-
1
-
-
0020391968
-
Clinical limits of amyotrophic lateral sclerosis
-
Rowland L. (Ed), Raven, New York
-
Mulder D. Clinical limits of amyotrophic lateral sclerosis. In: Rowland L. (Ed). Human motor neuron diseases (1982), Raven, New York 15-22
-
(1982)
Human motor neuron diseases
, pp. 15-22
-
-
Mulder, D.1
-
2
-
-
0008787510
-
The epidemiology of neurologic disease
-
Joynt R. (Ed), J.B. Lippincot, Philadelphia
-
Kurtzke J., and Kurland L. The epidemiology of neurologic disease. In: Joynt R. (Ed). Clinical neurology (1989), J.B. Lippincot, Philadelphia 1-43
-
(1989)
Clinical neurology
, pp. 1-43
-
-
Kurtzke, J.1
Kurland, L.2
-
3
-
-
0028097839
-
A controlled trial of Riluzole in amyotrophic lateral sclerosis
-
Bensimon G., Lacomblez L., and Meininger V. A controlled trial of Riluzole in amyotrophic lateral sclerosis. N Engl J Med 330 (1994) 585-591
-
(1994)
N Engl J Med
, vol.330
, pp. 585-591
-
-
Bensimon, G.1
Lacomblez, L.2
Meininger, V.3
-
4
-
-
0029977337
-
Dose-ranging study of riluzole in amyotrophic lateral sclerosis
-
Lacomblez L., Bensimon G., Leigh P., Guillett P., and Meininger V. Dose-ranging study of riluzole in amyotrophic lateral sclerosis. Lancet 347 (1996) 1425-1431
-
(1996)
Lancet
, vol.347
, pp. 1425-1431
-
-
Lacomblez, L.1
Bensimon, G.2
Leigh, P.3
Guillett, P.4
Meininger, V.5
-
5
-
-
0027401203
-
Mutations in Cu/Zn superoxide dismutase are associated with familial amyotrophic lateral sclerosis
-
Rosen D., Siddique T., Patterson D., Figlewicz D., Sapp P., Hentati A., et al. Mutations in Cu/Zn superoxide dismutase are associated with familial amyotrophic lateral sclerosis. Nature 362 (1993) 59-62
-
(1993)
Nature
, vol.362
, pp. 59-62
-
-
Rosen, D.1
Siddique, T.2
Patterson, D.3
Figlewicz, D.4
Sapp, P.5
Hentati, A.6
-
6
-
-
0030898560
-
Diagnosis and progression of ALS
-
Mitsumoto H. Diagnosis and progression of ALS. Neurology 48 (1997) S2-S8
-
(1997)
Neurology
, vol.48
-
-
Mitsumoto, H.1
-
7
-
-
0031724091
-
Diagnosis of amyotrophic lateral sclerosis
-
Rowland L. Diagnosis of amyotrophic lateral sclerosis. J Neurol Sci 160 Suppl (1998) 6-24
-
(1998)
J Neurol Sci
, vol.160
, Issue.SUPPL
, pp. 6-24
-
-
Rowland, L.1
-
8
-
-
0028142392
-
El Escorial World Federation of Neurology criteria for the diagnosis of amyotrophic lateral sclerosis
-
Brooks B. El Escorial World Federation of Neurology criteria for the diagnosis of amyotrophic lateral sclerosis. J Neurol Sci 124 (1994) 96-107
-
(1994)
J Neurol Sci
, vol.124
, pp. 96-107
-
-
Brooks, B.1
-
9
-
-
4244214320
-
Upper and lower motor neuron function and muscle weakness in amyotrophic lateral sclerosis
-
Kent-Braun J., Walker C., and Weiner M. Upper and lower motor neuron function and muscle weakness in amyotrophic lateral sclerosis. Neurology 46 (1996) A472
-
(1996)
Neurology
, vol.46
-
-
Kent-Braun, J.1
Walker, C.2
Weiner, M.3
-
10
-
-
0032843024
-
Motor neuron diseases: comparison of single-voxel proton MR spectroscopy of the motor cortex with MR imaging of the brain
-
Chan S., Sungu D., Douglas-Akinwande A., Lange D., and Rowland L. Motor neuron diseases: comparison of single-voxel proton MR spectroscopy of the motor cortex with MR imaging of the brain. Radiology 212 (1999) 763-769
-
(1999)
Radiology
, vol.212
, pp. 763-769
-
-
Chan, S.1
Sungu, D.2
Douglas-Akinwande, A.3
Lange, D.4
Rowland, L.5
-
11
-
-
0033595564
-
Diffusion tensor MRI assesses corticospinal tract damage in ALS
-
Ellis C., Simmons A., Jones D., Bland J., Dawson J., Horsfield M., et al. Diffusion tensor MRI assesses corticospinal tract damage in ALS. Neurology 53 (1999) 1051-1058
-
(1999)
Neurology
, vol.53
, pp. 1051-1058
-
-
Ellis, C.1
Simmons, A.2
Jones, D.3
Bland, J.4
Dawson, J.5
Horsfield, M.6
-
12
-
-
0027948962
-
Detection of cortical neuron loss in motor neuron disease by proton magnetic resonance spectroscopic imaging in vivo
-
Pioro E., Antel J., Cashman N., and Arnold D. Detection of cortical neuron loss in motor neuron disease by proton magnetic resonance spectroscopic imaging in vivo. Neurology 44 (1994) 1933-1938
-
(1994)
Neurology
, vol.44
, pp. 1933-1938
-
-
Pioro, E.1
Antel, J.2
Cashman, N.3
Arnold, D.4
-
13
-
-
34247123630
-
Detection of ALS by proton magnetic resonance imaging
-
Suhy J., Schuff N., Maudslley A., Weiner M., and Miller R. Detection of ALS by proton magnetic resonance imaging. Neurology 54 (2000) A254-A255
-
(2000)
Neurology
, vol.54
-
-
Suhy, J.1
Schuff, N.2
Maudslley, A.3
Weiner, M.4
Miller, R.5
-
14
-
-
0037066081
-
Early detection and longitudinal changes in amyotrophic lateral sclerosis by (1) H MRSI
-
Suhy J., Miller R., Rule R., Schuff N., Licht J., Dronsky V., et al. Early detection and longitudinal changes in amyotrophic lateral sclerosis by (1) H MRSI. Neurology 58 (2002) 773-779
-
(2002)
Neurology
, vol.58
, pp. 773-779
-
-
Suhy, J.1
Miller, R.2
Rule, R.3
Schuff, N.4
Licht, J.5
Dronsky, V.6
-
15
-
-
0742323507
-
Diffusion tensor MRI of early upper motor neuron involvement in amyotrophic lateral sclerosis
-
Sach M., Winkler G., Glauche V., Liepert J., Heimbach B., Koch M., Buchel C., and Weiller C. Diffusion tensor MRI of early upper motor neuron involvement in amyotrophic lateral sclerosis. Brain 127 (2004) 340-350
-
(2004)
Brain
, vol.127
, pp. 340-350
-
-
Sach, M.1
Winkler, G.2
Glauche, V.3
Liepert, J.4
Heimbach, B.5
Koch, M.6
Buchel, C.7
Weiller, C.8
-
16
-
-
0028284779
-
Motor neuron degeneration in mice that express a human Cu/Zn superoxide dismutase mutation
-
Gurney M., Pu H., Chiu A., Dal Canto M., Polchow C., Alexander D., et al. Motor neuron degeneration in mice that express a human Cu/Zn superoxide dismutase mutation. Science 264 (1994) 1772-1775
-
(1994)
Science
, vol.264
, pp. 1772-1775
-
-
Gurney, M.1
Pu, H.2
Chiu, A.3
Dal Canto, M.4
Polchow, C.5
Alexander, D.6
-
17
-
-
0037013264
-
Decreased metallation and activity in subsets of mutant superoxide dismutases associated with familial ALS
-
Hayward L., Rodriguez J., Kim J., Tiwari A., Goto J., Cabelli D., et al. Decreased metallation and activity in subsets of mutant superoxide dismutases associated with familial ALS. J Biol Chem (2002) 15923-I5931
-
(2002)
J Biol Chem
-
-
Hayward, L.1
Rodriguez, J.2
Kim, J.3
Tiwari, A.4
Goto, J.5
Cabelli, D.6
-
18
-
-
0032430185
-
Caspase-1 is activated in neural cells and tissue with amyotrophic lateral sclerosis-associated mutations in copper-zinc superoxide dismutase
-
Pasinelli P., Borchelt D., Houseweart M., Cleveland D., and Brown R. Caspase-1 is activated in neural cells and tissue with amyotrophic lateral sclerosis-associated mutations in copper-zinc superoxide dismutase. Proc Natl Acad Sci USA 95 (1998) 15763-15768
-
(1998)
Proc Natl Acad Sci USA
, vol.95
, pp. 15763-15768
-
-
Pasinelli, P.1
Borchelt, D.2
Houseweart, M.3
Cleveland, D.4
Brown, R.5
-
19
-
-
0034610328
-
Caspase-1 and -3 are sequentially activated in motor neuron death in Cu/Zn superoxide dismutase mediated familial amyotrophic lateral sclerosis
-
Pasinelli P., Houseweart M., Brown R., and Cleveland D. Caspase-1 and -3 are sequentially activated in motor neuron death in Cu/Zn superoxide dismutase mediated familial amyotrophic lateral sclerosis. Proc Natl Acad Sci USA 97 (2000) 13901-13906
