Misfolding of short-chain acyl-CoA dehydrogenase leads to mitochondrial fission and oxidative stress

Molecular Genetics and Metabolism

Volumn 100, Issue 2, 2010, Pages 155-162

  Schmidt, S P ^a   Corydon, T J ^b   Pedersen, C B ^a   Bross, P ^a   Gregersen, N ^a  

^a AARHUS UNIVERSITY HOSPITAL   (Denmark)

^b AARHUS UNIVERSITY   (Denmark)

Author keywords

Mitochondrial dynamics; Mitochondrial dysfunction; Oxidative stress; Protein aggregation; Protein misfolding; Short chain acyl CoA dehydrogenase

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; COMPLEMENTARY DNA; MITOCHONDRIAL PROTEIN; PROTEIN SUBUNIT; REACTIVE OXYGEN METABOLITE;

ARTICLE; ASTROCYTE; DISORDERS OF MITOCHONDRIAL FUNCTIONS; GENE OVEREXPRESSION; HUMAN; HUMAN CELL; PRIORITY JOURNAL; PROTEIN AGGREGATION; PROTEIN FOLDING; SHORT CHAIN ACYL COENZYME A DEHYDROGENASE DEFICIENCY; WILD TYPE;

ASTROCYTES; BUTYRYL-COA DEHYDROGENASE; CELL LINE; HUMANS; LIPID METABOLISM, INBORN ERRORS; MITOCHONDRIA; OXIDATIVE STRESS; PROTEIN FOLDING; PROTEOSTASIS DEFICIENCIES; REACTIVE OXYGEN SPECIES; TRANSFECTION;

EID: 77951978533     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2010.03.009     Document Type: Article

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