Chronic idiopathic neutropenias and severe congenital neutropenia

Current Opinion in Hematology

Volumn 15, Issue 1, 2008, Pages 8-14

  Palmblad, Jan ^a   Papadaki, Helen A ^b  

^a KAROLINSKA UNIVERSITY HOSPITAL   (Sweden)

^b UNIVERSITY OF CRETE   (Greece)

Author keywords

Acute leukemia; Chronic neutropenia; ELA2 mutations; HAX1 mutations; Inflammation; Severe congenital neutropenia

Indexed keywords

FAS LIGAND; GAMMA INTERFERON; GRANULOCYTE COLONY STIMULATING FACTOR; INTERLEUKIN 10; PROTEIN X; TRANSFORMING GROWTH FACTOR BETA1; TUMOR NECROSIS FACTOR ALPHA;

ANTIINFLAMMATORY ACTIVITY; APOPTOSIS; AUTOSOMAL DOMINANT INHERITANCE; CELL DEATH; CYTOKINE RELEASE; DISEASE COURSE; DISEASE SEVERITY; GENE MUTATION; HUMAN; LYMPHOCYTE ACTIVATION; MYELOPOIESIS; NEUTROPENIA; PATHOPHYSIOLOGY; PRIORITY JOURNAL; PROTEIN FUNCTION; RECESSIVE GENE; REVIEW; STEM CELL; SURVIVAL;

ACUTE DISEASE; APOPTOSIS; BONE DISEASES, METABOLIC; BONE MARROW; CELL TRANSFORMATION, NEOPLASTIC; CHRONIC DISEASE; DISEASE PROGRESSION; DISEASE SUSCEPTIBILITY; HUMANS; INFECTION; LEUKEMIA, MYELOID; LEUKOCYTE ELASTASE; MYELODYSPLASTIC SYNDROMES; NEUTROPENIA; OSTEOPOROSIS; PROTEINS; SERINE ENDOPEPTIDASES; T-LYMPHOCYTE SUBSETS;

EID: 36549080146     PISSN: 10656251     EISSN: 15317048     Source Type: Journal    
DOI: 10.1097/MOH.0b013e3282f172d3     Document Type: Review

References (54)

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