-
2
-
-
46749121818
-
A novel human disease with abnormal prion protein sensitive to protease
-
Gambetti P., Dong Z., Yuan J., Xiao X., Zheng M., Alshekhlee A., Castellani R., Cohen M., Barria M.A., Gonzalez-Romero D., Belay E.D., Schonberger L.B., Marder K., Harris C., Burke J.R., Montine T., Wisniewski T., Dickson D.W., Soto C., Hulette C.M., Mastrianni J.A., Kong Q., and Zou W.Q. A novel human disease with abnormal prion protein sensitive to protease. Ann. Neurol. 63 (2008) 697-708
-
(2008)
Ann. Neurol.
, vol.63
, pp. 697-708
-
-
Gambetti, P.1
Dong, Z.2
Yuan, J.3
Xiao, X.4
Zheng, M.5
Alshekhlee, A.6
Castellani, R.7
Cohen, M.8
Barria, M.A.9
Gonzalez-Romero, D.10
Belay, E.D.11
Schonberger, L.B.12
Marder, K.13
Harris, C.14
Burke, J.R.15
Montine, T.16
Wisniewski, T.17
Dickson, D.W.18
Soto, C.19
Hulette, C.M.20
Mastrianni, J.A.21
Kong, Q.22
Zou, W.Q.23
more..
-
3
-
-
0035066332
-
Alzheimer's disease: genes, proteins, and therapy
-
Selkoe D.J. Alzheimer's disease: genes, proteins, and therapy. Physiol. Rev. 81 (2001) 741-766
-
(2001)
Physiol. Rev.
, vol.81
, pp. 741-766
-
-
Selkoe, D.J.1
-
4
-
-
34547400403
-
Cellular prion protein regulates beta-secretase cleavage of the Alzheimer's amyloid precursor protein
-
Parkin E.T., Watt N.T., Hussain I., Eckman E.A., Eckman C.B., Manson J.C., Baybutt H.N., Turner A.J., and Hooper N.M. Cellular prion protein regulates beta-secretase cleavage of the Alzheimer's amyloid precursor protein. Proc. Natl. Acad. Sci. U. S. A. 104 (2007) 11062-11067
-
(2007)
Proc. Natl. Acad. Sci. U. S. A.
, vol.104
, pp. 11062-11067
-
-
Parkin, E.T.1
Watt, N.T.2
Hussain, I.3
Eckman, E.A.4
Eckman, C.B.5
Manson, J.C.6
Baybutt, H.N.7
Turner, A.J.8
Hooper, N.M.9
-
5
-
-
61349201380
-
Cellular prion protein mediates impairment of synaptic plasticity by amyloid-beta oligomers
-
Lauren J., Gimbel D.A., Nygaard H.B., Gilbert J.W., and Strittmatter S.M. Cellular prion protein mediates impairment of synaptic plasticity by amyloid-beta oligomers. Nature 457 (2009) 1128-1132
-
(2009)
Nature
, vol.457
, pp. 1128-1132
-
-
Lauren, J.1
Gimbel, D.A.2
Nygaard, H.B.3
Gilbert, J.W.4
Strittmatter, S.M.5
-
6
-
-
0037372585
-
PRNP Val129 homozygosity increases risk for early-onset Alzheimer's disease
-
Dermaut B., Croes E.A., Rademakers R., Van den Broeck M., Cruts M., Hofman A., van Duijn C.M., and Van Broeckhoven C. PRNP Val129 homozygosity increases risk for early-onset Alzheimer's disease. Ann. Neurol. 53 (2003) 409-412
-
(2003)
Ann. Neurol.
