Early signs of neurolipidosis-related behavioural alterations in a murine model of metachromatic leukodystrophy

Behavioural Brain Research

Volumn 189, Issue 2, 2008, Pages 306-316

  Stroobants, Stijn ^a   Leroy, Toon ^a   Eckhardt, Matthias ^b   Aerts, Jean Marie ^a   Berckmans, Daniel ^a   D'Hooge, Rudi ^a  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b UNIVERSITY OF BONN   (Germany)

Author keywords

Behavioural testing; Gait analysis; Lysosomal storage disorders; Metachromatic leukodystrophy; Mouse models; Operant conditioning

Indexed keywords

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; ATAXIA; BEHAVIOR MODIFICATION; CONTROLLED STUDY; DISEASE MODEL; EARLY DIAGNOSIS; EXPLORATORY BEHAVIOR; GAIT; INSTRUMENTAL CONDITIONING; LIPIDOSIS; LYSOSOME STORAGE DISEASE; MEMORY; METACHROMATIC LEUKODYSTROPHY; MOTONEURON; MOUSE; NONHUMAN; PATHOPHYSIOLOGY; PHENOTYPE; PRIORITY JOURNAL; QUANTITATIVE ANALYSIS; TREATMENT OUTCOME;

AGE FACTORS; ANIMALS; AVOIDANCE LEARNING; CEREBELLUM; CEREBROSIDE-SULFATASE; CEREBRUM; CONDITIONING, OPERANT; DISEASE MODELS, ANIMAL; EXPLORATORY BEHAVIOR; FEMALE; GAIT; GAIT ATAXIA; INHIBITION (PSYCHOLOGY); LEUKODYSTROPHY, METACHROMATIC; LIPIDOSES; MALE; MATCHED-PAIR ANALYSIS; MICE; MICE, INBRED C57BL; MICE, KNOCKOUT; MOTOR ACTIVITY; PHENOTYPE; PSYCHOMOTOR PERFORMANCE;

EID: 41349109499     PISSN: 01664328     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbr.2008.01.008     Document Type: Article

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