Effect of oculopharyngeal muscular dystrophy-associated extension of seven alanines on the fibrillation properties of the N-terminal domain of PABPN1

FEBS Journal

Volumn 274, Issue 2, 2007, Pages 346-355

  Lodderstedt, Grit ^a   Hess, Simone ^b   Hause, Gerd ^a   Scheuermann, Till ^a,c   Scheibel, Thomas ^b   Schwarz, Elisabeth ^a  

^a MARTIN LUTHER UNIVERSITY HALLE WITTENBERG   (Germany)

^b TECHNICAL UNIVERSITY OF MUNICH   (Germany)

^c ROCHE DIAGNOSTICS GMBH   (Germany)

Author keywords

AFM; Alanine expansions; Amyloid like; Kinetics of fibril formation; OPMD

Indexed keywords

POLYADENYLIC ACID BINDING PROTEIN;

ARTICLE; ATOMIC FORCE MICROSCOPY; BIOPHYSICS; CELL NUCLEUS INCLUSION BODY; CONCENTRATION RESPONSE; OCULOPHARYNGEAL MUSCULAR DYSTROPHY; PRIORITY JOURNAL; SOLUBILIZATION; WILD TYPE;

ALANINE; CHROMATOGRAPHY, HIGH PRESSURE LIQUID; HUMANS; KINETICS; MICROSCOPY, ATOMIC FORCE; MUSCULAR DYSTROPHY, OCULOPHARYNGEAL; PEPTIDES; POLY(A)-BINDING PROTEIN I; PROTEIN STRUCTURE, TERTIARY; RECOMBINANT PROTEINS; TIME FACTORS; TRINUCLEOTIDE REPEAT EXPANSION;

EID: 33845999251     PISSN: 1742464X     EISSN: 17424658     Source Type: Journal    
DOI: 10.1111/j.1742-4658.2006.05595.x     Document Type: Article

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