-
2
-
-
0015462460
-
Fluorescence studies of the binding of the polyene antibiotics filipin 3, amphotericin B, nystatin, and lagosin to cholesterol
-
Bittman R, Fischkoff SA. Fluorescence studies of the binding of the polyene antibiotics filipin 3, amphotericin B, nystatin, and lagosin to cholesterol. Proc Natl Acad Sci USA 1972; 69: 3795-3799.
-
(1972)
Proc Natl Acad Sci USA
, vol.69
, pp. 3795-3799
-
-
Bittman, R.1
Fischkoff, S.A.2
-
3
-
-
1842314819
-
Type-C Niemann-Pick disease: Low density lipoprotein uptake is associated with premature cholesterol accumulation in the Golgi complex and excessive cholesterol storage in lysosomes
-
Blanchette-Mackie EJ, Dwyer NK, Amende LM, Kruth HS, Butler JD, Sokol J, et al. Type-C Niemann-Pick disease: low density lipoprotein uptake is associated with premature cholesterol accumulation in the Golgi complex and excessive cholesterol storage in lysosomes. Proc Natl Acad Sci USA 1988; 85: 8022-8026.
-
(1988)
Proc Natl Acad Sci USA
, vol.85
, pp. 8022-8026
-
-
Blanchette-Mackie, E.J.1
Dwyer, N.K.2
Amende, L.M.3
Kruth, H.S.4
Butler, J.D.5
Sokol, J.6
-
6
-
-
23344445128
-
The sterol-sensing domain of the Niemann-Pick C1 (NPC1) protein regulates trafficking of low density lipoprotein cholesterol
-
Millard EE, Gale SE, Dudley N, Zhang J, Schaffer JE, Ory DS. The sterol-sensing domain of the Niemann-Pick C1 (NPC1) protein regulates trafficking of low density lipoprotein cholesterol. J Biol Chem 2005; 280: 28581-28590.
-
(2005)
J Biol Chem
, vol.280
, pp. 28581-28590
-
-
Millard, E.E.1
Gale, S.E.2
Dudley, N.3
Zhang, J.4
Schaffer, J.E.5
Ory, D.S.6
-
7
-
-
0036789434
-
Relevance of Niemann-Pick type C1 protein expression in controlling plasma cholesterol and biliary lipid secretion in mice
-
Amigo L, Mendoza H, Castro J, Quinones V, Miquel JF, Zanlungo S. Relevance of Niemann-Pick type C1 protein expression in controlling plasma cholesterol and biliary lipid secretion in mice. Hepatology 2002; 36: 819-828.
-
(2002)
Hepatology
, vol.36
, pp. 819-828
-
-
Amigo, L.1
Mendoza, H.2
Castro, J.3
Quinones, V.4
Miquel, J.F.5
Zanlungo, S.6
-
8
-
-
0036193438
-
Niemann-Pick C1 protein regulates cholesterol transport to the trans-Golgi network and plasma membrane caveolae
-
Garver WS, Krishnan K, Gallagos JR, Michikawa M, Francis GA, Heidenreich RA. Niemann-Pick C1 protein regulates cholesterol transport to the trans-Golgi network and plasma membrane caveolae. J Lipid Res 2002; 43: 579-589.
-
(2002)
J Lipid Res
, vol.43
, pp. 579-589
-
-
Garver, W.S.1
Krishnan, K.2
Gallagos, J.R.3
Michikawa, M.4
Francis, G.A.5
Heidenreich, R.A.6
-
9
-
-
0032563304
-
Circulation of cholesterol between lysosomes and the plasma membrane
-
Lange Y, Ye J, Steck TL. Circulation of cholesterol between lysosomes and the plasma membrane. J Biol Chem 1998; 273: 18915-18922.
-
(1998)
J Biol Chem
, vol.273
, pp. 18915-18922
-
-
Lange, Y.1
Ye, J.2
Steck, T.L.3
-
10
-
-
0141886877
-
Niemann-Pick disease type C
-
Vanier MT, Millat G. Niemann-Pick disease type C. Clin Genet 2003; 64: 269-281.
