Spinocerebellar ataxia type 6 (SCA6): Neurodegeneration goes beyond the known brain predilection sites

Neuropathology and Applied Neurobiology

Volumn 35, Issue 5, 2009, Pages 515-527

  Gierga, K ^a   Schelhaas, H J ^b   Brunt, E R ^c   Seidel, K ^a   Scherzed, W ^a   Egensperger, R ^c   De Vos, R A I ^d   Den Dunnen, W ^e   Ippel, P F ^f   Petrasch Parwez, E ^g   Deller, T ^a   Schols L ^h   Rub U ^a  

^a GOETHE UNIVERSITY   (Germany)

^b UNIVERSITY OF MUNICH   (Germany)

^c RUHR UNIVERSITY BOCHUM   (Germany)

^d UNIVERSITY OF TÜBINGEN   (Germany)

^e RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

^f UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^g Laboratorium Pathologie Oost Nederland   (Netherlands)

^h UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

Author keywords

Channelopathies; Pathoanatomy; Polyglutamine diseases; Spinocerebellar ataxia type 6; Spinocerebellar ataxias

Indexed keywords

ADULT; AGED; ARTICLE; BRAIN DAMAGE; BRAIN REGION; BRAIN STEM; CELL LOSS; CELL NUCLEUS; CEREBELLAR ATAXIA; CEREBELLUM NUCLEUS; CLINICAL ARTICLE; CONTROLLED STUDY; FEMALE; HUMAN; MALE; MOTOR CORTEX; PRIORITY JOURNAL; PURKINJE CELL; PYRAMIDAL NERVE CELL; SPINOCEREBELLAR ATAXIA TYPE 6; SPINOCEREBELLAR DEGENERATION;

AGED; AUTOPSY; BRAIN; FEMALE; HUMANS; MALE; NERVE DEGENERATION; PEDIGREE; SPINOCEREBELLAR ATAXIAS;

EID: 69949140208     PISSN: 03051846     EISSN: 13652990     Source Type: Journal    
DOI: 10.1111/j.1365-2990.2009.01015.x     Document Type: Article

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