MRI evidence of white matter damage in a mouse model of Nijmegen breakage syndrome

Experimental Neurology

Volumn 209, Issue 1, 2008, Pages 181-191

  Assaf, Yaniv ^a   Galron, Ronit ^a   Shapira, Itai ^a   Nitzan, Anat ^a   Blumenfeld Katzir, Tamar ^a   Solomon, Arieh S ^b   Holdengreber, Vered ^a   Wang, Zhao Qi ^c,d   Shiloh, Yosef ^a   Barzilai, Ari ^a  

^a TEL AVIV UNIVERSITY   (Israel)

^b SHEBA MEDICAL CENTER   (Israel)

^c FRITZ LIPMANN INSTITUTE   (Germany)

^d FRIEDRICH SCHILLER UNIVERSITY JENA   (Germany)

Author keywords

MRI; Myelin; NBS; Nbs1 conditional knockout; Oligodentrocytes; White matter

Indexed keywords

MYELIN; NIBRIN;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ANISOTROPY; ARTICLE; BRAIN; CAPSULA INTERNA; CEREBELLUM AGENESIS; CHEMICAL ANALYSIS; COMPARATIVE ANATOMY; CONTROLLED STUDY; CORPUS CALLOSUM; DIFFUSION TENSOR IMAGING; DISEASE MODEL; GENE DELETION; GRAY MATTER; MESENCEPHALON; MORPHOLOGY; MOUSE; MUTANT; MYELINATION; NERVE CELL DIFFERENTIATION; NERVE FIBER; NERVE INJURY; NIJMEGEN BREAKAGE SYNDROME; NONHUMAN; NUCLEAR MAGNETIC RESONANCE IMAGING; OLIGODENDROGLIA; PRIORITY JOURNAL; PROTEIN BLOOD LEVEL; WHITE MATTER; WILD TYPE;

ANIMALS; BLOTTING, WESTERN; BRAIN; CELL CYCLE PROTEINS; CHROMOSOMAL INSTABILITY; DEVELOPMENTAL DISABILITIES; DISEASE MODELS, ANIMAL; DNA DAMAGE; FACE; HUMANS; IMAGE PROCESSING, COMPUTER-ASSISTED; IMMUNOHISTOCHEMISTRY; INFANT, NEWBORN; MAGNETIC RESONANCE IMAGING; MENTAL RETARDATION; MICE; MICE, INBRED C57BL; MICROCEPHALY; MICROSCOPY, ELECTRON; MYELIN SHEATH; NUCLEAR PROTEINS; OLIGODENDROGLIA; SYNDROME;

EID: 37549035481     PISSN: 00144886     EISSN: 10902430     Source Type: Journal    
DOI: 10.1016/j.expneurol.2007.09.021     Document Type: Article

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