-
(2000)
Proc Natl Acad Sci USA
, vol.97
, pp. 13901-13906
-
-
Pasinelli, P.1
Houseweart, M.2
Brown, R.3
Cleveland, D.4
-
20
-
-
0035516124
-
From Charcot to Lou Gehrig: deciphering selective motor neuron death in ALS
-
Cleveland D., and Rothstein J. From Charcot to Lou Gehrig: deciphering selective motor neuron death in ALS. Nat Rev Neurosci 2 (2001) 806-819
-
(2001)
Nat Rev Neurosci
, vol.2
, pp. 806-819
-
-
Cleveland, D.1
Rothstein, J.2
-
21
-
-
0034785509
-
The gene encoding alsin, a protein with three guanine-nucleotide exchange factor domains, is mutated in a form of recessive amyotrophic lateral sclerosis
-
Yang Y., Hentati A., Deng H., Dabbagh O., Sasaki T., Hirano M., et al. The gene encoding alsin, a protein with three guanine-nucleotide exchange factor domains, is mutated in a form of recessive amyotrophic lateral sclerosis. Nat Genet 29 (2001) 160-165
-
(2001)
Nat Genet
, vol.29
, pp. 160-165
-
-
Yang, Y.1
Hentati, A.2
Deng, H.3
Dabbagh, O.4
Sasaki, T.5
Hirano, M.6
-
22
-
-
0034785483
-
A gene encoding a putative GTPase regulator is mutated in familial amyotrophic lateral sclerosis 2
-
Hadano S., Hand C., Osuga H., Yanagisawa Y., Otomo A., Devon R., et al. A gene encoding a putative GTPase regulator is mutated in familial amyotrophic lateral sclerosis 2. Nat Genet 29 (2001) 166-173
-
(2001)
Nat Genet
, vol.29
, pp. 166-173
-
-
Hadano, S.1
Hand, C.2
Osuga, H.3
Yanagisawa, Y.4
Otomo, A.5
Devon, R.6
-
23
-
-
0037382240
-
Mutant dynactin in motor neuron disease
-
Puls I., Jonnakuty C., LaMonte B., Holzbaur E., Tokito M., Mann E., et al. Mutant dynactin in motor neuron disease. Nat Genet 33 (2003) 455-456
-
(2003)
Nat Genet
, vol.33
, pp. 455-456
-
-
Puls, I.1
Jonnakuty, C.2
LaMonte, B.3
Holzbaur, E.4
Tokito, M.5
Mann, E.6
-
24
-
-
0035369084
-
Charcot-Marie-Tooth disease type 2A caused by mutation in a microtubule motor KIF1Bβ
-
Zhao C., Takita J., Tanaka Y., Setou M., Nakagawa T., Takeda S., et al. Charcot-Marie-Tooth disease type 2A caused by mutation in a microtubule motor KIF1Bβ. Cell 105 (2001) 587-597
-
(2001)
Cell
, vol.105
, pp. 587-597
-
-
Zhao, C.1
Takita, J.2
Tanaka, Y.3
Setou, M.4
Nakagawa, T.5
Takeda, S.6
-
25
-
-
0007731688
-
X-linked dominant locus for late-onset familial amyotrophic lateral sclerosis
-
Siddique T., Hong S., Brooks B., Hung W., Siddique N., Rimmler J., et al. X-linked dominant locus for late-onset familial amyotrophic lateral sclerosis. Am J Hum Genet (1998) A308
-
(1998)
Am J Hum Genet
-
-
Siddique, T.1
Hong, S.2
Brooks, B.3
Hung, W.4
Siddique, N.5
Rimmler, J.6
-
26
-
-
18244393223
-
A novel locus for familial amyotrophic lateral sclerosis on chromosome 18q
-
Hand C., Khoris J., and Salachas T. A novel locus for familial amyotrophic lateral sclerosis on chromosome 18q. Am J Hum Genet 70 (2002) 251-256
-
(2002)
Am J Hum Genet
, vol.70
, pp. 251-256
-
-
Hand, C.1
Khoris, J.2
Salachas, T.3
-
27
-
-
0031959591
-
Linkage of the gene for an autosomal dominant form of juvenile amyotrophic lateral sclerosis to chromosome 9q34
-
Chance P., Rabin B., Ryan S., Ding Y., Scavina M., Crain B., et al. Linkage of the gene for an autosomal dominant form of juvenile amyotrophic lateral sclerosis to chromosome 9q34. Am J Hum Genet 62 (1998) 633-640
-
(1998)
Am J Hum Genet
, vol.62
, pp. 633-640
-
-
Chance, P.1
Rabin, B.2
Ryan, S.3
Ding, Y.4
Scavina, M.5
Crain, B.6
-
28
-
-
0022652901
-
Quantitative motor assessment in amyotrophic lateral sclerosis
-
Andres P., Hedlund W., Finison L., Conlon T., Felmus M., and Munsat T. Quantitative motor assessment in amyotrophic lateral sclerosis. Neurology 36 (1986) 937-941
-
(1986)
Neurology
, vol.36
, pp. 937-941
-
-
Andres, P.1
Hedlund, W.2
Finison, L.3
Conlon, T.4
Felmus, M.5
Munsat, T.6
-
29
-
-
0023116564
-
Quantitative assessment of neuromuscular deficit in ALS
-
Andres P., Thibodeau L., Finison L., and Munsat T. Quantitative assessment of neuromuscular deficit in ALS. Neurol Clin 5 (1987) 125-141
-
(1987)
Neurol Clin
, vol.5
, pp. 125-141
-
-
Andres, P.1
Thibodeau, L.2
Finison, L.3
Munsat, T.4
-
30
-
-
0023841071
-
The natural history of motorneuron loss in amyotrophic lateral sclerosis
-
Munsat T., Andres P., Finison L., Conlon T., and Thibodeau L. The natural history of motorneuron loss in amyotrophic lateral sclerosis. Neurology 38 (1988) 409-413
-
(1988)
Neurology
, vol.38
, pp. 409-413
-
-
Munsat, T.1
Andres, P.2
Finison, L.3
Conlon, T.4
Thibodeau, L.5
-
31
-
-
9044219848
-
A placebo-controlled trial of recombinant human ciliary neurotrophic (rhCNTF) factor in amyotrophic lateral sclerosis
-
Miller R., Petajan J., Bryan W., Armon C., Barohn R., Goodpasture J., et al. A placebo-controlled trial of recombinant human ciliary neurotrophic (rhCNTF) factor in amyotrophic lateral sclerosis. Ann Neurol 39 (1996) 256-260
-
(1996)
Ann Neurol
, vol.39
, pp. 256-260
-
-
Miller, R.1
Petajan, J.2
Bryan, W.3
Armon, C.4
Barohn, R.5
Goodpasture, J.6
-
32
-
-
10544254257
-
Placebo-controlled trial of gabapentin in patients with amyotrophic lateral sclerosis
-
Miller R., Moore D., Young L., and Western ALS Study Group. Placebo-controlled trial of gabapentin in patients with amyotrophic lateral sclerosis. Neurology 47 (1996) 1383-1388
-
(1996)
Neurology
, vol.47
, pp. 1383-1388
-
-
Miller, R.1
Moore, D.2
Young, L.3
Western ALS Study Group4
-
33
-
-
10744222650
-
A randomized, placebo-controlled trial of topiramate in amyotrophic lateral sclerosis
-
Cudkowicz M., Shefner J., Schoenfeld D., Brown R., Johnson H., Qureshi M., et al. A randomized, placebo-controlled trial of topiramate in amyotrophic lateral sclerosis. Neurology 61 (2003) 456-464
-
(2003)
Neurology
, vol.61
, pp. 456-464
-
-
Cudkowicz, M.1
Shefner, J.2
Schoenfeld, D.3
Brown, R.4
Johnson, H.5
Qureshi, M.6
-
34
-
-
0035836649
-
Phase III randomized trial of gabapentin in patients with amyotrophic lateral sclerosis
-
Miller R., Moore D., Gelinas D., Dronsky B., Mendoza M., Barohn R., et al. Phase III randomized trial of gabapentin in patients with amyotrophic lateral sclerosis. Neurology 56 (2001) 843-848
-
(2001)
Neurology
, vol.56
, pp. 843-848
-
-
Miller, R.1
Moore, D.2
Gelinas, D.3
Dronsky, B.4
Mendoza, M.5
Barohn, R.6
-
35
-
-
0031005199
-
Reliability of maximal voluntary isometric contraction testing in a multicenter study of patients with keamyotrophic lateral sclerosis. Syntex/Synergen Neuroscience Joint Venture rhCNTF ALS Study Group
-
Hoagland R., Mendoza M., Armon C., Barohn R., Bryan W., Goodpasture J., et al. Reliability of maximal voluntary isometric contraction testing in a multicenter study of patients with keamyotrophic lateral sclerosis. Syntex/Synergen Neuroscience Joint Venture rhCNTF ALS Study Group. Muscle Nerve 20 (1997) 691-695
-
(1997)
Muscle Nerve
, vol.20
, pp. 691-695
-
-
Hoagland, R.1
Mendoza, M.2
Armon, C.3
Barohn, R.4
Bryan, W.5
Goodpasture, J.6
-
36
-
-
0022652901
-
Quantitative motor assessment in amyotrophic lateral sclerosis
-
Andres P., Hedlund W., Finison L., Conlon T., Felmus M., and Munsat T. Quantitative motor assessment in amyotrophic lateral sclerosis. Neurology 36 (1986) 937-941
-
(1986)
Neurology
, vol.36
, pp. 937-941
-
