High resolution MRI reveals global changes in brains of Cln3 mutant mice

European Journal of Paediatric Neurology

Volumn 5, Issue , 2001, Pages 103-107

  Greene, N D E ^a   Lythgoe, M F ^a   Thomas, D L ^a   Nussbaum, R L ^a   Bernard, D J ^a   Mitchison, H M ^a  

^a ROYAL FREE AND UNIVERSITY COLLEGE MEDICAL SCHOOL   (United Kingdom)

Author keywords

Batten disease; Cln3; Magnetic resonance imaging (MRI); Mouse model; Neuronal ceroid lipofuscinosis

Indexed keywords

CLN 3 PROTEIN; GENE PRODUCT; MEMBRANE PROTEIN; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ARTICLE; BIOACCUMULATION; BRAIN; BRAIN ATROPHY; BRAIN CORTEX; CALCULATION; CELL LOSS; CEREBELLUM; CHILD; CHILDHOOD DISEASE; CLINICAL FEATURE; CONTROLLED STUDY; DEGENERATIVE DISEASE; DIAGNOSTIC IMAGING; DISEASE COURSE; EVALUATION; GENE MUTATION; GENE TARGETING; GENETIC CODE; GRAY MATTER; HIPPOCAMPUS; HUMAN; MALE; METHODOLOGY; MOUSE; NERVE CELL; NEURONAL CEROID LIPOFUSCINOSIS; NONHUMAN; NUCLEAR MAGNETIC RESONANCE IMAGING; ONSET AGE; PATHOPHYSIOLOGY; PRIORITY JOURNAL; THERAPY; VALIDATION PROCESS;

ANIMALS; ATROPHY; BRAIN; DISEASE MODELS, ANIMAL; MAGNETIC RESONANCE IMAGING; MALE; MEMBRANE GLYCOPROTEINS; MICE; MICE, MUTANT STRAINS; MOLECULAR CHAPERONES; NEURONAL CEROID-LIPOFUSCINOSES; PROTEINS;

EID: 0034925201     PISSN: 10903798     EISSN: None     Source Type: Journal    
DOI: 10.1053/ejpn.2000.0444     Document Type: Article

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