A comparison of the defective granulopoiesis in childhood cyclic neutropenia and in severe congenital neutropenia

Haematologica

Volumn 90, Issue 8, 2005, Pages 1032-1041

  Sera, Yasuhiko ^a   Kawaguchi, Hiroshi ^a   Nakamura, Kazuhiro ^a   Sato, Takashi ^a   Habara, Masakazu ^a   Okada, Satoshi ^a   Ishikawa, Nobutsune ^a   Kojima, Seiji ^b   Katoh, Osamu ^c   Kobayashi, Masao ^a  

^a HIROSHIMA UNIVERSITY   (Japan)

^b NAGOYA UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^c HIROSHIMA UNIVERSITY   (Japan)

Author keywords

Cyclic neutropenia; Granulopoiesis; Neutrophil elastase; Severe congenital neutropenia

Indexed keywords

CD34 ANTIGEN; GRANULOCYTE COLONY STIMULATING FACTOR RECEPTOR; LEUKOCYTE ELASTASE; STEM CELL FACTOR;

ANTIGEN EXPRESSION; ARTICLE; BONE MARROW CELL; CELL PROLIFERATION; CHILD; CHILDHOOD DISEASE; CLINICAL ARTICLE; COLONY FORMATION; CONGENITAL NEUTROPENIA; DIFFERENTIAL DIAGNOSIS; ELA2 GENE; FEMALE; GENE; GENE MUTATION; GRANULOPOIESIS; HETEROZYGOSITY; HUMAN; INFANT; MALE; MYELOID PROGENITOR CELL; NEUTROPENIA; PATHOPHYSIOLOGY; PROTEIN EXPRESSION; STATISTICAL SIGNIFICANCE; SYMPTOMATOLOGY; TRANSCRIPTION REGULATION;

AGRANULOCYTOSIS; CHILD; CHILD, PRESCHOOL; DNA PRIMERS; EXONS; FEMALE; HUMANS; INFANT; LEUKOCYTE ELASTASE; MALE; MUTATION; NEUTROPENIA; SERINE ENDOPEPTIDASES;

EID: 24944566743     PISSN: 03906078     EISSN: None     Source Type: Journal    
DOI: None     Document Type: Article

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