-
Andres, P.1
Hedlund, W.2
Finison, L.3
Conlon, T.4
Felmus, M.5
Munsat, T.6
-
37
-
-
2442646665
-
A double-blind placebo-controlled clinical trial of subcutaneous recombinant human ciliary neurotrophic factor (rhCNTF) in amyotrophic lateral sclerosis
-
ALS CNTF Treatment Study Group. A double-blind placebo-controlled clinical trial of subcutaneous recombinant human ciliary neurotrophic factor (rhCNTF) in amyotrophic lateral sclerosis. Neurology 46 (1996) 1244-1249
-
(1996)
Neurology
, vol.46
, pp. 1244-1249
-
-
ALS CNTF Treatment Study Group1
-
38
-
-
0027316166
-
Recombinant growth hormone treatment of amyotrophic lateral sclerosis
-
Smith R., Melmed S., Sherman B., Fane J., Munsat T., and Festoff B. Recombinant growth hormone treatment of amyotrophic lateral sclerosis. Muscle Nerve 16 (1993) 624-633
-
(1993)
Muscle Nerve
, vol.16
, pp. 624-633
-
-
Smith, R.1
Melmed, S.2
Sherman, B.3
Fane, J.4
Munsat, T.5
Festoff, B.6
-
40
-
-
0028007449
-
Distal lower motor neuron syndrome with high-titer serum IgM anti-GM1 antibodies: improvement following immunotherapy with monthly plasma exchange and intravenous cyclophosphamide
-
Pestronk A., Lopate G., Kornberg A., Elliott J., Blume G., Yee W., et al. Distal lower motor neuron syndrome with high-titer serum IgM anti-GM1 antibodies: improvement following immunotherapy with monthly plasma exchange and intravenous cyclophosphamide. Neurology 44 (1994) 2027-2031
-
(1994)
Neurology
, vol.44
, pp. 2027-2031
-
-
Pestronk, A.1
Lopate, G.2
Kornberg, A.3
Elliott, J.4
Blume, G.5
Yee, W.6
-
41
-
-
0037432120
-
Creatine monohydrate in DM2/PROMM: a double-blind placebo-controlled clinical study. Proximal myotonic myopathy
-
Schneider-Gold C., Beck M., Wessig C., George A., Kele H., Reiners K., et al. Creatine monohydrate in DM2/PROMM: a double-blind placebo-controlled clinical study. Proximal myotonic myopathy. Neurology 60 (2003) 500-502
-
(2003)
Neurology
, vol.60
, pp. 500-502
-
-
Schneider-Gold, C.1
Beck, M.2
Wessig, C.3
George, A.4
Kele, H.5
Reiners, K.6
-
42
-
-
0028121750
-
Trial of immunosuppression in amyotrophic lateral sclerosis using total lymphoid irradiation
-
Drachman D., Chaudhry V., Cornblath D., Kuncl R., Pestronk A., Clawson L., et al. Trial of immunosuppression in amyotrophic lateral sclerosis using total lymphoid irradiation. Ann Neurol 35 (1994) 142-150
-
(1994)
Ann Neurol
, vol.35
, pp. 142-150
-
-
Drachman, D.1
Chaudhry, V.2
Cornblath, D.3
Kuncl, R.4
Pestronk, A.5
Clawson, L.6
-
43
-
-
0032841891
-
Comparison of maximal voluntary isometric contraction and Drachman's hand-held dynamometry in evaluating patients with amyotrophic lateral sclerosis
-
Beck M., Giess R., Wurffel W., et al. Comparison of maximal voluntary isometric contraction and Drachman's hand-held dynamometry in evaluating patients with amyotrophic lateral sclerosis. Muscle Nerve 22 (1999) 1265-1270
-
(1999)
Muscle Nerve
, vol.22
, pp. 1265-1270
-
-
Beck, M.1
Giess, R.2
Wurffel, W.3
-
44
-
-
0345043998
-
A comparison of muscle strength testing techniques in amyotrophic lateral sclerosis
-
Great Lakes ALS Study Group. A comparison of muscle strength testing techniques in amyotrophic lateral sclerosis. Neurology 61 (2003) 1503-1506
-
(2003)
Neurology
, vol.61
, pp. 1503-1506
-
-
Great Lakes ALS Study Group1
-
45
-
-
0017696693
-
Assessment of muscle strength in Duchenne muscular dystrophy
-
Ziter F., Allsop K., and Tyler F. Assessment of muscle strength in Duchenne muscular dystrophy. Neurology 27 (1977) 981-984
-
(1977)
Neurology
, vol.27
, pp. 981-984
-
-
Ziter, F.1
Allsop, K.2
Tyler, F.3
-
46
-
-
0021366563
-
Clinical trials in Duchenne dystrophy. Standardization and reliability of evaluation procedures
-
Florence J., Pandya S., King W., Robison J., Signore L., Wentzell M., et al. Clinical trials in Duchenne dystrophy. Standardization and reliability of evaluation procedures. Phys Ther 64 (1984) 41-45
-
(1984)
Phys Ther
, vol.64
, pp. 41-45
-
-
Florence, J.1
Pandya, S.2
King, W.3
Robison, J.4
Signore, L.5
Wentzell, M.6
-
47
-
-
0002272061
-
Design of clinical therapeutic trials in amyotrophic lateral
-
Rowland L. (Ed), Raven, New York
-
Brooks B., Sufit R., DePaul R., Tan Y., Sanjak M., and Robbins J. Design of clinical therapeutic trials in amyotrophic lateral. In: Rowland L. (Ed). Amyotrophic lateral sclerosis and other motor neuron disease (1991), Raven, New York
-
(1991)
Amyotrophic lateral sclerosis and other motor neuron disease
-
-
Brooks, B.1
Sufit, R.2
DePaul, R.3
Tan, Y.4
Sanjak, M.5
Robbins, J.6
-
48
-
-
0034784364
-
Respiratory muscle strength and ventilatory failure in amyotrophic lateral sclerosis
-
Lyall R., Polkey M., Leigh P., and Moxham J. Respiratory muscle strength and ventilatory failure in amyotrophic lateral sclerosis. Brain 124 (2001) 2000-2013
-
(2001)
Brain
, vol.124
, pp. 2000-2013
-
-
Lyall, R.1
Polkey, M.2
Leigh, P.3
Moxham, J.4
-
49
-
-
0035943097
-
Postural change of forced vital capacity predicts some respiratory symptoms in ALS
-
Varrato J., Siderowf A., Damiano P., Gregory S., Feinberg D., and McCluskey L. Postural change of forced vital capacity predicts some respiratory symptoms in ALS. Neurology 57 (2001) 357-359
-
(2001)
Neurology
, vol.57
, pp. 357-359
-
-
Varrato, J.1
Siderowf, A.2
Damiano, P.3
Gregory, S.4
Feinberg, D.5
McCluskey, L.6
-
50
-
-
0036234975
-
Disease progression in amyotrophic lateral sclerosis: predictors of survival
-
Magnus T., Beck M., Giess R., Puls I., Naumann M., and Toyka K. Disease progression in amyotrophic lateral sclerosis: predictors of survival. Muscle Nerve 25 (2002) 709-714
-
(2002)
Muscle Nerve
, vol.25
, pp. 709-714
-
-
Magnus, T.1
Beck, M.2
Giess, R.3
Puls, I.4
Naumann, M.5
Toyka, K.6
-
51
-
-
0014514097
-
Maximal respiratory pressures: normal values and relationship to age and sex
-
Black L., and Hyatt R. Maximal respiratory pressures: normal values and relationship to age and sex. Am Rev Respir Dis 99 (1969) 696-702
-
(1969)
Am Rev Respir Dis
, vol.99
, pp. 696-702
-
-
Black, L.1
Hyatt, R.2
-
52
-
-
0023195073
-
A rating scale for amyotrophic lateral sclerosis: description and preliminary experience
-
Appel V., Stewart S., Smith G., and Appel S. A rating scale for amyotrophic lateral sclerosis: description and preliminary experience. Ann Neurol 22 (1987) 328-333
-
(1987)
Ann Neurol
, vol.22
, pp. 328-333
-
-
Appel, V.1
Stewart, S.2
Smith, G.3
Appel, S.4
-
53
-
-
0029037348
-
Natural history of amyotrophic lateral sclerosis in a database population. Validation of a scoring system and a model for survival prediction
-
Haverkamp L., Appel V., and Appel S. Natural history of amyotrophic lateral sclerosis in a database population. Validation of a scoring system and a model for survival prediction. Brain 118 (1995) 707-719
-
(1995)
Brain
, vol.118
, pp. 707-719
-
-
Haverkamp, L.1
Appel, V.2
Appel, S.3
-
55
-
-
0001163277
-
The amyotrophic lateral sclerosis functional rating scale (ALSFRS)
-
Cedarbaum J. The amyotrophic lateral sclerosis functional rating scale (ALSFRS). Arch Neurol 53 (1996) 141-147
-
(1996)
Arch Neurol
, vol.53
, pp. 141-147
-
-
Cedarbaum, J.1
-
56
-
-
0032692481
-
