Antagonistic effect of the matricellular signaling protein CCN3 on TGF-Β-and Wnt-mediated fibrillinogenesis in systemic sclerosis and marfan syndrome

Journal of Investigative Dermatology

Volumn 130, Issue 6, 2010, Pages 1514-1523

  Lemaire, Raphael ^a,b   Farina, Giuseppina ^a   Bayle, Julie ^a   Dimarzio, Michael ^a   Pendergrass, Sarah A ^c   Milano, Ausra ^c   Whitfield, Michael L ^c   Lafyatis, Robert ^a  

^a BOSTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b Research Department   (United States)

^c DARTMOUTH MEDICAL SCHOOL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

CELL PROTEIN; FIBRILLIN 1; NEPHROBLASTOMA OVEREXPRESSED PROTEIN; SMAD3 PROTEIN; TRANSFORMING GROWTH FACTOR BETA; WNT PROTEIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BLOOD SAMPLING; CONTROLLED STUDY; GENE CONTROL; GENE DELETION; GENE EXPRESSION; GENE OVEREXPRESSION; HUMAN; HUMAN TISSUE; IN VITRO STUDY; MARFAN SYNDROME; MOUSE; NONHUMAN; PRIORITY JOURNAL; SYSTEMIC SCLEROSIS;

ANIMALS; BIOPSY; CASE-CONTROL STUDIES; CELLS, CULTURED; DISEASE MODELS, ANIMAL; HUMANS; INTRACELLULAR SIGNALING PEPTIDES AND PROTEINS; MARFAN SYNDROME; MICE; MICE, MUTANT STRAINS; MICROFILAMENT PROTEINS; NEPHROBLASTOMA OVEREXPRESSED PROTEIN; PROTO-ONCOGENE PROTEINS; SCLERODERMA, SYSTEMIC; SIGNAL TRANSDUCTION; SKIN; SMAD3 PROTEIN; TRANSFORMING GROWTH FACTOR BETA; WNT PROTEINS;

EID: 77952429470     PISSN: 0022202X     EISSN: 15231747     Source Type: Journal    
DOI: 10.1038/jid.2010.15     Document Type: Article

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