Inhibitory control over Ca2+ sparks via mechanosensitive channels is disrupted in dystrophin deficient muscle but restored by mini-dystrophin expression

PLoS ONE

Volumn 3, Issue 11, 2008, Pages

  Teichmann, Martin D H ^a   Wegner, Frederic V ^a   Fink, Rainer H A ^a   Chamberlain, Jeffrey S ^b   Launikonis, Bradley S ^c   Martinac, Boris ^c   Friedrich, Oliver ^a,c  

^a UNIVERSITY OF HEIDELBERG   (Germany)

^b UNIVERSITY OF WASHINGTON   (United States)

^c UNIVERSITY OF QUEENSLAND   (Australia)

Author keywords

[No Author keywords available]

Indexed keywords

CALCIUM; DYSTROPHIN; METHOTREXATE; PEPTIDE; RYANODINE RECEPTOR; SPIDER PEPTIDE; STREPTOMYCIN; UNCLASSIFIED DRUG; CALCIUM CHANNEL L TYPE; ION CHANNEL;

ANIMAL TISSUE; ARTICLE; CALCIUM TRANSPORT; CELL MEMBRANE DEPOLARIZATION; CONFOCAL MICROSCOPY; CONTROLLED STUDY; DUCHENNE MUSCULAR DYSTROPHY; GENE REPRESSION; GENE TRANSFER; HUMAN; HUMAN TISSUE; MECHANOTRANSDUCTION; MEMBRANE POTENTIAL; MOUSE; MUSCLE ISOTONIC CONTRACTION; NONHUMAN; PATHOGENESIS; PROTEIN EXPRESSION; SKELETAL MUSCLE; ADULT; ANIMAL; C57BL MOUSE; CALCIUM SIGNALING; CELL MEMBRANE POTENTIAL; CYTOLOGY; GENETICS; METABOLISM; OSMOTIC PRESSURE; PATHOPHYSIOLOGY; PHYSIOLOGY; TRANSGENIC MOUSE; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE;

ARANEAE; MUS;

ADULT; ANIMALS; CALCIUM CHANNELS, L-TYPE; CALCIUM SIGNALING; DYSTROPHIN; HUMANS; ION CHANNELS; MECHANOTRANSDUCTION, CELLULAR; MEMBRANE POTENTIALS; MICE; MICE, INBRED C57BL; MICE, INBRED MDX; MICE, TRANSGENIC; MUSCLE FIBERS, SKELETAL; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, DUCHENNE; OSMOTIC PRESSURE; RYANODINE RECEPTOR CALCIUM RELEASE CHANNEL;

EID: 56149120851     PISSN: None     EISSN: 19326203     Source Type: Journal    
DOI: 10.1371/journal.pone.0003644     Document Type: Article

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