Modeling human mitochondrial diseases in flies

Biochimica et Biophysica Acta - Bioenergetics

Volumn 1757, Issue 9-10, 2006, Pages 1190-1198

  Sánchez Martínez, Álvaro ^a   Luo, Ningguang ^b   Clemente, Paula ^a   Adán, Cristina ^a   Hernández Sierra, Rosana ^a   Ochoa, Pilar ^a   Fernández Moreno, Miguel Ángel ^a   Kaguni, Laurie S ^b   Garesse, Rafael ^a  

^a AUTONOMOUS UNIVERSITY OF MADRID   (Spain)

^b Michigan State University   (United States)

Author keywords

Drosophila; Gene targeting; Mitochondria; Mitochondrial diseases; Oxidative phosphorylation

Indexed keywords

DOUBLE STRANDED DNA; FRATAXIN; MITOCHONDRIAL DNA; PROSTAGLANDIN SYNTHASE; PROTON TRANSPORTING ADENOSINE TRIPHOSPHATE SYNTHASE; TRANSFER RNA;

BIOGENESIS; BRAIN DISEASE; DISEASE ASSOCIATION; DISEASE MODEL; DISEASE PREDISPOSITION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; DNA SEQUENCE; DROSOPHILA; EMBRYO DEVELOPMENT; EXTERNAL OPHTHALMOPLEGIA; FANCONI RENOTUBULAR SYNDROME; FLY; FRIEDREICH ATAXIA; GENE CONTROL; GENE EXPRESSION; GENE MUTATION; GENE SEQUENCE; GENE STRUCTURE; GENE TARGETING; GENETIC MANIPULATION; GENETIC RECOMBINATION; HEARING IMPAIRMENT; LEIGH DISEASE; LIVER DISEASE; MITOCHONDRIAL DNA DEPLETION; MITOCHONDRIAL DNA DEPLETION SYNDROME; MITOCHONDRIAL ENCEPHALOPATHY; MOLECULAR PHYLOGENY; MUSCLE HYPOTONIA; NONHUMAN; OXIDATIVE PHOSPHORYLATION; PRIORITY JOURNAL; RETINITIS PIGMENTOSA; REVIEW; RNA INTERFERENCE; SITE DIRECTED MUTAGENESIS;

ANIMALS; DIPTERA; DISEASE MODELS, ANIMAL; DNA-DIRECTED DNA POLYMERASE; GENE TARGETING; HUMANS; MITOCHONDRIAL DISEASES;

ANIMALIA; ATAXIA;

EID: 33748985452     PISSN: 00052728     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.bbabio.2006.05.008     Document Type: Review

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