The ALSFRS-R: a revised ALS functional rating scale that incorporates assessments of respiratory function. BDNF ALS Study Group (Phase III)
-
Cedarbaum J., Stambler N., Malta E., Fuller C., Hilt D., Thurmond B., et al. The ALSFRS-R: a revised ALS functional rating scale that incorporates assessments of respiratory function. BDNF ALS Study Group (Phase III). J Neurol Sci 169 (1999) 13-21
-
(1999)
J Neurol Sci
, vol.169
, pp. 13-21
-
-
Cedarbaum, J.1
Stambler, N.2
Malta, E.3
Fuller, C.4
Hilt, D.5
Thurmond, B.6
-
58
-
-
0006512680
-
Sur la paralysie musculaire progressive atrophique
-
Cruveilhier J. Sur la paralysie musculaire progressive atrophique. Arch Gen Med 91 (1853) 561-603
-
(1853)
Arch Gen Med
, vol.91
, pp. 561-603
-
-
Cruveilhier, J.1
-
59
-
-
0000280462
-
Deux cas d'atrophie musculaire progressive ave lesions de la substance grise et des faisceaux anterolateraux de la moelle epineire
-
Charcot J., and Joffroy A. Deux cas d'atrophie musculaire progressive ave lesions de la substance grise et des faisceaux anterolateraux de la moelle epineire. Arch Physiol 2 (1869) 354-367
-
(1869)
Arch Physiol
, vol.2
, pp. 354-367
-
-
Charcot, J.1
Joffroy, A.2
-
60
-
-
0037251889
-
Neuropathology with clinical correlations of sporadic amyotrophic lateral sclerosis: 102 autopsy cases examined between 1962 and 2000
-
Piao Y., Wakabayashi K., Kakita A., Yamada M., Hayashi S., Morita T., et al. Neuropathology with clinical correlations of sporadic amyotrophic lateral sclerosis: 102 autopsy cases examined between 1962 and 2000. Brain Pathol 13 (2003) 10-22
-
(2003)
Brain Pathol
, vol.13
, pp. 10-22
-
-
Piao, Y.1
Wakabayashi, K.2
Kakita, A.3
Yamada, M.4
Hayashi, S.5
Morita, T.6
-
61
-
-
0035666703
-
Ultrastructural study of Betz cells in the primary motor cortex of the human brain
-
Sasaki S., and Iwata M. Ultrastructural study of Betz cells in the primary motor cortex of the human brain. J Anat 199 (2001) 699-708
-
(2001)
J Anat
, vol.199
, pp. 699-708
-
-
Sasaki, S.1
Iwata, M.2
-
62
-
-
0036940998
-
Constant involvement of the Betz cells and pyramidal tract in amyotrophic lateral sclerosis with dementia: a clinicopathological study of eight autopsy cases
-
Tsuchiya K., Ikeda K., Mimura M., Takahashi M., Miyazaki H., Anno M., et al. Constant involvement of the Betz cells and pyramidal tract in amyotrophic lateral sclerosis with dementia: a clinicopathological study of eight autopsy cases. Acta Neuropathol (Berl) 104 (2002) 249-259
-
(2002)
Acta Neuropathol (Berl)
, vol.104
, pp. 249-259
-
-
Tsuchiya, K.1
Ikeda, K.2
Mimura, M.3
Takahashi, M.4
Miyazaki, H.5
Anno, M.6
-
63
-
-
0036941560
-
The relationship between Bunina bodies, skein-like inclusions and neuronal loss in amyotrophic lateral sclerosis
-
van Welsem M., Hogenhuis J., Meininger V., Metsaars W., Hauw J., and Seilhean D. The relationship between Bunina bodies, skein-like inclusions and neuronal loss in amyotrophic lateral sclerosis. Acta Neuropathol (Berl) 103 (2002) 583-589
-
(2002)
Acta Neuropathol (Berl)
, vol.103
, pp. 583-589
-
-
van Welsem, M.1
Hogenhuis, J.2
Meininger, V.3
Metsaars, W.4
Hauw, J.5
Seilhean, D.6
-
64
-
-
0038137137
-
Reduction of the size of the Golgi apparatus of spinal anterior horn cells in patients with X-linked spinal and bulbar muscular atrophy
-
Yaguchi M., Hashizume Y., Yoshida M., Gonatas N., and Okamoto K. Reduction of the size of the Golgi apparatus of spinal anterior horn cells in patients with X-linked spinal and bulbar muscular atrophy. Amyotroph Lateral Scler Other Motor Neuron Disord 4 (2003) 17-21
-
(2003)
Amyotroph Lateral Scler Other Motor Neuron Disord
, vol.4
, pp. 17-21
-
-
Yaguchi, M.1
Hashizume, Y.2
Yoshida, M.3
Gonatas, N.4
Okamoto, K.5
-
65
-
-
0036943001
-
The Golgi apparatus is fragmented in spinal cord motor neurons of amyotrophic lateral sclerosis with basophilic inclusions
-
Fujita Y., Okamoto K., Sakurai A., Kusaka H., Aizawa H., Mihara B., et al. The Golgi apparatus is fragmented in spinal cord motor neurons of amyotrophic lateral sclerosis with basophilic inclusions. Acta Neuropathol (Berl) 103 (2002) 243-247
-
(2002)
Acta Neuropathol (Berl)
, vol.103
, pp. 243-247
-
-
Fujita, Y.1
Okamoto, K.2
Sakurai, A.3
Kusaka, H.4
Aizawa, H.5
Mihara, B.6
-
67
-
-
0018341399
-
Morphometric quantification of the cervical limb motor cells in controls and in amyotrophic lateral sclerosis
-
Tsukagoshi H., Yanagisawa N., Oguchi K., Nagashima K., and Murakami T. Morphometric quantification of the cervical limb motor cells in controls and in amyotrophic lateral sclerosis. J Neurol Sci 41 (1979) 287-297
-
(1979)
J Neurol Sci
, vol.41
, pp. 287-297
-
-
Tsukagoshi, H.1
Yanagisawa, N.2
Oguchi, K.3
Nagashima, K.4
Murakami, T.5
-
68
-
-
0034980087
-
Motor unit number estimation in human neurological diseases and animal models
-
Shefner J. Motor unit number estimation in human neurological diseases and animal models. Clin Neurophysiol 112 (2001) 955-964
-
(2001)
Clin Neurophysiol
, vol.112
, pp. 955-964
-
-
Shefner, J.1
-
69
-
-
0036372761
-
Motor unit number estimation in neurologic disease
-
Shefner J., and Gooch C. Motor unit number estimation in neurologic disease. Adv Neurol 88 (2002) 33-52
-
(2002)
Adv Neurol
, vol.88
, pp. 33-52
-
-
Shefner, J.1
Gooch, C.2
-
70
-
-
0027361165
-
Motor unit number estimation, isometric strength, and electromyographic measures in amyotrophic lateral sclerosis
-
Bromberg M., Forshew D., Nau K., Bromberg J., Simmons Z., and Fries T. Motor unit number estimation, isometric strength, and electromyographic measures in amyotrophic lateral sclerosis. Muscle Nerve 16 (1993) 1213-1219
-
(1993)
Muscle Nerve
, vol.16
, pp. 1213-1219
-
-
Bromberg, M.1
Forshew, D.2
Nau, K.3
Bromberg, J.4
Simmons, Z.5
Fries, T.6
-
72
-
-
0029787778
-
Relationships between motor-unit number estimates and isometric strength in distal muscles in ALS/MND
-
Bromberg M., and Larson W. Relationships between motor-unit number estimates and isometric strength in distal muscles in ALS/MND. J Neurol Sci 139 Suppl (1996) 38-42
-
(1996)
J Neurol Sci
, vol.139
, Issue.SUPPL
, pp. 38-42
-
-
Bromberg, M.1
Larson, W.2
-
73
-
-
0029091823
-
Sources of error in the spike-triggered averaging method of motor unit number estimation (MUNE)
-
Bromberg M., and Abrams J. Sources of error in the spike-triggered averaging method of motor unit number estimation (MUNE). Muscle Nerve 18 (1995) 1139-1146
-
(1995)
Muscle Nerve
, vol.18
, pp. 1139-1146
-
-
Bromberg, M.1
Abrams, J.2
-
74
-
-
0027426148
-
Determinants of mean motor unit size: impact on estimates of motor unit number
-
Doherty T., Stashuk D., and Brown W. Determinants of mean motor unit size: impact on estimates of motor unit number. Muscle Nerve 16 (1993) 1326-1331
-
(1993)
Muscle Nerve
, vol.16
, pp. 1326-1331
-
-
Doherty, T.1
Stashuk, D.2
Brown, W.3
-
75
-
-
0033818818
-
Comparison of multiple point and statistical motor unit number estimation
-
Lomen-Hoerth C., and Olney R. Comparison of multiple point and statistical motor unit number estimation. Muscle Nerve 23 (2000) 1525-1533
-
(2000)
Muscle Nerve
, vol.23
, pp. 1525-1533
-
-
Lomen-Hoerth, C.1
Olney, R.2
-
76
-
-
0032709241
-
Motor unit number estimate-based rates of progression of ALS predict patient survival
