Protein synthesis and its control in neuronal cells with a focus on vanishing white matter disease

Biochemical Society Transactions

Volumn 37, Issue 6, 2009, Pages 1298-1310

  Pavitt, Graham D ^a   Proud, Christopher G ^b  

^a UNIVERSITY OF MANCHESTER   (United Kingdom)

^b UNIVERSITY OF SOUTHAMPTON   (United Kingdom)

Author keywords

Autism spectrum disorder (ASD); Childhood ataxia with central nervous system hypomyelination (CACH); Disease; Eukaryotic initiation factor 2B (eIF2B); Protein synthesis; Vanishing white matter (VWM)

Indexed keywords

ACTIVATING TRANSCRIPTION FACTOR 4; ELONGATION FACTOR; GLOBIN; INITIATION FACTOR; MAMMALIAN TARGET OF RAPAMYCIN; MESSENGER RNA; PROTEIN KINASE R;

AMINO TERMINAL SEQUENCE; BINDING AFFINITY; CHROMOSOME TRANSLOCATION; DISEASE SEVERITY; DOWN REGULATION; EUKARYOTIC CELL; GENE ACTIVATION; GENE EXPRESSION; GENE EXPRESSION REGULATION; GENE MUTATION; GENETIC ASSOCIATION; HUMAN; INTRON; NERVE CELL; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN BINDING; PROTEIN DOMAIN; PROTEIN FUNCTION; PROTEIN PHOSPHORYLATION; PROTEIN PROTEIN INTERACTION; PROTEIN SYNTHESIS; RETICULOCYTE; REVIEW; RIBOSOME; RNA TRANSLATION; TRANSLATION INITIATION; WHITE MATTER;

ANIMALS; ELONGATION FACTOR 2 KINASE; EUKARYOTIC INITIATION FACTOR-2B; GENE EXPRESSION REGULATION; HEREDITARY CENTRAL NERVOUS SYSTEM DEMYELINATING DISEASES; HUMANS; LONG-TERM SYNAPTIC DEPRESSION; MEMORY; MODELS, MOLECULAR; MULTIPLE SCLEROSIS; MUTATION; PROTEIN BIOSYNTHESIS; PROTEIN CONFORMATION;

EUKARYOTA;

EID: 70450207226     PISSN: 03005127     EISSN: 14708752     Source Type: Journal    
DOI: 10.1042/BST0371298     Document Type: Review

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