-
(2003)
Clin Genet
, vol.64
, pp. 269-281
-
-
Vanier, M.T.1
Millat, G.2
-
11
-
-
33747335165
-
Roles of endogenously synthesized sterols in the endocytic pathway
-
Sugii S, Lin S, Ohgami N, Ohashi M, Chang CC, Chang TY. Roles of endogenously synthesized sterols in the endocytic pathway. J Biol Chem 2006; 281: 23191-23206.
-
(2006)
J Biol Chem
, vol.281
, pp. 23191-23206
-
-
Sugii, S.1
Lin, S.2
Ohgami, N.3
Ohashi, M.4
Chang, C.C.5
Chang, T.Y.6
-
12
-
-
2942665893
-
Cellular pathology of Niemann-Pick type C disease
-
Ikonen E, Holtta-Vuori M. Cellular pathology of Niemann-Pick type C disease. Semin Cell Dev Biol 2004; 15: 445-454.
-
(2004)
Semin Cell Dev Biol
, vol.15
, pp. 445-454
-
-
Ikonen, E.1
Holtta-Vuori, M.2
-
13
-
-
0022917296
-
Type C Niemann-Pick disease. A parallel loss of regulatory responses in both the uptake and esterification of low density lipoprotein-derived cholesterol in cultured fibroblasts
-
Pentchev PG, Kruth HS, Comly ME, Butler JD, Vanier MT, Wenger DA, et al. Type C Niemann-Pick disease. A parallel loss of regulatory responses in both the uptake and esterification of low density lipoprotein-derived cholesterol in cultured fibroblasts. J Biol Chem 1986; 261: 16775-16780.
-
(1986)
J Biol Chem
, vol.261
, pp. 16775-16780
-
-
Pentchev, P.G.1
Kruth, H.S.2
Comly, M.E.3
Butler, J.D.4
Vanier, M.T.5
Wenger, D.A.6
-
14
-
-
0027190308
-
Nuclear protein that binds sterol regulatory element of low density lipoprotein receptor promoter. I. Identification of the protein and delineation of its target nucleotide sequence
-
Briggs MR, Yokoyama C, Wang X, Brown MS, Goldstein JL. Nuclear protein that binds sterol regulatory element of low density lipoprotein receptor promoter. I. Identification of the protein and delineation of its target nucleotide sequence. J Biol Chem 1993; 268: 14490-14496.
-
(1993)
J Biol Chem
, vol.268
, pp. 14490-14496
-
-
Briggs, M.R.1
Yokoyama, C.2
Wang, X.3
Brown, M.S.4
Goldstein, J.L.5
-
15
-
-
0030298339
-
Sterol resistance in CHO cells traced to point mutation in SREBP cleavage-activating protein
-
Hua X, Nohturfft A, Goldstein JL, Brown MS. Sterol resistance in CHO cells traced to point mutation in SREBP cleavage-activating protein. Cell 1996; 87: 415-426.
-
(1996)
Cell
, vol.87
, pp. 415-426
-
-
Hua, X.1
Nohturfft, A.2
Goldstein, J.L.3
Brown, M.S.4
-
16
-
-
0030604717
-
Sterol-regulated release of SREBP-2 from cell membranes requires two sequential cleavages, one within a transmembrane segment
-
Sakai J, Duncan EA, Rawson RB, Hua X, Brown MS, Goldstein JL. Sterol-regulated release of SREBP-2 from cell membranes requires two sequential cleavages, one within a transmembrane segment. Cell 1996; 85: 1037-1046.
-
(1996)
Cell
, vol.85
, pp. 1037-1046
-
-
Sakai, J.1
Duncan, E.A.2
Rawson, R.B.3
Hua, X.4
Brown, M.S.5
Goldstein, J.L.6
-
17
-
-
0033049909
-
Cholesterol balance and metabolism in mice with loss of function of Niemann-Pick C protein
-
Xie C, Turley SD, Pentchev PG, Dietschy JM. Cholesterol balance and metabolism in mice with loss of function of Niemann-Pick C protein. Am J Physiol 1999; 276: E336-E344.