-
Armon C., and Brandstater M. Motor unit number estimate-based rates of progression of ALS predict patient survival. Muscle Nerve 22 (1999) 1571-1575
-
(1999)
Muscle Nerve
, vol.22
, pp. 1571-1575
-
-
Armon, C.1
Brandstater, M.2
-
77
-
-
0031038871
-
A longitudinal study comparing thenar motor unit number estimates to other quantitative tests in patients with amyotrophic lateral sclerosis
-
Felice K. A longitudinal study comparing thenar motor unit number estimates to other quantitative tests in patients with amyotrophic lateral sclerosis. Muscle Nerve 20 (1997) 179-185
-
(1997)
Muscle Nerve
, vol.20
, pp. 179-185
-
-
Felice, K.1
-
78
-
-
0030864155
-
Longitudinal study of fiber density and motor unit number estimate in patients with amyotrophic lateral sclerosis
-
Yuen E., and Olney R. Longitudinal study of fiber density and motor unit number estimate in patients with amyotrophic lateral sclerosis. Neurology 49 (1997) 573-578
-
(1997)
Neurology
, vol.49
, pp. 573-578
-
-
Yuen, E.1
Olney, R.2
-
79
-
-
0028857121
-
Estimating the number of motor units in a muscle
-
Daube J. Estimating the number of motor units in a muscle. J Clin Neurophysiol 12 (1995) 585-594
-
(1995)
J Clin Neurophysiol
, vol.12
, pp. 585-594
-
-
Daube, J.1
-
80
-
-
0015045633
-
Electrophysiological estimation of the number of motor units within a human muscle
-
McComas A., Fawcett P., Campbell M., and Sica R. Electrophysiological estimation of the number of motor units within a human muscle. J Neurol Neurosurg Psychiatry 34 (1971) 121-131
-
(1971)
J Neurol Neurosurg Psychiatry
, vol.34
, pp. 121-131
-
-
McComas, A.1
Fawcett, P.2
Campbell, M.3
Sica, R.4
-
81
-
-
0027522111
-
Motor unit populations in healthy and diseased muscles
-
McComas A., Galea V., and de Bruin H. Motor unit populations in healthy and diseased muscles. Phys Ther 73 (1993) 868-877
-
(1993)
Phys Ther
, vol.73
, pp. 868-877
-
-
McComas, A.1
Galea, V.2
de Bruin, H.3
-
82
-
-
0030796561
-
Early and late losses of motor units after poliomyelitis
-
McComas A., Quartly C., and Griggs R. Early and late losses of motor units after poliomyelitis. Brain 120 (1997) 1415-1421
-
(1997)
Brain
, vol.120
, pp. 1415-1421
-
-
McComas, A.1
Quartly, C.2
Griggs, R.3
-
83
-
-
0015449206
-
A method for estimating the number of motor units in thenar muscles and the changes in motor unit count with ageing
-
Brown W. A method for estimating the number of motor units in thenar muscles and the changes in motor unit count with ageing. J Neurol Neurosurg Psychiatry 35 (1972) 845-852
-
(1972)
J Neurol Neurosurg Psychiatry
, vol.35
, pp. 845-852
-
-
Brown, W.1
-
84
-
-
0015828278
-
Thenar motor unit count estimates in the carpal tunnel syndrome
-
Brown W. Thenar motor unit count estimates in the carpal tunnel syndrome. J Neurol Neurosurg Psychiatry 36 (1973) 194-198
-
(1973)
J Neurol Neurosurg Psychiatry
, vol.36
, pp. 194-198
-
-
Brown, W.1
-
85
-
-
0033969253
-
Statistical motor unit number estimation: reproducibility and sources of error in patients with amyotrophic lateral sclerosis
-
Olney R., Yuen E., and Engstrom J. Statistical motor unit number estimation: reproducibility and sources of error in patients with amyotrophic lateral sclerosis. Muscle Nerve 23 (2000) 193-197
-
(2000)
Muscle Nerve
, vol.23
, pp. 193-197
-
-
Olney, R.1
Yuen, E.2
Engstrom, J.3
-
86
-
-
0032882343
-
Reducing intersubject variability in motor unit number estimation
-
Shefner J., Jillapalli D., and Bradshaw D. Reducing intersubject variability in motor unit number estimation. Muscle Nerve 22 (1999) 1457-1460
-
(1999)
Muscle Nerve
, vol.22
, pp. 1457-1460
-
-
Shefner, J.1
Jillapalli, D.2
Bradshaw, D.3
-
87
-
-
0017844051
-
A quantitative electrophysiological study of motor neurone disease
-
Hansen S., and Ballantyne J. A quantitative electrophysiological study of motor neurone disease. J Neurol Neurosurg Psychiatry 41 (1978) 773-783
-
(1978)
J Neurol Neurosurg Psychiatry
, vol.41
, pp. 773-783
-
-
Hansen, S.1
Ballantyne, J.2
-
88
-
-
0018409512
-
Changes in motor unit populations in motor neurone disease
-
Carleton S., and Brown W. Changes in motor unit populations in motor neurone disease. J Neurol Neurosurg Psychiatry 42 (1979) 42-51
-
(1979)
J Neurol Neurosurg Psychiatry
, vol.42
, pp. 42-51
-
-
Carleton, S.1
Brown, W.2
-
89
-
-
0026342465
-
The extent and time course of motoneuron involvement in amyotrophic lateral sclerosis
-
Dantes M., and McComas A. The extent and time course of motoneuron involvement in amyotrophic lateral sclerosis. Muscle Nerve 7 (1991) 416-421
-
(1991)
Muscle Nerve
, vol.7
, pp. 416-421
-
-
Dantes, M.1
McComas, A.2
-
90
-
-
0031753142
-
A loss of functional spinal alpha motor neurons in amyotrophic lateral sclerosis
-
Arasaki K., and Tamaki M. A loss of functional spinal alpha motor neurons in amyotrophic lateral sclerosis. Neurology 51 (1998) 603-605
-
(1998)
Neurology
, vol.51
, pp. 603-605
-
-
Arasaki, K.1
Tamaki, M.2
-
91
-
-
0023116564
-
Quantitative assessment of neuromuscular deficit in ALS
-
Andres P., Thibodeau L., Finison L., and Munsat T. Quantitative assessment of neuromuscular deficit in ALS. Neurol Clin 5 (1987) 125-141
-
(1987)
Neurol Clin
, vol.5
, pp. 125-141
-
-
Andres, P.1
Thibodeau, L.2
Finison, L.3
Munsat, T.4
-
92
-
-
0023860093
-
Use of composite scores (megascores) to measure deficit in amyotrophic lateral sclerosis
-
Andres P., Finison L., Conlon T., Thibodeau L., and Munsat T. Use of composite scores (megascores) to measure deficit in amyotrophic lateral sclerosis. Neurology 38 (1988) 405-408
-
(1988)
Neurology
, vol.38
, pp. 405-408
-
-
Andres, P.1
Finison, L.2
Conlon, T.3
Thibodeau, L.4
Munsat, T.5
-
93
-
-
0000977540
-
The rate of change in motor unit number estimates predicts survival in patients with amyotrophic lateral sclerosis
-
Olney R., Yuen E., and Engstrom J. The rate of change in motor unit number estimates predicts survival in patients with amyotrophic lateral sclerosis. Neurology 52 Suppl 2 (1999) A3
-
(1999)
Neurology
, vol.52
, Issue.SUPPL. 2
-
-
Olney, R.1
Yuen, E.2
Engstrom, J.3
-
94
-
-
0031753445
-
Linear estimates of rates of disease progression as predictors of survival in patients with ALS entering clinical trials
-
Armon C., and Moses D. Linear estimates of rates of disease progression as predictors of survival in patients with ALS entering clinical trials. J Neurol Sci 160 Suppl 1 (1998) S37-S41
-
(1998)
J Neurol Sci
, vol.160
, Issue.SUPPL. 1
-
-
Armon, C.1
Moses, D.2
-
95
-
-
0034094573
-
Linear estimates of disease progression predict survival in patients with amyotrophic lateral sclerosis
-
Armon C., Graves M., Moses D., Forte D., Sepulveda L., Darby S., et al. Linear estimates of disease progression predict survival in patients with amyotrophic lateral sclerosis. Muscle Nerve 23 (2000) 874-882
-
(2000)
Muscle Nerve
, vol.23
, pp. 874-882
-
-
Armon, C.1
Graves, M.2
Moses, D.3
Forte, D.4
Sepulveda, L.5
Darby, S.6
-
96
-
-
34247167561
-
-
Shefner JM. Motor unit number estimation in a multicenter clinical trial. Paper presented at the 14th international symposium on ALS/MND, Milan, Italy, November, 2003.