, vol.53
, pp. 409-412
-
-
Dermaut, B.1
Croes, E.A.2
Rademakers, R.3
Van den Broeck, M.4
Cruts, M.5
Hofman, A.6
van Duijn, C.M.7
Van Broeckhoven, C.8
-
7
-
-
3242778476
-
Prion protein codon 129 polymorphism and risk of Alzheimer disease
-
Riemenschneider M., Klopp N., Xiang W., Wagenpfeil S., Vollmert C., Muller U., Forstl H., Illig T., Kretzschmar H., and Kurz A. Prion protein codon 129 polymorphism and risk of Alzheimer disease. Neurology 63 (2004) 364-366
-
(2004)
Neurology
, vol.63
, pp. 364-366
-
-
Riemenschneider, M.1
Klopp, N.2
Xiang, W.3
Wagenpfeil, S.4
Vollmert, C.5
Muller, U.6
Forstl, H.7
Illig, T.8
Kretzschmar, H.9
Kurz, A.10
-
8
-
-
33745440706
-
Kuru in the 21st century-an acquired human prion disease with very long incubation periods
-
Collinge J., Whitfield J., McKintosh E., Beck J., Mead S., Thomas D.J., and Alpers M.P. Kuru in the 21st century-an acquired human prion disease with very long incubation periods. Lancet 367 (2006) 2068-2074
-
(2006)
Lancet
, vol.367
, pp. 2068-2074
-
-
Collinge, J.1
Whitfield, J.2
McKintosh, E.3
Beck, J.4
Mead, S.5
Thomas, D.J.6
Alpers, M.P.7
-
9
-
-
42049122359
-
Systematic review of therapeutic interventions in human prion disease
-
Stewart L.A., Rydzewska L.H., Keogh G.F., and Knight R.S. Systematic review of therapeutic interventions in human prion disease. Neurology 70 (2008) 1272-1281
-
(2008)
Neurology
, vol.70
, pp. 1272-1281
-
-
Stewart, L.A.1
Rydzewska, L.H.2
Keogh, G.F.3
Knight, R.S.4
-
10
-
-
34547881525
-
Therapeutic approaches for prion disorders
-
Ludewigs H., Zuber C., Vana K., Nikles D., Zerr I., and Weiss S. Therapeutic approaches for prion disorders. Expert Rev. Anti Infect. Ther. 5 (2007) 613-630
-
(2007)
Expert Rev. Anti Infect. Ther.
, vol.5
, pp. 613-630
-
-
Ludewigs, H.1
Zuber, C.2
Vana, K.3
Nikles, D.4
Zerr, I.5
Weiss, S.6
-
11
-
-
0034711993
-
Porphyrin and phthalocyanine antiscrapie compounds
-
Priola S.A., Raines A., and Caughey W.S. Porphyrin and phthalocyanine antiscrapie compounds. Science 287 (2000) 1503-1506
-
(2000)
Science
, vol.287
, pp. 1503-1506
-
-
Priola, S.A.1
Raines, A.2
Caughey, W.S.3
-
12
-
-
50949110043
-
Effects of new amphotericin analogues on the scrapie isoform of the prion protein
-
Soler L., Caffrey P., and McMahon H.E. Effects of new amphotericin analogues on the scrapie isoform of the prion protein. Biochim. Biophys. Acta 1780 (2008) 1162-1167
-
(2008)
Biochim. Biophys. Acta
, vol.1780
, pp. 1162-1167
-
-
Soler, L.1
Caffrey, P.2
McMahon, H.E.3
-
13
-
-
0038206890
-
Pentosan polysulfate as a prophylactic and therapeutic agent against prion disease
-
Dealler S., and Rainov N.G. Pentosan polysulfate as a prophylactic and therapeutic agent against prion disease. IDrugs 6 (2003) 470-478
-
(2003)
IDrugs
, vol.6
, pp. 470-478
-
-
Dealler, S.1
Rainov, N.G.2
-
14
-
-
0033537348
-
Prophylactic potential of pentosan polysulphate in transmissible spongiform encephalopathies
-
Farquhar C., Dickinson A., and Bruce M. Prophylactic potential of pentosan polysulphate in transmissible spongiform encephalopathies. Lancet 353 (1999) 117
-
(1999)
Lancet
, vol.353
, pp. 117
-
-
Farquhar, C.1
Dickinson, A.2
Bruce, M.3
-
15
-
-
34247214020
-
Antibodies to a nonconjugated prion protein peptide 95-123 interfere with PrP(Sc) propagation in prion-infected cells
-
Oboznaya M.B., Gilch S., Titova M.A., Koroev D.O., Volkova T.D., Volpina O.M., and Schatzl H.M. Antibodies to a nonconjugated prion protein peptide 95-123 interfere with PrP(Sc) propagation in prion-infected cells. Cell Mol. Neurobiol. 27 (2007) 271-284
-
(2007)
Cell Mol. Neurobiol.
