A drosophila model of menkes disease reveals a role for DmATP7 in copper absorption and neurodevelopment

DMM Disease Models and Mechanisms

Volumn 3, Issue 1-2, 2010, Pages 84-91

  Bahadorani, Sepehr ^a,b   Bahadorani, Peyman ^a   Marcon, Edyta ^a   Walker, David W ^b   Hilliker, Arthur J ^a  

^a YORK UNIVERSITY   (Canada)

^b UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

COPPER; COPPER EXPORTING ADENOSINE TRIPHOSPHATASE; COPPER SULFATE; DROSOPHILA MELANOGASTER COPPER TRANSPORTING ADENOSINE TRIPHOSPHATASE 7; DROSOPHILA PROTEIN; MESSENGER RNA; TETRATHIOMOLYBDATE AMMONIUM; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ATOMIC ABSORPTION SPECTROMETRY; CONTROLLED STUDY; COPPER METABOLISM; DIET SUPPLEMENTATION; DMATP 7 GENE; DROSOPHILA MELANOGASTER; FEMALE; GENE; GENE OVEREXPRESSION; HISTOLOGY; INTESTINE ABSORPTION; MALE; MENKES SYNDROME; METAL RESPONSIVE TRANSCRIPTION FACTOR 1 GENE; METAMORPHOSIS; MORPHOLOGY; NERVOUS SYSTEM DEVELOPMENT; NONHUMAN; OXIDATIVE STRESS; PRIORITY JOURNAL; PROTEIN FUNCTION; QUANTITATIVE ANALYSIS; REAL TIME POLYMERASE CHAIN REACTION; REVERSE TRANSCRIPTION POLYMERASE CHAIN REACTION; RNA INTERFERENCE; SCANNING ELECTRON MICROSCOPY; SURVIVAL; TISSUE DISTRIBUTION; TRANSGENIC ANIMAL;

ABSORPTION; AGING; ANIMALS; CATION TRANSPORT PROTEINS; COPPER; DIETARY SUPPLEMENTS; DIGESTIVE SYSTEM; DISEASE MODELS, ANIMAL; DNA-BINDING PROTEINS; DROSOPHILA MELANOGASTER; GENE EXPRESSION REGULATION, DEVELOPMENTAL; GENES, INSECT; LARVA; MENKES KINKY HAIR SYNDROME; NERVOUS SYSTEM; OXIDATIVE STRESS; PUPA; RNA INTERFERENCE; SUPPRESSION, GENETIC; SURVIVAL ANALYSIS; TRANSCRIPTION FACTORS;

DROSOPHILA MELANOGASTER; MAMMALIA;

EID: 77649205678     PISSN: 17548403     EISSN: 17548411     Source Type: Journal    
DOI: 10.1242/dmm.002642     Document Type: Article

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