-
-
-
-
97
-
-
0035217574
-
Clinical neurophysiology of ALS
-
Eisen A., and Swash M. Clinical neurophysiology of ALS. Clin Neurophysiol 112 (2001) 2190-2201
-
(2001)
Clin Neurophysiol
, vol.112
, pp. 2190-2201
-
-
Eisen, A.1
Swash, M.2
-
98
-
-
0034797639
-
Sensitivity of transcranial magnetic stimulation of cortico-bulbar vs. cortico-spinal tract involvement in amyotrophic lateral sclerosis (ALS)
-
Urban P., Wicht S., and Hopf H. Sensitivity of transcranial magnetic stimulation of cortico-bulbar vs. cortico-spinal tract involvement in amyotrophic lateral sclerosis (ALS). J Neurol 248 (2001) 850-855
-
(2001)
J Neurol
, vol.248
, pp. 850-855
-
-
Urban, P.1
Wicht, S.2
Hopf, H.3
-
99
-
-
0023577649
-
Magnetic brain stimulation: central motor conduction studies in multiple sclerosis
-
Hess C., Mills K., Murray N., and Schriefer T. Magnetic brain stimulation: central motor conduction studies in multiple sclerosis. Ann Neurol 22 (1987) 744-752
-
(1987)
Ann Neurol
, vol.22
, pp. 744-752
-
-
Hess, C.1
Mills, K.2
Murray, N.3
Schriefer, T.4
-
100
-
-
0030789324
-
Corticomotor threshold is reduced in early sporadic amyotrophic lateral sclerosis
-
Mills K., and Nithi K. Corticomotor threshold is reduced in early sporadic amyotrophic lateral sclerosis. Muscle Nerve 20 (1997) 1137-1141
-
(1997)
Muscle Nerve
, vol.20
, pp. 1137-1141
-
-
Mills, K.1
Nithi, K.2
-
101
-
-
0027446580
-
Cortical excitability in amyotrophic lateral sclerosis: a clue to pathogenesis
-
Eisen A., Pant B., and Stewart H. Cortical excitability in amyotrophic lateral sclerosis: a clue to pathogenesis. Can J Neurol Sci 20 (1993) 11-16
-
(1993)
Can J Neurol Sci
, vol.20
, pp. 11-16
-
-
Eisen, A.1
Pant, B.2
Stewart, H.3
-
102
-
-
0030695278
-
Impaired motor cortex inhibition in patients with amyotrophic lateral sclerosis. Evidence from paired transcranial magnetic stimulation
-
Ziemann U., Winter M., Reimers C., Reimers K., Tergau F., and Paulus W. Impaired motor cortex inhibition in patients with amyotrophic lateral sclerosis. Evidence from paired transcranial magnetic stimulation. Neurology 49 (1997) 1292-1298
-
(1997)
Neurology
, vol.49
, pp. 1292-1298
-
-
Ziemann, U.1
Winter, M.2
Reimers, C.3
Reimers, K.4
Tergau, F.5
Paulus, W.6
-
103
-
-
0033041668
-
Assessment of upper and lower motor neurons in Kennedy's disease: implications for corticomotoneuronal PSTH studies
-
Weber M., and Eisen A. Assessment of upper and lower motor neurons in Kennedy's disease: implications for corticomotoneuronal PSTH studies. Muscle Nerve 22 (1999) 299-306
-
(1999)
Muscle Nerve
, vol.22
, pp. 299-306
-
-
Weber, M.1
Eisen, A.2
-
104
-
-
0345270007
-
Changes in motor cortex inhibition over time in patients with amyotrophic lateral sclerosis
-
Zanette G., Tamburin S., Manganotti P., Refatti N., Forgione A., and Rizzuto N. Changes in motor cortex inhibition over time in patients with amyotrophic lateral sclerosis. J Neurol 249 (2002) 1723-1728
-
(2002)
J Neurol
, vol.249
, pp. 1723-1728
-
-
Zanette, G.1
Tamburin, S.2
Manganotti, P.3
Refatti, N.4
Forgione, A.5
Rizzuto, N.6
-
105
-
-
0035119074
-
Magnetic resonance imaging and 1H-magnetic resonance spectroscopy in amyotrophic lateral sclerosis
-
Sarchielli P., Pelliccioli G., Tarducci R., Chiarini P., Presciutti O., Gobbi G., et al. Magnetic resonance imaging and 1H-magnetic resonance spectroscopy in amyotrophic lateral sclerosis. Neuroradiology 43 (2001) 189-197
-
(2001)
Neuroradiology
, vol.43
, pp. 189-197
-
-
Sarchielli, P.1
Pelliccioli, G.2
Tarducci, R.3
Chiarini, P.4
Presciutti, O.5
Gobbi, G.6
-
106
-
-
0031799685
-
Decreased N-acetylaspartate in motor cortex and corticospinal tract in ALS
-
Rooney W., Miller R., Gelinas D., Schuff N., Maudsley A., and Weiner M. Decreased N-acetylaspartate in motor cortex and corticospinal tract in ALS. Neurology 50 (1998) 1800-1805
-
(1998)
Neurology
, vol.50
, pp. 1800-1805
-
-
Rooney, W.1
Miller, R.2
Gelinas, D.3
Schuff, N.4
Maudsley, A.5
Weiner, M.6
-
108
-
-
0033551415
-
1H-MRS evidence of neurodegeneration and excess glutamate + glutamine in ALS medulla
-
Pioro E., Majors A., Mitsumoto H., Nelson D., and Ng T. 1H-MRS evidence of neurodegeneration and excess glutamate + glutamine in ALS medulla. Neurology 53 (1999) 71-79
-
(1999)
Neurology
, vol.53
, pp. 71-79
-
-
Pioro, E.1
Majors, A.2
Mitsumoto, H.3
Nelson, D.4
Ng, T.5
-
109
-
-
0035015381
-
Proton magnetic resonance spectroscopy of the motor cortex in 70 patients with amyotrophic lateral sclerosis
-
Pohl C., Block W., Karitzky J., Traber F., Schmidt S., Grothe C., et al. Proton magnetic resonance spectroscopy of the motor cortex in 70 patients with amyotrophic lateral sclerosis. Arch Neurol 58 (2001) 729-735
-
(2001)
Arch Neurol
, vol.58
, pp. 729-735
-
-
Pohl, C.1
Block, W.2
Karitzky, J.3
Traber, F.4
Schmidt, S.5
Grothe, C.6
-
110
-
-
0034743262
-
1H spectroscopy in patients with amyotrophic lateral sclerosis
-
Kenn W., Ochs G., Pabst T., and Hahn D. 1H spectroscopy in patients with amyotrophic lateral sclerosis. J Neuroimaging 11 (2001) 293-297
-
(2001)
J Neuroimaging
, vol.11
, pp. 293-297
-
-
Kenn, W.1
Ochs, G.2
Pabst, T.3
Hahn, D.4
-
111
-
-
0035003304
-
Amyotrophic lateral sclerosis: the search for a spectroscopic marker of upper motoneuron involvement
-
Bowen B., and Bradley W. Amyotrophic lateral sclerosis: the search for a spectroscopic marker of upper motoneuron involvement. Arch Neurol 58 (2001) 714-716
-
(2001)
Arch Neurol
, vol.58
, pp. 714-716
-
-
Bowen, B.1
Bradley, W.2
-
112
-
-
0034115380
-
MR imaging and localized proton spectroscopy of the precentral gyrus in amyotrophic lateral sclerosis
-
Bowen B., Pattany P., Bradley W., Murdoch J., Rotta F., Younis A., et al. MR imaging and localized proton spectroscopy of the precentral gyrus in amyotrophic lateral sclerosis. AJNR Am J Neuroradiol 21 (2000) 647-658
-
(2000)
AJNR Am J Neuroradiol
, vol.21
, pp. 647-658
-
-
Bowen, B.1
Pattany, P.2
Bradley, W.3
Murdoch, J.4
Rotta, F.5
Younis, A.6
-
113
-
-
0038147334
-
A prospective, randomized, placebo-controlled evaluation of corticoneuronal response to intrathecal BDNF therapy in ALS using magnetic resonance spectroscopy: feasibility and results
