Glutaric aciduria type I and kynurenine pathway metabolites: A modified hypothesis

Journal of Inherited Metabolic Disease

Volumn 27, Issue 6, 2004, Pages 835-842

  Varadkar, S ^a   Surtees, R ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

3 HYDROXYGLUTARIC ACID; GLUTARIC ACID; GLUTARIC ACID DERIVATIVE; GLUTARYL COENZYME A DEHYDROGENASE; INDOLEAMINE 2,3 DIOXYGENASE; KYNURENINE; N METHYL DEXTRO ASPARTIC ACID RECEPTOR STIMULATING AGENT; NEUROTOXIN; QUINOLINIC ACID; UNCLASSIFIED DRUG;

ACIDURIA; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN NECROSIS; CONTROLLED STUDY; CORPUS STRIATUM; ENZYME ACTIVATION; ENZYME DEFICIENCY; GLUTARIC ACIDURIA TYPE 1; HUMAN; HYPOTHESIS; INBORN ERROR OF METABOLISM; MACROPHAGE ACTIVATION; METABOLITE; MONOCYTE; NERVE CELL STIMULATION; NERVOUS SYSTEM INFLAMMATION; NEUROPATHOLOGY; NEUROTOXICITY; NONHUMAN; PATHOGENESIS; PATHOPHYSIOLOGY; PUTAMEN; RAT;

AMINO ACID METABOLISM, INBORN ERRORS; ANIMALS; GLUTARATES; HUMANS; KYNURENINE; PHENOTYPE;

EID: 7244260428     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/B:BOLI.0000045767.42193.97     Document Type: Article

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