PGC-1α regulates the neuromuscular junction program and ameliorates Duchenne muscular dystrophy

Genes and Development

Volumn 21, Issue 7, 2007, Pages 770-783

  Handschin, Christoph ^a,b   Kobayashi, Yvonne M ^c   Chin, Sherry ^a   Seale, Patrick ^a   Campbell, Kevin P ^c   Spiegelman, Bruce M ^a  

^a HARVARD MEDICAL SCHOOL   (United States)

^b UNIVERSITY OF ZURICH   (Switzerland)

^c UNIVERSITY OF IOWA   (United States)

Author keywords

Duchenne muscular dystrophy; GA binding protein; Neuromuscular junction; PGC 1; Transcriptional regulation

Indexed keywords

AGRIN; CHOLINERGIC RECEPTOR; GA BINDING PROTEIN; NEU DIFFERENTIATION FACTOR; PEROXISOME PROLIFERATOR ACTIVATED RECEPTOR GAMMA COACTIVATOR 1ALPHA; PPARGC1A PROTEIN, MOUSE; TRANSACTIVATOR PROTEIN; UNCLASSIFIED DRUG;

ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CONTROLLED STUDY; CREATINE KINASE BLOOD LEVEL; DRUG EFFECT; DUCHENNE MUSCULAR DYSTROPHY; GENE EXPRESSION; GENETIC TRANSCRIPTION; HUMAN; HUMAN CELL; MALE; MOTOR NERVE; MOUSE; MUSCLE CELL; MYOTUBE; NEUROMUSCULAR SYNAPSE; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; PROTEIN PHOSPHORYLATION; SKELETAL MUSCLE; X CHROMOSOME LINKED MUSCULAR DYSTROPHIC MOUSE; ANIMAL; BINDING SITE; C57BL MOUSE; GENETIC TRANSFECTION; GENETICS; METABOLISM; MOUSE MUTANT; PHOSPHORYLATION;

ANIMALIA; MUS;

ANIMALS; BINDING SITES; GA-BINDING PROTEIN TRANSCRIPTION FACTOR; MICE; MICE, INBRED C57BL; MICE, INBRED MDX; MICE, KNOCKOUT; MUSCLE FIBERS; MUSCULAR DYSTROPHY, DUCHENNE; NEUROMUSCULAR JUNCTION; PHOSPHORYLATION; RECEPTORS, CHOLINERGIC; TRANS-ACTIVATORS; TRANSFECTION;

EID: 34147109662     PISSN: 08909369     EISSN: 15495477     Source Type: Journal    
DOI: 10.1101/gad.1525107     Document Type: Article

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