Lamin A/C haploinsufficiency causes dilated cardiomyopathy and apoptosis-triggered cardiac conduction system disease

Journal of Molecular and Cellular Cardiology

Volumn 44, Issue 2, 2008, Pages 293-303

  Wolf, Cordula M ^a   Wang, Libin ^b   Alcalai, Ronny ^b   Pizard, Anne ^b,c   Burgon, Patrick G ^b,d   Ahmad, Ferhaan ^b,e   Sherwood, Megan ^a,f   Branco, Dorothy M ^a   Wakimoto, Hiroko ^a   Fishman, Glenn I ^g   See, Vincent ^h   Stewart, Colin L ⁱ   Conner, David A ^b   Berul, Charles I ^a   Seidman, Christine E ^b,j   Seidman, J G ^b  

^a BOSTON CHILDREN S HOSPITAL   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

^c CENTRE DE RECHERCHE DES CORDELIERS   (France)

^d UNIVERSITY OF OTTAWA HEART INSTITUTE   (Canada)

^e UNIVERSITY OF PITTSBURGH   (United States)

^f CHILDREN S HOSPITAL AT WESTMEAD   (Australia)

^g NEW YORK UNIVERSITY SCHOOL OF MEDICINE   (United States)

^h BOSTON UNIVERSITY SCHOOL OF MEDICINE   (United States)

ⁱ NATIONAL CANCER INSTITUTE   (United States)

^j HOWARD HUGHES MEDICAL INSTITUTE   (United States)

more..

Author keywords

Arrhythmia; Cardiac conduction system; Dilated cardiomyopathy; Heart block; Laminopathies

Indexed keywords

LAMIN A; LAMIN C;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL TISSUE; APOPTOSIS; ARTICLE; CONGESTIVE CARDIOMYOPATHY; CONTROLLED STUDY; ELECTROCARDIOGRAM; HEART FUNCTION; HEART MUSCLE CELL; HISTOPATHOLOGY; IMMUNOHISTOCHEMISTRY; MOUSE; MUTATIONAL ANALYSIS; NICK END LABELING; NONHUMAN; PRIORITY JOURNAL;

AGE OF ONSET; ANIMALS; APOPTOSIS; ARRHYTHMIAS, CARDIAC; ATRIOVENTRICULAR NODE; CARDIOMYOPATHY, DILATED; CELL NUCLEUS; CELL SEPARATION; ELECTROPHYSIOLOGY; HEART CONDUCTION SYSTEM; HETEROZYGOTE; IN SITU NICK-END LABELING; LAMIN TYPE A; MAP KINASE SIGNALING SYSTEM; MICE; MUSCULAR DISEASES; MYOCARDIUM; TELEMETRY;

MUS;

EID: 39149083716     PISSN: 00222828     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.yjmcc.2007.11.008     Document Type: Article

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