In ataxia-teleangiectasia betamethasone response is inversely correlated to cerebellar atrophy and directly to antioxidative capacity

European Journal of Neurology

Volumn 16, Issue 6, 2009, Pages 755-759

  Russo, I ^a   Cosentino, C ^b   Del Giudice, E ^a   Broccoletti, T ^a   Amorosi, S ^a   Cirillo, E ^a   Aloj, G ^a   Fusco, A ^a   Costanzo, V ^b   Pignata, C ^a  

^a UNIVERSITY OF NAPLES FEDERICO II   (Italy)

^b London Research Institute   (United Kingdom)

Author keywords

Ataxia teleangiectasia; Betamethasone; Neurological features; Reactive oxygen species

Indexed keywords

BETAMETHASONE; GLUTATHIONE; REACTIVE OXYGEN METABOLITE;

ADULT; ARTICLE; ATAXIA TELANGIECTASIA; CEREBELLUM ATROPHY; CHILD; COLORIMETRY; DISEASE SEVERITY; DRUG RESPONSE; FEMALE; HUMAN; HUMAN CELL; LIPID PEROXIDATION; LYMPHOCYTE; MALE; PRESCHOOL CHILD; PRIORITY JOURNAL; RATING SCALE; SCHOOL CHILD; STEROID THERAPY;

ADOLESCENT; ADULT; ANTI-INFLAMMATORY AGENTS; ANTIOXIDANTS; ATAXIA TELANGIECTASIA; ATROPHY; BETAMETHASONE; CELLS, CULTURED; CEREBELLAR DISEASES; CEREBELLUM; CHILD; CHILD, PRESCHOOL; DISEASE PROGRESSION; FEMALE; GLUTATHIONE; HUMANS; LIPID PEROXIDATION; MALE; OXIDATIVE STRESS; REACTIVE OXYGEN SPECIES; SEVERITY OF ILLNESS INDEX; TREATMENT OUTCOME; YOUNG ADULT;

EID: 65449119169     PISSN: 13515101     EISSN: 14681331     Source Type: Journal    
DOI: 10.1111/j.1468-1331.2009.02600.x     Document Type: Article

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