Epidermal expression of the truncated prelamin A causing Hutchinson - Gilford progeria syndrome: Effects on keratinocytes, hair and skin

Human Molecular Genetics

Volumn 17, Issue 15, 2008, Pages 2357-2369

  Wang, Yuexia ^a,b   Panteleyev, Andrey A ^c   Owens, David M ^a   Djabali, Karima ^a   Stewart, Colin L ^d   Worman, Howard J ^a,b  

^a Columbia University ^*  (United States)

^b NewYork Presbyterian Hospital   (United States)

^c UNIVERSITY OF DUNDEE   (United Kingdom)

^d INSTITUTE OF MEDICAL BIOLOGY   (Singapore)

Author keywords

[No Author keywords available]

Indexed keywords

CYTOKERATIN 14; LAMIN A; PRELAMIN A; PROGERIN; PROTEIN; PROTEIN FARNESYLTRANSFERASE INHIBITOR; PROTEIN PRECURSOR;

AGING; ALOPECIA; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; ARTICLE; CELL IMMORTALIZATION; CELL ISOLATION; CELL NUCLEUS; CELL NUCLEUS MEMBRANE; CONTROLLED STUDY; ENZYME INHIBITION; EPIDERMIS; HAIR; HAIR GROWTH; KERATINOCYTE; MALE; MOUSE; NONHUMAN; POINT MUTATION; PRIORITY JOURNAL; PROGERIA; PROMOTER REGION; RNA SPLICING; SKIN; SKIN MALFORMATION; SKIN STRUCTURE; SKINFOLD THICKNESS; TRANSGENIC MOUSE; WOUND HEALING;

ANIMALS; CELL NUCLEUS; CELL NUCLEUS SHAPE; EPIDERMIS; FARNESYLTRANSTRANSFERASE; HAIR; HUMANS; KERATINOCYTES; MICE; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; NUCLEAR PROTEINS; PROGERIA; PROTEIN PRECURSORS; SKIN; WOUND HEALING;

MUS; MUS MUSCULUS;

EID: 48049117058     PISSN: 09646906     EISSN: 14602083     Source Type: Journal    
DOI: 10.1093/hmg/ddn136     Document Type: Article

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