Bile duct proliferation in Jag1/fringe heterozygous mice identifies candidate modifiers of the Alagille syndrome hepatic phenotype

Hepatology

Volumn 48, Issue 6, 2008, Pages 1989-1997

  Ryan, Matthew J ^a,b   Bales, Christina ^a   Nelson, Anthony ^a   Gonzalez, Dorian M ^a   Underkoffler, Lara ^a   Segalov, Michelle ^a   Wilson Rawls, Jeanne ^c,d   Cole, Susan E ^e   Moran, Jennifer L ^f   Russo, Pierre ^a,b   Spinner, Nancy B ^a,b   Kusumi, Kenro ^a,b,d   Loomes, Kathleen M ^a,b  

^a CHILDREN S HOSPITAL OF PHILADELPHIA   (United States)

^b UNIVERSITY OF PENNSYLVANIA   (United States)

^c ARIZONA STATE UNIVERSITY   (United States)

^d UNIVERSITY OF ARIZONA COLLEGE OF MEDICINE   (United States)

^e OHIO STATE UNIVERSITY   (United States)

^f BROAD INSTITUTE OF MIT AND HARVARD   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FRINGE PROTEIN; GLYCOSYLTRANSFERASE; JAGGED1; LUNATIC FRINGE PROTEIN; MANIC FRINGE PROTEIN; NOTCH RECEPTOR; RADICAL FRINGE PROTEIN; TRANSFERASE; UNCLASSIFIED DRUG; CALCIUM BINDING PROTEIN; LFNG PROTEIN, MOUSE; MEMBRANE PROTEIN; MFNG PROTEIN, MOUSE; PROTEIN; RFNG PROTEIN, MOUSE; SERRATE PROTEINS; SIGNAL PEPTIDE;

ALAGILLE SYNDROME; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BILE DUCT DISEASE; BILIARY TRACT FIBROSIS; CONTROLLED STUDY; DEVELOPMENTAL DISORDER; DEVELOPMENTAL STAGE; FEMALE; GENE FUNCTION; GENE MUTATION; HETEROZYGOSITY; MALE; MOUSE; MOUSE MUTANT; NEWBORN PERIOD; NONHUMAN; PATHOGENESIS; PHENOTYPIC VARIATION; PORTAL VEIN; PRIORITY JOURNAL; ANIMAL; BILE DUCT; C57BL MOUSE; CELL PROLIFERATION; CONGENITAL MALFORMATION; DISEASE MODEL; GENETICS; LIVER; METABOLISM; MUTATION; PATHOLOGY; PHENOTYPE; PHYSIOLOGY; SIGNAL TRANSDUCTION;

ALAGILLE SYNDROME; ANIMALS; BILE DUCTS; CALCIUM-BINDING PROTEINS; CELL PROLIFERATION; DISEASE MODELS, ANIMAL; GLYCOSYLTRANSFERASES; INTERCELLULAR SIGNALING PEPTIDES AND PROTEINS; LIVER; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MUTATION; PHENOTYPE; PROTEINS; SIGNAL TRANSDUCTION;

EID: 58149396934     PISSN: 02709139     EISSN: None     Source Type: Journal    
DOI: 10.1002/hep.22538     Document Type: Article

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