Involvement of the auditory brainstem system in spinocerebellar ataxia type 2 (SCA2), type 3 (SCA3) and type 7 (SCA7)

Neuropathology and Applied Neurobiology

Volumn 34, Issue 5, 2008, Pages 479-491

  Hoche, F ^a   Seidel, K ^a   Brunt, E R ^b   Auburger, G ^a   Schols L ^c   Burk K ^d   De Vos, R A ^e   Den Dunnen, W ^b   Bechmann, I ^a   Egensperger, R ^f   Van Broeckhoven, C ^g   Gierga, K ^a   Deller, T ^a   Rub U ^a  

^a GOETHE UNIVERSITY   (Germany)

^b UNIVERSITY MEDICAL CENTER GRONINGEN   (Netherlands)

^c UNIVERSITY OF TÜBINGEN   (Germany)

^d UNIVERSITY OF TÜBINGEN   (Germany)

^e Laboratorium Pathologie Oost Nederland   (Netherlands)

^f UNIVERSITY HOSPITAL ESSEN   (Germany)

^g UNIVERSITY OF ANTWERP   (Belgium)

Author keywords

Auditory system; Brainstem; Brainstem auditory evoked potentials; Polyglutamine diseases; Spinocerebellar ataxias

Indexed keywords

LIPOFUSCIN; POLYGLUTAMINE;

ADULT; AGED; ARTICLE; AUTOPSY; BRAIN STEM; CLINICAL FEATURE; COCHLEAR NUCLEUS; CONTROLLED STUDY; DYSARTHRIA; DYSPHAGIA; EVOKED BRAIN STEM AUDITORY RESPONSE; EXTRAPYRAMIDAL SYNDROME; EYE MOVEMENT DISORDER; FEMALE; GENETIC ASSOCIATION; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INFERIOR COLLICULUS; MALE; MYELINATED NERVE; NEUROPHYSIOLOGY; NISSL STAINING; PATHOLOGICAL ANATOMY; PRIORITY JOURNAL; PYRAMIDAL SIGN; SENSORY DYSFUNCTION; SPINOCEREBELLAR ATAXIA TYPE 2; SPINOCEREBELLAR ATAXIA TYPE 3; SPINOCEREBELLAR ATAXIA TYPE 7; SPINOCEREBELLAR DEGENERATION; SUPERIOR OLIVARY NUCLEUS; VESTIBULOCOCHLEAR NERVE;

EID: 52949135556     PISSN: 03051846     EISSN: 13652990     Source Type: Journal    
DOI: 10.1111/j.1365-2990.2007.00933.x     Document Type: Article

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