-
(1999)
Am J Physiol
, vol.276
-
-
Xie, C.1
Turley, S.D.2
Pentchev, P.G.3
Dietschy, J.M.4
-
18
-
-
8744222698
-
Effects of 25-hydroxycholesterol on cholesterol esterification and sterol regulatory element-binding protein processing are dissociable: Implications for cholesterol movement to the regulatory pool in the endoplasmic reticulum
-
Du X, Pham YH, Brown AJ. Effects of 25-hydroxycholesterol on cholesterol esterification and sterol regulatory element-binding protein processing are dissociable: implications for cholesterol movement to the regulatory pool in the endoplasmic reticulum. J Biol Chem 2004; 279: 47010-47016.
-
(2004)
J Biol Chem
, vol.279
, pp. 47010-47016
-
-
Du, X.1
Pham, Y.H.2
Brown, A.J.3
-
19
-
-
0034806289
-
Cholesterol signaling at the endoplasmic reticulum occurs in npc1(-/-) but not in npc1(-/-), LDLR(-/-) mice
-
Erickson RP, Kiela M, Garver WS, Krishnan K, Heidenreich RA. Cholesterol signaling at the endoplasmic reticulum occurs in npc1(-/-) but not in npc1(-/-), LDLR(-/-) mice. Biochem Biophys Res Commun 2001; 284: 326-330.
-
(2001)
Biochem Biophys Res Commun
, vol.284
, pp. 326-330
-
-
Erickson, R.P.1
Kiela, M.2
Garver, W.S.3
Krishnan, K.4
Heidenreich, R.A.5
-
20
-
-
0037815282
-
NPC1 and NPC2 regulate cellular cholesterol homeostasis through generation of low density lipoprotein cholesterol-derived oxysterols
-
Frolov A, Zielinski SE, Crowley JR, Dudley-Rucker N, Schaffer JE, Ory DS. NPC1 and NPC2 regulate cellular cholesterol homeostasis through generation of low density lipoprotein cholesterol-derived oxysterols. J Biol Chem 2003; 278: 25517-25525.
-
(2003)
J Biol Chem
, vol.278
, pp. 25517-25525
-
-
Frolov, A.1
Zielinski, S.E.2
Crowley, J.R.3
Dudley-Rucker, N.4
Schaffer, J.E.5
Ory, D.S.6
-
21
-
-
0034625354
-
Cholesterol movement in Niemann-Pick type C cells and in cells treated with amphiphiles
-
Lange Y, Ye J, Rigney M, Steck T. Cholesterol movement in Niemann-Pick type C cells and in cells treated with amphiphiles. J Biol Chem 2000; 275: 17468-17475.
-
(2000)
J Biol Chem
, vol.275
, pp. 17468-17475
-
-
Lange, Y.1
Ye, J.2
Rigney, M.3
Steck, T.4
-
22
-
-
0020973547
-
Receptor-mediated endocytosis of low-density lipoprotein in cultured cells
-
Goldstein JL, Basu SK, Brown MS. Receptor-mediated endocytosis of low-density lipoprotein in cultured cells. Methods Enzymol 1983; 98: 241-260.
-
(1983)
Methods Enzymol
, vol.98
, pp. 241-260
-
-
Goldstein, J.L.1
Basu, S.K.2
Brown, M.S.3
-
23
-
-
0029872744
-
Free and esterified oxysterol: Formation during copper-oxidation of low density lipoprotein and uptake by macrophages
-
Brown AJ, Dean RT, Jessup W. Free and esterified oxysterol: formation during copper-oxidation of low density lipoprotein and uptake by macrophages. J Lipid Res 1996; 37: 320-335.
