-
0028265949
-
Effect of ATP concentration on CFTR Cl channels: A kinetic analysis of channel regulation
-
Winter MC, Sheppard DN, Carson MR & Welsh MJ (1994). Effect of ATP concentration on CFTR Cl channels: A kinetic analysis of channel regulation. Biophys J 66, 1398-1408.
-
(1994)
Biophys J
, vol.66
, pp. 1398-1408
-
-
Winter, M.C.1
Sheppard, D.N.2
Carson, M.R.3
Welsh, M.J.4
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