, vol.27
, pp. 271-284
-
-
Oboznaya, M.B.1
Gilch, S.2
Titova, M.A.3
Koroev, D.O.4
Volkova, T.D.5
Volpina, O.M.6
Schatzl, H.M.7
-
16
-
-
33744478405
-
Clearance and prevention of prion infection in cell culture by anti-PrP antibodies
-
Pankiewicz J., Prelli F., Sy M.S., Kascsak R.J., Kascsak R.B., Spinner D.S., Carp R.I., Meeker H.C., Sadowski M., and Wisniewski T. Clearance and prevention of prion infection in cell culture by anti-PrP antibodies. Eur. J. Neurosci. 23 (2006) 2635-2647
-
(2006)
Eur. J. Neurosci.
, vol.23
, pp. 2635-2647
-
-
Pankiewicz, J.1
Prelli, F.2
Sy, M.S.3
Kascsak, R.J.4
Kascsak, R.B.5
Spinner, D.S.6
Carp, R.I.7
Meeker, H.C.8
Sadowski, M.9
Wisniewski, T.10
-
17
-
-
35148878615
-
Cyclodextrins inhibit replication of scrapie prion protein in cell culture
-
Prior M., Lehmann S., Sy M.S., Molloy B., and McMahon H.E. Cyclodextrins inhibit replication of scrapie prion protein in cell culture. J. Virol. 81 (2007) 11195-11207
-
(2007)
J. Virol.
, vol.81
, pp. 11195-11207
-
-
Prior, M.1
Lehmann, S.2
Sy, M.S.3
Molloy, B.4
McMahon, H.E.5
-
18
-
-
9444267651
-
The state of the prion
-
Weissmann C. The state of the prion. Nat. Rev. Microbiol. 2 (2004) 861-871
-
(2004)
Nat. Rev. Microbiol.
, vol.2
, pp. 861-871
-
-
Weissmann, C.1
-
19
-
-
0035253848
-
Sulfated glycans and elevated temperature stimulate PrP(Sc)-dependent cell-free formation of protease-resistant prion protein
-
Wong C., Xiong L.W., Horiuchi M., Raymond L., Wehrly K., Chesebro B., and Caughey B. Sulfated glycans and elevated temperature stimulate PrP(Sc)-dependent cell-free formation of protease-resistant prion protein. EMBO J. 20 (2001) 377-386
-
(2001)
EMBO J.
, vol.20
, pp. 377-386
-
-
Wong, C.1
Xiong, L.W.2
Horiuchi, M.3
Raymond, L.4
Wehrly, K.5
Chesebro, B.6
Caughey, B.7
-
20
-
-
0142184333
-
RNA molecules stimulate prion protein conversion
-
Deleault N.R., Lucassen R.W., and Supattapone S. RNA molecules stimulate prion protein conversion. Nature 425 (2003) 717-720
-
(2003)
Nature
, vol.425
, pp. 717-720
-
-
Deleault, N.R.1
Lucassen, R.W.2
Supattapone, S.3
-
23
-
-
33847607573
-
Comparison of CR36, a new heparan mimetic, and pentosan polysulfate in the treatment of prion diseases
-
Larramendy-Gozalo C., Barret A., Daudigeos E., Mathieu E., Antonangeli L., Riffet C., Petit E., Papy-Garcia D., Barritault D., Brown P., and Deslys J.P. Comparison of CR36, a new heparan mimetic, and pentosan polysulfate in the treatment of prion diseases. J. Gen. Virol. 88 (2007) 1062-1067
-
(2007)