-
(1996)
J Lipid Res
, vol.37
, pp. 320-335
-
-
Brown, A.J.1
Dean, R.T.2
Jessup, W.3
-
24
-
-
0034604350
-
Regulated step in cholesterol feedback localized to budding of SCAP from ER membranes
-
Nohturfft A, Yabe D, Goldstein JL, Brown MS, Espenshade PJ. Regulated step in cholesterol feedback localized to budding of SCAP from ER membranes. Cell 2000; 102: 315-323.
-
(2000)
Cell
, vol.102
, pp. 315-323
-
-
Nohturfft, A.1
Yabe, D.2
Goldstein, J.L.3
Brown, M.S.4
Espenshade, P.J.5
-
25
-
-
0015911779
-
Filipin as a fluorescent probe for the location of cholesterol in the membranes of fragmented sarcoplasmic reticulum
-
Drabikowski W, Lagwinska E, Sarzala MG. Filipin as a fluorescent probe for the location of cholesterol in the membranes of fragmented sarcoplasmic reticulum. Biochim Biophys Acta 1973; 291: 61-70.
-
(1973)
Biochim Biophys Acta
, vol.291
, pp. 61-70
-
-
Drabikowski, W.1
Lagwinska, E.2
Sarzala, M.G.3
-
26
-
-
0037137346
-
Cholesterol homeostasis: Not until the SCAP lady INSIGs
-
Loewen CJ, Levine TP. Cholesterol homeostasis: not until the SCAP lady INSIGs. Curr Biol 2002; 12: R779-R781.
-
(2002)
Curr Biol
, vol.12
-
-
Loewen, C.J.1
Levine, T.P.2
-
27
-
-
0034983188
-
The sterol regulatory element-binding protein pathway: Control of lipid homeostasis through regulated intracellular transport
-
Sakai J, Rawson RB. The sterol regulatory element-binding protein pathway: control of lipid homeostasis through regulated intracellular transport. Curr Opin Lipidol 2001; 12: 261-266.
-
(2001)
Curr Opin Lipidol
, vol.12
, pp. 261-266
-
-
Sakai, J.1
Rawson, R.B.2
-
28
-
-
4344637102
-
Binding between the Niemann-Pick C1 protein and a photoactivatable cholesterol analog requires 3 functional sterol-sensing domain
-
Ongami N, Ko DC, Thomas M, Scott MP, Chang CC, Chang TY. Binding between the Niemann-Pick C1 protein and a photoactivatable cholesterol analog requires 3 functional sterol-sensing domain. Proc Natl Acad Sci USA 2004; 101: 12473-12478.
-
(2004)
Proc Natl Acad Sci USA
, vol.101
, pp. 12473-12478
-
-
Ongami, N.1
Ko, D.C.2
Thomas, M.3
Scott, M.P.4
Chang, C.C.5
Chang, T.Y.6
-
29
-
-
0028332493
-
Structure-specific inhibition of lysosomal cholesterol transport in macrophages by various steroids
-
Aikawa K, Furuchi T, Fujimoto Y, Arai H, Inoue K. Structure-specific inhibition of lysosomal cholesterol transport in macrophages by various steroids. Biochim Biophys Acta 1994; 1213: 127-134.
-
(1994)
Biochim Biophys Acta
, vol.1213
, pp. 127-134
-
-
Aikawa, K.1
Furuchi, T.2
Fujimoto, Y.3
Arai, H.4
Inoue, K.5
-
30
-
-
0036731938
-
Reproductive pathology and sperm physiology in acid sphingomyelinase-deficient mice
-
Butler A, He X, Gordon RE, Wu HS, Gatt S, Schuchman EH. Reproductive pathology and sperm physiology in acid sphingomyelinase-deficient mice. Am J Pathol 2002; 161: 1061-1075.
-
(2002)
Am J Pathol
, vol.161
, pp. 1061-1075
-
-
Butler, A.1
He, X.2
Gordon, R.E.3
Wu, H.S.4
Gatt, S.5
Schuchman, E.H.6
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