Mitochondrial structure and function in the untreated Jackson toxic milk (tx-j) mouse, a model for Wilson disease

Molecular Genetics and Metabolism

Volumn 93, Issue 1, 2008, Pages 54-65

  Roberts, Eve A ^a,b,c   Robinson, Brian H ^a,c   Yang, Suyun ^a  

^a HOSPITAL FOR SICK CHILDREN RESEARCH INSTITUTE   (Canada)

^b UNIVERSITY OF TORONTO   (Canada)

^c UNIVERSITY OF TORONTO   (Canada)

Author keywords

[No Author keywords available]

Indexed keywords

ANTIOXIDANT; CITRATE SYNTHASE; COPPER; MITOCHONDRIAL DNA; PEROXIREDOXIN; THIOREDOXIN;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; CONTROLLED STUDY; ENZYME ACTIVITY; FATTY LIVER; FEMALE; HISTOLOGY; INFLAMMATION; LIVER; MALE; MILK; MITOCHONDRIAL DNA DEPLETION; MITOCHONDRION; MOUSE; NONHUMAN; OXIDATIVE STRESS; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; PROTEIN BINDING; TRANSMISSION ELECTRON MICROSCOPY; WILSON DISEASE;

ANIMALS; CITRATE (SI)-SYNTHASE; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; DNA, MITOCHONDRIAL; DNA-BINDING PROTEINS; ELECTRON TRANSPORT CHAIN COMPLEX PROTEINS; FEMALE; HEPATOCYTES; HEPATOLENTICULAR DEGENERATION; HIGH MOBILITY GROUP PROTEINS; HUMANS; MALE; MICE; MICE, INBRED C3H; MICE, MUTANT STRAINS; MILK; MITOCHONDRIA, LIVER; OXIDATIVE PHOSPHORYLATION; PEROXIREDOXINS; THIOREDOXINS; TIME FACTORS;

MUS;

EID: 36849017921     PISSN: 10967192     EISSN: 10967206     Source Type: Journal    
DOI: 10.1016/j.ymgme.2007.08.127     Document Type: Article

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