-
Kalra S., Genge A., and Arnold D. A prospective, randomized, placebo-controlled evaluation of corticoneuronal response to intrathecal BDNF therapy in ALS using magnetic resonance spectroscopy: feasibility and results. Amyotroph Lateral Scler Other Motor Neuron Disord 4 (2003) 22-26
-
(2003)
Amyotroph Lateral Scler Other Motor Neuron Disord
, vol.4
, pp. 22-26
-
-
Kalra, S.1
Genge, A.2
Arnold, D.3
-
114
-
-
0345700290
-
Gabapentin therapy for amyotrophic lateral sclerosis: lack of improvement in neuronal integrity shown by MR spectroscopy
-
Kalra S., Cashman N., Caramanos Z., Genge A., and Arnold D. Gabapentin therapy for amyotrophic lateral sclerosis: lack of improvement in neuronal integrity shown by MR spectroscopy. AJNR Am J Neuroradiol 24 (2003) 476-480
-
(2003)
AJNR Am J Neuroradiol
, vol.24
, pp. 476-480
-
-
Kalra, S.1
Cashman, N.2
Caramanos, Z.3
Genge, A.4
Arnold, D.5
-
115
-
-
0035693093
-
Effect of creatine supplementation on metabolite levels in ALS motor cortices
-
Vielhaber S., Kaufmann J., Kanowski M., Sailer M., Feistner H., Tempelmann C., et al. Effect of creatine supplementation on metabolite levels in ALS motor cortices. Exp Neurol 172 (2001) 377-382
-
(2001)
Exp Neurol
, vol.172
, pp. 377-382
-
-
Vielhaber, S.1
Kaufmann, J.2
Kanowski, M.3
Sailer, M.4
Feistner, H.5
Tempelmann, C.6
-
116
-
-
0037379650
-
A randomized sequential trial of creatine in amyotrophic lateral sclerosis
-
Groeneveld G., Veldink J., van der Tweel I., Kalmijn S., Beijer C., de Visser M., et al. A randomized sequential trial of creatine in amyotrophic lateral sclerosis. Ann Neurol 53 (2003) 437-445
-
(2003)
Ann Neurol
, vol.53
, pp. 437-445
-
-
Groeneveld, G.1
Veldink, J.2
van der Tweel, I.3
Kalmijn, S.4
Beijer, C.5
de Visser, M.6
-
117
-
-
0025299819
-
Abnormal excitatory amino acid metabolism in amyotrophic lateral sclerosis
-
Rothstein J., Tsai G., Kuncl R., et al. Abnormal excitatory amino acid metabolism in amyotrophic lateral sclerosis. Ann Neurol 28 (1990) 18-25
-
(1990)
Ann Neurol
, vol.28
, pp. 18-25
-
-
Rothstein, J.1
Tsai, G.2
Kuncl, R.3
-
118
-
-
0027228269
-
Fasting plasma and CSF amino acid levels in amyotrophic lateral sclerosis: a subtype analysis
-
Camu W., Billiard M., and Baldy-Moulinier M. Fasting plasma and CSF amino acid levels in amyotrophic lateral sclerosis: a subtype analysis. Acta Neurol Scand 88 (1993) 51-55
-
(1993)
Acta Neurol Scand
, vol.88
, pp. 51-55
-
-
Camu, W.1
Billiard, M.2
Baldy-Moulinier, M.3
-
119
-
-
0033807443
-
Increased oxidative damage to DNA in ALS patients
-
Bogdanov M., Brown R., Matson W., Hayden D., O'Donnell H., Beal F., et al. Increased oxidative damage to DNA in ALS patients. Free Radical Biology 29 (2000) 652-658
-
(2000)
Free Radical Biology
, vol.29
, pp. 652-658
-
-
Bogdanov, M.1
Brown, R.2
Matson, W.3
Hayden, D.4
O'Donnell, H.5
Beal, F.6
-
120
-
-
0030851761
-
Increased 3-Nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis
-
Beal M., Ferrante R., Browne S., Matthews R., Kowall N., and Brown R. Increased 3-Nitrotyrosine in both sporadic and familial amyotrophic lateral sclerosis. Ann Neurol 42 (1997) 644-654
-
(1997)
Ann Neurol
, vol.42
, pp. 644-654
-
-
Beal, M.1
Ferrante, R.2
Browne, S.3
Matthews, R.4
Kowall, N.5
Brown, R.6
-
121
-
-
0031722955
-
Presence of 4-hydroxynonenal in cerebrospinal fluid of patients with sporadic amyotrophic lateral sclerosis
-
Smith R., Henry Y., Mattson M., and Appel S. Presence of 4-hydroxynonenal in cerebrospinal fluid of patients with sporadic amyotrophic lateral sclerosis. Ann Neurol 44 (1998) 696-699
-
(1998)
Ann Neurol
, vol.44
, pp. 696-699
-
-
Smith, R.1
Henry, Y.2
Mattson, M.3
Appel, S.4
-
122
-
-
20344385712
-
Elevated levels of 4-HNE in the sera of patients with amyotrophic lateral sclerosis
-
Simpson E., Henkel J., Henry Y., Smith R., and Appel S. Elevated levels of 4-HNE in the sera of patients with amyotrophic lateral sclerosis. Neurology 60 (2003) A242
-
(2003)
Neurology
, vol.60
-
-
Simpson, E.1
Henkel, J.2
Henry, Y.3
Smith, R.4
Appel, S.5
-
123
-
-
0034626855
-
Matrix metalloproteinase-9 is elevated in serum of patients with amyotrophic lateral sclerosis
-
Beuche W., Yushchenko M., Mader M., Maliszewska M., Felgenhauer K., and Weber F. Matrix metalloproteinase-9 is elevated in serum of patients with amyotrophic lateral sclerosis. NeuroReport 11 (2000) 3419-3422
-
(2000)
NeuroReport
, vol.11
, pp. 3419-3422
-
-
Beuche, W.1
Yushchenko, M.2
Mader, M.3
Maliszewska, M.4
Felgenhauer, K.5
Weber, F.6
-
124
-
-
0036838167
-
Increased plasma TGF-beta1 in patients with amyotrophic lateral sclerosis
-
Houi K., Kobayashi T., Kato S., Mochio S., and Inoue K. Increased plasma TGF-beta1 in patients with amyotrophic lateral sclerosis. Acta Neurol Scand 106 (2002) 299-301
-
(2002)
Acta Neurol Scand
, vol.106
, pp. 299-301
-
-
Houi, K.1
Kobayashi, T.2
Kato, S.3
Mochio, S.4
Inoue, K.5
-
125
-
-
21344451069
-
Identification of ALS specific biomarkers by protein profiling of cerebral spinal fluid
-
Ranganathan S., Jordan K., Sathanoonri R., Henry S., Wood P., Urbinelli L., et al. Identification of ALS specific biomarkers by protein profiling of cerebral spinal fluid. Amyotroph Lateral Scler Other Motor Neuron Disord 4 (2003) 12
-
(2003)
Amyotroph Lateral Scler Other Motor Neuron Disord
, vol.4
, pp. 12
-
-
Ranganathan, S.1
Jordan, K.2
Sathanoonri, R.3
Henry, S.4
Wood, P.5
Urbinelli, L.6
-
126
-
-
34247137866
-
Metabolic profiling and signatures in ALS
-
Bogdanov M., Rozen S., Kristall B., Matson W., Vigneau-Callahan K., Flarakos J., et al. Metabolic profiling and signatures in ALS. Amyotroph Lateral Scler Other Motor Neuron Disord 3 (2002) 26
-
(2002)
Amyotroph Lateral Scler Other Motor Neuron Disord
, vol.3
, pp. 26
-
-
Bogdanov, M.1
Rozen, S.2
Kristall, B.3
Matson, W.4
Vigneau-Callahan, K.5
Flarakos, J.6
-
127
-
-
0029943383
-
Analysis of chromosome 5q13 genes in amyotrophic lateral sclerosis: homozygous NAIP deletion in a sporadic case
-
Jackson M., Morrison K., al-Chalabi A., Bakker M., and Leigh P. Analysis of chromosome 5q13 genes in amyotrophic lateral sclerosis: homozygous NAIP deletion in a sporadic case. Ann Neurol 39 (1996) 796-800
-