J. Gen. Virol.
, vol.88
, pp. 1062-1067
-
-
Larramendy-Gozalo, C.1
Barret, A.2
Daudigeos, E.3
Mathieu, E.4
Antonangeli, L.5
Riffet, C.6
Petit, E.7
Papy-Garcia, D.8
Barritault, D.9
Brown, P.10
Deslys, J.P.11
-
24
-
-
41849091490
-
Intraventricular pentosan polysulphate in human prion diseases: an observational study in the UK
-
Bone I., Belton L., Walker A.S., and Darbyshire J. Intraventricular pentosan polysulphate in human prion diseases: an observational study in the UK. Eur. J. Neurol. 15 (2008) 458-464
-
(2008)
Eur. J. Neurol.
, vol.15
, pp. 458-464
-
-
Bone, I.1
Belton, L.2
Walker, A.S.3
Darbyshire, J.4
-
25
-
-
10444279209
-
Cyclodextrin-based pharmaceutics: past, present and future
-
Davis M.E., and Brewster M.E. Cyclodextrin-based pharmaceutics: past, present and future. Nat. Rev. Drug Discov. 3 (2004) 1023-1035
-
(2004)
Nat. Rev. Drug Discov.
, vol.3
, pp. 1023-1035
-
-
Davis, M.E.1
Brewster, M.E.2
-
26
-
-
42049112995
-
Structural behaviour of 2-hydroxypropyl-beta-cyclodextrin in water: molecular dynamics simulation studies
-
Yong C.W., Washington C., and Smith W. Structural behaviour of 2-hydroxypropyl-beta-cyclodextrin in water: molecular dynamics simulation studies. Pharm. Res. 25 (2008) 1092-1099
-
(2008)
Pharm. Res.
, vol.25
, pp. 1092-1099
-
-
Yong, C.W.1
Washington, C.2
Smith, W.3
-
27
-
-
0030813917
-
A basic compositional requirement of agents having heparin-like cell-modulating activities
-
Weisz P.B., Joullie M.M., Hunter C.M., Kumor K.M., Zhang Z., Levine E., Macarak E., Weiner D., and Barnathan E.S. A basic compositional requirement of agents having heparin-like cell-modulating activities. Biochem. Pharmacol. 54 (1997) 149-157
-
(1997)
Biochem. Pharmacol.
, vol.54
, pp. 149-157
-
-
Weisz, P.B.1
Joullie, M.M.2
Hunter, C.M.3
Kumor, K.M.4
Zhang, Z.5
Levine, E.6
Macarak, E.7
Weiner, D.8
Barnathan, E.S.9
-
28
-
-
0024593040
-
Control of angiogenesis with synthetic heparin substitutes
-
Folkman J., Weisz P.B., Joullie M.M., Li W.W., and Ewing W.R. Control of angiogenesis with synthetic heparin substitutes. Science 243 (1989) 1490-1493
-
(1989)
Science
, vol.243
, pp. 1490-1493
-
-
Folkman, J.1
Weisz, P.B.2
Joullie, M.M.3
Li, W.W.4
Ewing, W.R.5
-
29
-
-
0034682866
-
Identification of an epitope in the C terminus of normal prion protein whose expression is modulated by binding events in the N terminus
-
Li R., Liu T., Wong B.S., Pan T., Morillas M., Swietnicki W., O'Rourke K., Gambetti P., Surewicz W.K., and Sy M.S. Identification of an epitope in the C terminus of normal prion protein whose expression is modulated by binding events in the N terminus. J. Mol. Biol. 301 (2000) 567-573
-
(2000)
J. Mol. Biol.
, vol.301
, pp. 567-573
-
-
Li, R.1
Liu, T.2
Wong, B.S.3
Pan, T.4
Morillas, M.5
Swietnicki, W.6
O'Rourke, K.7
Gambetti, P.8
Surewicz, W.K.9
Sy, M.S.10
-
30
-
-
0025112476
-
An improved method for determining proteoglycans synthesized by chondrocytes in culture
-
Goldberg R.L., and Kolibas L.M. An improved method for determining proteoglycans synthesized by chondrocytes in culture. Connect Tissue Res. 24 (1990) 265-275
-
(1990)
Connect Tissue Res.
