Correction of a mouse model of Menkes disease by the human Menkes gene

Biochimica et Biophysica Acta - Molecular Basis of Disease

Volumn 1762, Issue 4, 2006, Pages 485-493

  Llanos, Roxana M ^a   Ke, Bi Xia ^a   Wright, Magali ^a   Deal, Yolanda ^a   Monty, Francois ^a   Kramer, David R ^a   Mercer, Julian F B ^a  

^a DEAKIN UNIVERSITY   (Australia)

Author keywords

Brindled mutant mouse; CAG promoter; Copper transporting ATPase; Gene correction; Menkes disease; Menkes protein

Indexed keywords

COPPER; COPPER EXPORTING ADENOSINE TRIPHOSPHATASE; MENKES PROTEIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; COPPER DEFICIENCY; COPPER METABOLISM; FEMALE; GENE EXPRESSION; GENE THERAPY; KIDNEY; MALE; MENKES SYNDROME; MOSAICISM; MOUSE; NONHUMAN; PRIORITY JOURNAL; PROMOTER REGION; SMALL INTESTINE; TRANSGENIC MOUSE;

ADENOSINE TRIPHOSPHATASES; ANIMALS; CATION TRANSPORT PROTEINS; CHICKENS; COPPER; DISEASE MODELS, ANIMAL; FEMALE; FERTILITY; HUMANS; INTESTINE, SMALL; KIDNEY; MALE; MENKES KINKY HAIR SYNDROME; MICE; MICE, TRANSGENIC; MUTATION; PROMOTER REGIONS (GENETICS);

AGOUTI; ANIMALIA; MUS MUSCULUS;

EID: 33644774582     PISSN: 09254439     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbadis.2005.12.011     Document Type: Article

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