(1996)
Ann Neurol
, vol.39
, pp. 796-800
-
-
Jackson, M.1
Morrison, K.2
al-Chalabi, A.3
Bakker, M.4
Leigh, P.5
-
128
-
-
0033058289
-
Deletions causing spinal muscular atrophy do not predispose to amyotrophic lateral sclerosis
-
Parboosingh J., Meininger V., McKenna-Yasek D., Brown R., and Rouleau G. Deletions causing spinal muscular atrophy do not predispose to amyotrophic lateral sclerosis. Arch Neurol 56 (1999) 710-712
-
(1999)
Arch Neurol
, vol.56
, pp. 710-712
-
-
Parboosingh, J.1
Meininger, V.2
McKenna-Yasek, D.3
Brown, R.4
Rouleau, G.5
-
129
-
-
0031958077
-
Association between centromeric deletions of the SMN gene and sporadic adult-onset lower motor neuron disease
-
Moulard B., Salachas F., and Chassande B. Association between centromeric deletions of the SMN gene and sporadic adult-onset lower motor neuron disease. Ann Neurol 43 (1998) 640-644
-
(1998)
Ann Neurol
, vol.43
, pp. 640-644
-
-
Moulard, B.1
Salachas, F.2
Chassande, B.3
-
130
-
-
0036156999
-
Abnormal SMN1 gene copy number is a susceptibility factor for amyotrophic lateral sclerosis
-
Corcia P., Mayeux-Portas V., and Khoris J. Abnormal SMN1 gene copy number is a susceptibility factor for amyotrophic lateral sclerosis. Ann Neurol 51 (2002) 243-246
-
(2002)
Ann Neurol
, vol.51
, pp. 243-246
-
-
Corcia, P.1
Mayeux-Portas, V.2
Khoris, J.3
-
131
-
-
0028991091
-
Apolipoprotein E E4 allele is not associated with earlier age at onset in amyotrophic lateral sclerosis
-
Mui S., Rebeck G., McKenna-Yasek D., Hyman B., and Brown R. Apolipoprotein E E4 allele is not associated with earlier age at onset in amyotrophic lateral sclerosis. Ann Neurol 38 (1995) 460-463
-
(1995)
Ann Neurol
, vol.38
, pp. 460-463
-
-
Mui, S.1
Rebeck, G.2
McKenna-Yasek, D.3
Hyman, B.4
Brown, R.5
-
132
-
-
0030025431
-
Association of apolipoprotein E E4 allele with bulbar-onset motor neuron disease
-
Al-Chalabi A., Enayat Z., Bakker M., et al. Association of apolipoprotein E E4 allele with bulbar-onset motor neuron disease. Lancet 347 (1996) 159-160
-
(1996)
Lancet
, vol.347
, pp. 159-160
-
-
Al-Chalabi, A.1
Enayat, Z.2
Bakker, M.3
-
133
-
-
0029787386
-
Apolipoprotein E genotyping in sporadic amyotrophic lateral sclerosis: evidence for a major influence on the clinical presentation and prognosis
-
Moulard B., Sefiani A., Laamri A., Malafosse A., and Camu W. Apolipoprotein E genotyping in sporadic amyotrophic lateral sclerosis: evidence for a major influence on the clinical presentation and prognosis. J Neurol Sci 139 Suppl (1996) 34-137
-
(1996)
J Neurol Sci
, vol.139
, Issue.SUPPL
, pp. 34-137
-
-
Moulard, B.1
Sefiani, A.2
Laamri, A.3
Malafosse, A.4
Camu, W.5
-
134
-
-
0029666061
-
Apolipoprotein E E4 in bulbar-onset motor neuron disease
-
Smith R., Haverkamp L., Case S., Appel S., and Appel V. Apolipoprotein E E4 in bulbar-onset motor neuron disease. Lancet 348 (1996) 334-335
-
(1996)
Lancet
, vol.348
, pp. 334-335
-
-
Smith, R.1
Haverkamp, L.2
Case, S.3
Appel, S.4
Appel, V.5
-
135
-
-
0029553701
-
Deficiency of human ciliary neurotrophic factor (CNTF) is not causally related to amyotrophic lateral sclerosis (ALS)
-
Takahashi R. Deficiency of human ciliary neurotrophic factor (CNTF) is not causally related to amyotrophic lateral sclerosis (ALS). Rinsho Shinkeigakku 35 (1995) 1543-1545
-
(1995)
Rinsho Shinkeigakku
, vol.35
, pp. 1543-1545
-
-
Takahashi, R.1
-
136
-
-
0028021552
-
A null mutation in the human CNTF gene is not causally related to neurological diseases
-
Takahashi R., Yokoji H., Misawa H., et al. A null mutation in the human CNTF gene is not causally related to neurological diseases. Nat Genet 7 (1994) 79-84
-
(1994)
Nat Genet
, vol.7
, pp. 79-84
-
-
Takahashi, R.1
Yokoji, H.2
Misawa, H.3
-
137
-
-
0029142863
-
Investigation of a null mutation of the CNTF gene in familial amyotrophic lateral sclerosis
-
Orrell R., King A., Lane R., and de Belleroche J. Investigation of a null mutation of the CNTF gene in familial amyotrophic lateral sclerosis. J Neurol Sci 132 (1995) 126-128
-
(1995)
J Neurol Sci
, vol.132
, pp. 126-128
-
-
Orrell, R.1
King, A.2
Lane, R.3
de Belleroche, J.4
-
138
-
-
0027484249
-
Disruption of the CNTF gene results in motor neuron degeneration
-
Masu Y., Wolf E., Holtmann B., et al. Disruption of the CNTF gene results in motor neuron degeneration. Nature 365 (1993) 27-32
-
(1993)
Nature
, vol.365
, pp. 27-32
-
-
Masu, Y.1
Wolf, E.2
Holtmann, B.3
-
139
-
-
0038799979
-
CNTF genotype does not influence clinical phenotype in amyotrophic lateral sclerosis
-
Al-Chalabi A., Scheffler M., Smith B., Parton M., Cudkowicz M., Andersen P., et al. CNTF genotype does not influence clinical phenotype in amyotrophic lateral sclerosis. Ann Neurol 54 (2003) 130-134
-
(2003)
Ann Neurol
, vol.54
, pp. 130-134
-
-
Al-Chalabi, A.1
Scheffler, M.2
Smith, B.3
Parton, M.4
Cudkowicz, M.5
Andersen, P.6
-
140
-
-
0032032013
-
Aberrant RNA processing in a neurodegenerative disease: the cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis
-
Lin C., Bristol L., Jin L., Dykes-Hoberg M., Crawford T., Clawson L., et al. Aberrant RNA processing in a neurodegenerative disease: the cause for absent EAAT2, a glutamate transporter, in amyotrophic lateral sclerosis. Neuron 20 (1998) 589-602
-
(1998)
Neuron
, vol.20
, pp. 589-602
-
-
Lin, C.1
Bristol, L.2
Jin, L.3
Dykes-Hoberg, M.4
Crawford, T.5
Clawson, L.6
-
141
-
-
0033366461
-
SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter
-
Trotti D., Rolfs A., Danbolt N., Brown R., and Hediger M. SOD1 mutants linked to amyotrophic lateral sclerosis selectively inactivate a glial glutamate transporter. Nat Neurosci 2 (1999) 427-433
-
(1999)
Nat Neurosci
, vol.2
, pp. 427-433
-
-
Trotti, D.1
Rolfs, A.2
Danbolt, N.3
Brown, R.4
Hediger, M.5
-
142
-
-
0037461293
-
High rate of constitutional chromosomal rearrangements in apparently sporadic ALS
-
Meyer T., Albert B., Roemer K., Martin T., Kalscheuer V., Gottert E., et al. High rate of constitutional chromosomal rearrangements in apparently sporadic ALS. Neurology 60 (2003) 1348-1350
-
(2003)
Neurology
, vol.60
, pp. 1348-1350
-
-
Meyer, T.1
Albert, B.2
Roemer, K.3
Martin, T.4
Kalscheuer, V.5
Gottert, E.6
|