, vol.24
, pp. 265-275
-
-
Goldberg, R.L.1
Kolibas, L.M.2
-
31
-
-
34247483875
-
Prolongation of intrathecal and sciatic nerve blocks using a complex of levobupivacaine with maltosyl-beta-cyclodextrin in rats
-
tables of contents
-
Karashima K., Taniguchi M., Nakamura T., Takasaki M., Matsuo K., Irikura M., and Irie T. Prolongation of intrathecal and sciatic nerve blocks using a complex of levobupivacaine with maltosyl-beta-cyclodextrin in rats. Anesth. Analg. 104 (2007) 1121-1128 tables of contents
-
(2007)
Anesth. Analg.
, vol.104
, pp. 1121-1128
-
-
Karashima, K.1
Taniguchi, M.2
Nakamura, T.3
Takasaki, M.4
Matsuo, K.5
Irikura, M.6
Irie, T.7
-
32
-
-
0035013727
-
Influence of cyclodextrin ring substituents on folding-related aggregation of bovine carbonic anhydrase
-
Sharma L., and Sharma A. Influence of cyclodextrin ring substituents on folding-related aggregation of bovine carbonic anhydrase. Eur. J. Biochem. 268 (2001) 2456-2463
-
(2001)
Eur. J. Biochem.
, vol.268
, pp. 2456-2463
-
-
Sharma, L.1
Sharma, A.2
-
33
-
-
0033650826
-
Conformation and dynamics of heparin and heparan sulfate
-
Mulloy B., and Forster M.J. Conformation and dynamics of heparin and heparan sulfate. Glycobiology 10 (2000) 1147-1156
-
(2000)
Glycobiology
, vol.10
, pp. 1147-1156
-
-
Mulloy, B.1
Forster, M.J.2
-
34
-
-
0032904465
-
Metachromatic activity of beta-cyclodextrin sulfates as heparin mimics
-
Baumann R., and Rys P. Metachromatic activity of beta-cyclodextrin sulfates as heparin mimics. Int. J. Biol. Macromol. 24 (1999) 15-18
-
(1999)
Int. J. Biol. Macromol.
, vol.24
, pp. 15-18
-
-
Baumann, R.1
Rys, P.2
-
35
-
-
0023718086
-
The basis and applicability of the dimethylmethylene blue binding assay for sulfated glycosaminoglycans
-
Templeton D.M. The basis and applicability of the dimethylmethylene blue binding assay for sulfated glycosaminoglycans. Connect Tissue Res. 17 (1988) 23-32
-
(1988)
Connect Tissue Res.
, vol.17
, pp. 23-32
-
-
Templeton, D.M.1
-
36
-
-
0021338870
-
Metachromatic activity of heparin and heparin fragments
-
Grant A.C., Linhardt R.J., Fitzgerald G.L., Park J.J., and Langer R. Metachromatic activity of heparin and heparin fragments. Anal. Biochem. 137 (1984) 25-32
-
(1984)
Anal. Biochem.
, vol.137
, pp. 25-32
-
-
Grant, A.C.1
Linhardt, R.J.2
Fitzgerald, G.L.3
Park, J.J.4
Langer, R.5
-
37
-
-
0033104290
-
Cyclodextrin-based controlled drug release system
-
Hirayama F., and Uekama K. Cyclodextrin-based controlled drug release system. Adv. Drug Deliv. Rev. 36 (1999) 125-141
-
(1999)
Adv. Drug Deliv. Rev.
, vol.36
, pp. 125-141
-
-
Hirayama, F.1
Uekama, K.2
-
38
-
-
18244395819
-
Thermal characterization of natural and modified cyclodextrins using TG-MS combined technique
-
Éhen Z., Giordano F., Sztatisz J., Jicsinszky L., and Novák C. Thermal characterization of natural and modified cyclodextrins using TG-MS combined technique. J. Therm. Anal. Calorim. 80 (2005) 419-424
-
(2005)
J. Therm. Anal. Calorim.
, vol.80
, pp. 419-424
-
-
Éhen, Z.1
Giordano, F.2
Sztatisz, J.3
Jicsinszky, L.4
Novák, C.5
-
39
-
-
8244248457
-
Cyclodextrins: their future in drug formulation and delivery
-
Stella V.J., and Rajewski R.A. Cyclodextrins: their future in drug formulation and delivery. Pharm. Res. 14 (1997) 556-567
-
(1997)
Pharm. Res.
, vol.14
, pp. 556-567
-
-
Stella, V.J.1
Rajewski, R.A.2
-
40
-
-
0022647867
-
Hydroxypropyl-beta-cyclodextrin derivatives: influence of average degree of substitution on complexing ability and surface activity
-
Muller B.W., and Brauns U. Hydroxypropyl-beta-cyclodextrin derivatives: influence of average degree of substitution on complexing ability and surface activity. J. Pharm. Sci. 75 (1986) 571-572
-
(1986)
J. Pharm. Sci.
, vol.75
, pp. 571-572
-
-
Muller, B.W.1
Brauns, U.2
-
42
-
-
34547471499
-
Supramolecular chemistry of cyclodextrins in enzyme technology
-
Villalonga R., Cao R., and Fragoso A. Supramolecular chemistry of cyclodextrins in enzyme technology. Chem. Rev. 107 (2007) 3088-3116
-
(2007)
Chem. Rev.
, vol.107
, pp. 3088-3116
-
-
Villalonga, R.1
Cao, R.2
Fragoso, A.3
-
43
-
-
0141994735
-
Cellular heparan sulfate participates in the metabolism of prions
-
Ben-Zaken O., Tzaban S., Tal Y., Horonchik L., Esko J.D., Vlodavsky I., and Taraboulos A. Cellular heparan sulfate participates in the metabolism of prions. J. Biol. Chem. 278 (2003) 40041-40049
-
(2003)
J. Biol. Chem.
, vol.278
, pp. 40041-40049
-
-
Ben-Zaken, O.1
Tzaban, S.2
Tal, Y.3
Horonchik, L.4
Esko, J.D.5
Vlodavsky, I.6
Taraboulos, A.7
-
44
-
-
0037465821
-
Structural changes of the prion protein in lipid membranes leading to aggregation and fibrillization
-
Kazlauskaite J., Sanghera N., Sylvester I., Venien-Bryan C., and Pinheiro T.J. Structural changes of the prion protein in lipid membranes leading to aggregation and fibrillization. Biochemistry 42 (2003) 3295-3304
-
(2003)
Biochemistry
, vol.42
, pp. 3295-3304
-
-
Kazlauskaite, J.1
Sanghera, N.2
Sylvester, I.3
Venien-Bryan, C.4
Pinheiro, T.J.5
-
45
-
-
0035957944
-
Reconstitution of prion infectivity from solubilized protease-resistant PrP and nonprotein components of prion rods
-
Shaked G.M., Meiner Z., Avraham I., Taraboulos A., and Gabizon R. Reconstitution of prion infectivity from solubilized protease-resistant PrP and nonprotein components of prion rods. J. Biol. Chem. 276 (2001) 14324-14328
-
(2001)
J. Biol. Chem.
, vol.276
, pp. 14324-14328
-
-
Shaked, G.M.1
Meiner, Z.2
Avraham, I.3
Taraboulos, A.4
Gabizon, R.5
-
46
-
-
0032119526
-
Cyclodextrin drug carrier systems
-
Uekama K., Hirayama F., and Irie T. Cyclodextrin drug carrier systems. Chem. Rev. 98 (1998) 2045-2076
-
(1998)
Chem. Rev.
, vol.98
, pp. 2045-2076
-
-
Uekama, K.1
Hirayama, F.2
Irie, T.3
|